Molecular pathogenesis of sporadic prion diseases in man

Conserved properties of human and bovine prion strains on transmission to guinea pigs

(2011) Jiri G Safar et al.   LABORATORY INVESTIGATION

Protease-Sensitive Conformers in Broad Spectrum of Distinct PrPSc Structures in Sporadic Creutzfeldt-Jakob Disease Are Indicator of Progression Rate

(2011) Chae Kim et al.   PLoS Pathogens

Distinct Stability States of Disease-Associated Human Prion Protein Identified by Conformation-Dependent Immunoassay

(2010) Y. P. Choi et al.   JOURNAL OF VIROLOGY

Human Prion Diseases in the United States

(2010) Robert C. Holman et al.   PLoS One

A New Method for the Characterization of Strain-Specific Conformational Stability of Protease-Sensitive and Protease-Resistant PrPSc

(2010) Laura Pirisinu et al.   PLoS One

Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties

(2010) M. T. Bishop et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Darwinian Evolution of Prions in Cell Culture

(2010) J. Li et al.   SCIENCE

Protease-Sensitive Synthetic Prions

(2010) David W. Colby et al.   PLoS Pathogens

Getting a Grip on Prions: Oligomers, Amyloids, and Pathological Membrane Interactions

(2009) Byron Caughey et al.   Annual Review of Biochemistry

Prion Diseases and Their Biochemical Mechanisms†

(2009) Nathan J. Cobb et al.   BIOCHEMISTRY

Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt–Jakob disease: its effect on the phenotype and prion-type characteristics

(2009) Ignazio Cali et al.   BRAIN

Extracellular mutant SOD1 induces microglial-mediated motoneuron injury

(2009) Weihua Zhao et al.   GLIA

Distinct Structures of Scrapie Prion Protein (PrPSc)-seededVersusSpontaneous Recombinant Prion Protein Fibrils Revealed by Hydrogen/Deuterium Exchange

(2009) Vytautas Smirnovas et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Propagation of Tau Misfolding from the Outside to the Inside of a Cell

(2009) Bess Frost et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Prion proteins in subpopulations of white blood cells from patients with sporadic Creutzfeldt–Jakob disease

(2009) Ed M Choi et al.   LABORATORY INVESTIGATION

Inclusion formation and neuronal cell death through neuron-to-neuron transmission of  -synuclein

(2009) P. Desplats et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Exogenous  -synuclein fibrils seed the formation of Lewy body-like intracellular inclusions in cultured cells

(2009) K. C. Luk et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Human platelets as a substrate source for the in vitro amplification of the abnormal prion protein (PrPSc) associated with variant Creutzfeldt-Jakob disease

(2009) Michael Jones et al.   TRANSFUSION

A novel human disease with abnormal prion protein sensitive to protease

(2008) Pierluigi Gambetti et al.   ANNALS OF NEUROLOGY

The Prion's Elusive Reason for Being

(2008) Adriano Aguzzi et al.   Annual Review of Neuroscience

Detection and characterization of proteinase K-sensitive disease-related prion protein with thermolysin

(2008) Sabrina Cronier et al.   BIOCHEMICAL JOURNAL

Characterization of Truncated Forms of Abnormal Prion Protein in Creutzfeldt-Jakob Disease

(2008) Silvio Notari et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Beyond PrPres Type 1/Type 2 Dichotomy in Creutzfeldt-Jakob Disease

(2008) Emmanuelle Uro-Coste et al.   PLoS Pathogens