Electrophysiological and Histological Characterization of Rod-Cone Retinal Degeneration and Microglia Activation in a Mouse Model of Mucopolysaccharidosis Type IIIB
Published 2015 View Full Article
- Home
- Publications
- Publication Search
- Publication Details
Title
Electrophysiological and Histological Characterization of Rod-Cone Retinal Degeneration and Microglia Activation in a Mouse Model of Mucopolysaccharidosis Type IIIB
Authors
Keywords
-
Journal
Scientific Reports
Volume 5, Issue 1, Pages -
Publisher
Springer Nature
Online
2015-11-26
DOI
10.1038/srep17143
References
Ask authors/readers for more resources
Related references
Note: Only part of the references are listed.- The effect of neonatal gene therapy on skeletal manifestations in mucopolysaccharidosis VII dogs after a decade
- (2013) Elizabeth M. Xing et al. MOLECULAR GENETICS AND METABOLISM
- Pathogenesis of mitral valve disease in mucopolysaccharidosis VII dogs
- (2013) Paul W. Bigg et al. MOLECULAR GENETICS AND METABOLISM
- Testing for a Gap Junction-Mediated Bystander Effect in Retinitis Pigmentosa: Secondary Cone Death Is Not Altered by Deletion of Connexin36 from Cones
- (2013) Katharina Kranz et al. PLoS One
- A Rapid and Sensitive Method for Measuring N-Acetylglucosaminidase Activity in Cultured Cells
- (2013) Victor Mauri et al. PLoS One
- Whole Mount Immunofluorescent Staining of the Neonatal Mouse Retina to Investigate Angiogenesis In vivo
- (2013) Simon Tual-Chalot et al. Jove-Journal of Visualized Experiments
- IOP induces upregulation of GFAP and MHC-II and microglia reactivity in mice retina contralateral to experimental glaucoma
- (2012) Beatriz I Gallego et al. Journal of Neuroinflammation
- Lysosomal enhancement: A CLEAR answer to cellular degradative needs
- (2011) Marco Sardiello et al. CELL CYCLE
- Gene Therapy Regenerates Protein Expression in Cone Photoreceptors in Rpe65R91W/R91W Mice
- (2011) Corinne Kostic et al. PLoS One
- Gene therapy prevents photoreceptor death and preserves retinal function in a Bardet-Biedl syndrome mouse model
- (2011) D. L. Simons et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Genetic heterogeneity and clinical variability in the Sanfilippo syndrome (types A, B, and C)
- (2010) J. J. P. VAN DE Kamp et al. CLINICAL GENETICS
- Microglial Cx3cr1 knockout prevents neuron loss in a mouse model of Alzheimer's disease
- (2010) Martin Fuhrmann et al. NATURE NEUROSCIENCE
- The Role of Neuroimmunomodulation in Alzheimer's Disease
- (2009) Ricardo B. Maccioni et al. Annals of the New York Academy of Sciences
- Pathogenic cascades in lysosomal disease—Why so complex?
- (2009) S. U. Walkley JOURNAL OF INHERITED METABOLIC DISEASE
- Genetic Dissection of Rod and Cone Pathways in the Dark-Adapted Mouse Retina
- (2009) Muhammad M. Abd-El-Barr et al. JOURNAL OF NEUROPHYSIOLOGY
- Microglia in the Mouse Retina Alter the Structure and Function of Retinal Pigmented Epithelial Cells: A Potential Cellular Interaction Relevant to AMD
- (2009) Wenxin Ma et al. PLoS One
- A Gene Network Regulating Lysosomal Biogenesis and Function
- (2009) Marco Sardiello et al. SCIENCE
- Sanfilippo syndrome: A mini-review
- (2008) M. J. Valstar et al. JOURNAL OF INHERITED METABOLIC DISEASE
- Clinical and genetic spectrum of Sanfilippo type C (MPS IIIC) disease in The Netherlands
- (2007) G.J.G. Ruijter et al. MOLECULAR GENETICS AND METABOLISM
Discover Peeref hubs
Discuss science. Find collaborators. Network.
Join a conversationCreate your own webinar
Interested in hosting your own webinar? Check the schedule and propose your idea to the Peeref Content Team.
Create Now