Variant CJD

Postmortem findings in a case of variant Creutzfeldt-Jakob disease treated with intraventricular pentosan polysulfate

(2014) P. K. Newman et al.   JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY

Doxycycline in Creutzfeldt-Jakob disease: a phase 2, randomised, double-blind, placebo-controlled trial

(2014) Stéphane Haïk et al.   LANCET NEUROLOGY

Variant Creutzfeldt-Jakob Disease With Extremely Low Lymphoreticular Deposition of Prion Protein

(2014) Simon Mead et al.   JAMA Neurology

Prion infectivity in the spleen of a PRNP heterozygous individual with subclinical variant Creutzfeldt–Jakob disease

(2013) Matthew T. Bishop et al.   BRAIN

Variably protease-sensitive prionopathy in the UK: a retrospective review 1991–2008

(2013) Mark W. Head et al.   BRAIN

Assessment of prion reduction filters in decreasing infectivity of ultracentrifuged 263K scrapie-infected brain homogenates in “spiked” human blood and red blood cells

(2013) Franco Cardone et al.   TRANSFUSION

The French surveillance network of Creutzfeldt–Jakob disease. Epidemiological data in France and worldwide

(2013) J.-P. Brandel et al.   TRANSFUSION CLINIQUE ET BIOLOGIQUE

Evaluation of a test for its suitability in the diagnosis of variant Creutzfeldt-Jakob disease

(2013) J. K. Cooper et al.   VOX SANGUINIS

Prevalent abnormal prion protein in human appendixes after bovine spongiform encephalopathy epizootic: large scale survey

(2013) O. N. Gill et al.   BMJ-British Medical Journal

MM2-Thalamic Creutzfeldt-Jakob Disease: Neuropathological, Biochemical and Transmission Studies Identify a Distinctive Prion Strain

(2012) Fabio Moda et al.   BRAIN PATHOLOGY

Chronic wasting disease and atypical forms of bovine spongiform encephalopathy and scrapie are not transmissible to mice expressing wild-type levels of human prion protein

(2012) R. Wilson et al.   JOURNAL OF GENERAL VIROLOGY

Impact of Leucocyte Depletion and Prion Reduction Filters on TSE Blood Borne Transmission

(2012) Caroline Lacroux et al.   PLoS One

Highly Efficient Prion Transmission by Blood Transfusion

(2012) Olivier Andréoletti et al.   PLoS Pathogens

Prionemia and Leukocyte-Platelet-Associated Infectivity in Sheep Transmissible Spongiform Encephalopathy Models

(2011) C. Lacroux et al.   JOURNAL OF VIROLOGY

A prototype assay to detect vCJD-infected blood

(2011) Luisa Gregori   LANCET

Detection of prion infection in variant Creutzfeldt-Jakob disease: a blood-based assay

(2011) Julie Ann Edgeworth et al.   LANCET

All Clinically-Relevant Blood Components Transmit Prion Disease following a Single Blood Transfusion: A Sheep Model of vCJD

(2011) Sandra McCutcheon et al.   PLoS One

Prion Disease Blood Test Using Immunoprecipitation and Improved Quaking-Induced Conversion

(2011) C. D. Orru et al.   mBio

Correlation of Polydispersed Prion Protein and Characteristic Pathology in the Thalamus in Variant Creutzfeldt-Jakob Disease: Implication of Small Oligomeric Species

(2010) Young Pyo Choi et al.   BRAIN PATHOLOGY

Risk reduction strategies for variant Creutzfeldt-Jakob disease transmission by UK plasma products and their impact on patients with inherited bleeding disorders

(2010) C. M. MILLAR et al.   HAEMOPHILIA

Variant CJD infection in the spleen of a neurologically asymptomatic UK adult patient with haemophilia

(2010) A. PEDEN et al.   HAEMOPHILIA

Variant Creutzfeldt-Jakob disease

(2010) J. W. IRONSIDE   HAEMOPHILIA

Comparison of the level, distribution and form of disease-associated prion protein in variant and sporadic Creutzfeldt-Jakob diseased brain using conformation-dependent immunoassay and Western blot

(2010) Y. P. Choi et al.   JOURNAL OF GENERAL VIROLOGY

Chronic wasting disease prions are not transmissible to transgenic mice overexpressing human prion protein

(2010) M. K. Sandberg et al.   JOURNAL OF GENERAL VIROLOGY

Diagnosing variant Creutzfeldt-Jakob disease: a retrospective analysis of the first 150 cases in the UK

(2010) C. A. Heath et al.   JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY

Large-scale immunohistochemical examination for lymphoreticular prion protein in tonsil specimens collected in Britain

(2010) Mar Fernandez de Marco et al.   JOURNAL OF PATHOLOGY

Distinct Stability States of Disease-Associated Human Prion Protein Identified by Conformation-Dependent Immunoassay

(2010) Y. P. Choi et al.   JOURNAL OF VIROLOGY

B Cells and Platelets Harbor Prion Infectivity in the Blood of Deer Infected with Chronic Wasting Disease

(2010) C. K. Mathiason et al.   JOURNAL OF VIROLOGY

Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties

(2010) M. T. Bishop et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Variant Creutzfeldt-Jakob disease in France and the United Kingdom: Evidence for the same agent strain

(2009) Jean-Philippe Brandel et al.   ANNALS OF NEUROLOGY

Transmissions of variant Creutzfeldt-Jakob disease from brain and lymphoreticular tissue show uniform and conserved bovine spongiform encephalopathy-related phenotypic properties on primary and secondary passage in wild-type mice

(2009) D. L. Ritchie et al.   JOURNAL OF GENERAL VIROLOGY

Variant CJD in an individual heterozygous for PRNP codon 129

(2009) Diego Kaski et al.   LANCET

Safety and efficacy of quinacrine in human prion disease (PRION-1 study): a patient-preference trial

(2009) John Collinge et al.   LANCET NEUROLOGY

Pathological investigation of the first blood donor and recipient pair linked by transfusion-associated variant Creutzfeldt-Jakob disease transmission

(2009)   NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY

A case of protease sensitive prionopathy in a patient in the UK

(2009)   NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY

Infectious Prions in Pre-Clinical Deer and Transmission of Chronic Wasting Disease Solely by Environmental Exposure

(2009) Candace K. Mathiason et al.   PLoS One

A novel human disease with abnormal prion protein sensitive to protease

(2008) Pierluigi Gambetti et al.   ANNALS OF NEUROLOGY

Prion diseases are efficiently transmitted by blood transfusion in sheep

(2008) F. Houston et al.   BLOOD

Inter-Laboratory Assessment of PrPScTyping in Creutzfeldt-Jakob Disease: A Western Blot Study within the NeuroPrion Consortium

(2008) Piero Parchi et al.   BRAIN PATHOLOGY

Intraventricular pentosan polysulphate in human prion diseases: an observational study in the UK

(2008) I. Bone et al.   EUROPEAN JOURNAL OF NEUROLOGY

Evaluation of the Human Transmission Risk of an Atypical Bovine Spongiform Encephalopathy Prion Strain

(2008) Q. Kong et al.   JOURNAL OF VIROLOGY