Rationale, design and objectives of ARegPKD, a European ARPKD registry study

Effect of Pravastatin on Total Kidney Volume, Left Ventricular Mass Index, and Microalbuminuria in Pediatric Autosomal Dominant Polycystic Kidney Disease

(2014) M. A. Cadnapaphornchai et al.   Clinical Journal of the American Society of Nephrology

Intragenic motifs regulate the transcriptional complexity of Pkhd1/PKHD1

(2014) Ravindra Boddu et al.   JOURNAL OF MOLECULAR MEDICINE-JMM

Consensus Expert Recommendations for the Diagnosis and Management of Autosomal Recessive Polycystic Kidney Disease: Report of an International Conference

(2014) Lisa M. Guay-Woodford et al.   JOURNAL OF PEDIATRICS

Imaging Classification of Autosomal Dominant Polycystic Kidney Disease: A Simple Model for Selecting Patients for Clinical Trials

(2014) M. V. Irazabal et al.   JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY

Blood Pressure in Early Autosomal Dominant Polycystic Kidney Disease

(2014) Robert W. Schrier et al.   NEW ENGLAND JOURNAL OF MEDICINE

Angiotensin Blockade in Late Autosomal Dominant Polycystic Kidney Disease

(2014) Vicente E. Torres et al.   NEW ENGLAND JOURNAL OF MEDICINE

Autosomal Recessive Polycystic Kidney Disease: A Hepatorenal Fibrocystic Disorder With Pleiotropic Effects

(2014) E. A. Hartung et al.   PEDIATRICS

Activation of the PI3K/mTOR Pathway Is Involved in Cystic Proliferation of Cholangiocytes of the PCK Rat

(2014) Xiang Shan Ren et al.   PLoS One

An Emerging Molecular Understanding and Novel Targeted Treatment Approaches in Pediatric Kidney Diseases

(2014) Max Christoph Liebau   Frontiers in Pediatrics

Effect of longacting somatostatin analogue on kidney and cyst growth in autosomal dominant polycystic kidney disease (ALADIN): a randomised, placebo-controlled, multicentre trial

(2013) Anna Caroli et al.   LANCET

Clinical manifestations of autosomal recessive polycystic kidney disease (ARPKD): kidney-related and non-kidney-related phenotypes

(2013) Rainer Büscher et al.   PEDIATRIC NEPHROLOGY

Pathophysiology of childhood polycystic kidney diseases: new insights into disease-specific therapy

(2013) William E. Sweeney et al.   PEDIATRIC RESEARCH

Combined liver-kidney transplantation for children with autosomal recessive polycystic kidney disease (ARPKD): indication and outcome

(2013) Florian Brinkert et al.   TRANSPLANT INTERNATIONAL

Characteristics of Congenital Hepatic Fibrosis in a Large Cohort of Patients With Autosomal Recessive Polycystic Kidney Disease

(2012) Meral Gunay–Aygun et al.   GASTROENTEROLOGY

Rapamycin-mediated suppression of renal cyst expansion in del34Pkd1−/−mutant mouse embryos: An investigation of the feasibility of renal cyst prevention in the foetus

(2012) CHERIE STAYNER et al.   NEPHROLOGY

Tolvaptan in Patients with Autosomal Dominant Polycystic Kidney Disease

(2012) Vicente E. Torres et al.   NEW ENGLAND JOURNAL OF MEDICINE

Modeling Human Disease in Humans: The Ciliopathies

(2011) Gaia Novarino et al.   CELL

Congenital Hepatic Fibrosis and Autosomal Recessive Polycystic Kidney Disease

(2011) Arvind Srinath et al.   JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION

Kidney and liver transplantation in patients with autosomal recessive polycystic kidney disease: a multicentric study

(2011) M. Chapal et al.   NEPHROLOGY DIALYSIS TRANSPLANTATION

Clinical treatment of polycystic kidney disease (APKD): do we need further suggestions from rodents?

(2011) M. Sabbatini et al.   NEPHROLOGY DIALYSIS TRANSPLANTATION

Ciliopathies

(2011) Friedhelm Hildebrandt et al.   NEW ENGLAND JOURNAL OF MEDICINE

Renin-angiotensin System Activation in Congenital Hepatic Fibrosis in the PCK Rat Model of Autosomal Recessive Polycystic Kidney Disease

(2010) Miwa Goto et al.   JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION

Inhibition of mTOR with sirolimus does not attenuate progression of liver and kidney disease in PCK rats

(2010) C. Renken et al.   NEPHROLOGY DIALYSIS TRANSPLANTATION

Sirolimus and Kidney Growth in Autosomal Dominant Polycystic Kidney Disease

(2010) Andreas L. Serra et al.   NEW ENGLAND JOURNAL OF MEDICINE

Everolimus in Patients with Autosomal Dominant Polycystic Kidney Disease

(2010) Gerd Walz et al.   NEW ENGLAND JOURNAL OF MEDICINE

The renin-angiotensin system and hypertension in autosomal recessive polycystic kidney disease

(2010) Miwa Goto et al.   PEDIATRIC NEPHROLOGY

Chronic treatment with lisinopril decreases proliferative and apoptotic pathways in autosomal recessive polycystic kidney disease

(2010) Guangfu Jia et al.   PEDIATRIC NEPHROLOGY

Strict Blood-Pressure Control and Progression of Renal Failure in Children

(2009)   NEW ENGLAND JOURNAL OF MEDICINE