Functional Characterization of Friedreich Ataxia iPS-Derived Neuronal Progenitors and Their Integration in the Adult Brain
Published 2014 View Full Article
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Title
Functional Characterization of Friedreich Ataxia iPS-Derived Neuronal Progenitors and Their Integration in the Adult Brain
Authors
Keywords
Neurons, Neuronal differentiation, Neurospheres, Induced pluripotent stem cells, Mitochondria, Action potentials, Neuronal tuning, Membrane potential
Journal
PLoS One
Volume 9, Issue 7, Pages e101718
Publisher
Public Library of Science (PLoS)
Online
2014-07-08
DOI
10.1371/journal.pone.0101718
References
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- (2012) A. Hick et al. Disease Models & Mechanisms
- Clinical Features of Friedreich Ataxia
- (2012) Martin B. Delatycki et al. JOURNAL OF CHILD NEUROLOGY
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- (2012) Mark Denham et al. STEM CELLS
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- (2011) Leanne Coyne et al. NEUROCHEMISTRY INTERNATIONAL
- Friedreich's Ataxia Induced Pluripotent Stem Cells Model Intergenerational GAA⋅TTC Triplet Repeat Instability
- (2010) Sherman Ku et al. Cell Stem Cell
- Blood cells from Friedreich ataxia patients harbor frataxin deficiency without a loss of mitochondrial function
- (2010) Mary A. Selak et al. MITOCHONDRION
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- (2010) Eric C. Deutsch et al. MOLECULAR GENETICS AND METABOLISM
- High-throughput, pooled sequencing identifies mutations in NUBPL and FOXRED1 in human complex I deficiency
- (2010) Sarah E Calvo et al. NATURE GENETICS
- Generation of Induced Pluripotent Stem Cell Lines from Friedreich Ataxia Patients
- (2010) Jun Liu et al. Stem Cell Reviews and Reports
- Friedreich ataxia: The clinical picture
- (2009) Massimo Pandolfo JOURNAL OF NEUROLOGY
- Overexpression of the yeast frataxin homolog (Yfh1): Contrasting effects on iron–sulfur cluster assembly, heme synthesis and resistance to oxidative stress
- (2009) Alexandra Seguin et al. MITOCHONDRION
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- Cell functions impaired by frataxin deficiency are restored by drug-mediated iron relocation
- (2008) O. Kakhlon et al. BLOOD
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- (2008) C. Vonesch et al. IEEE TRANSACTIONS ON IMAGE PROCESSING
- Iron–sulfur cluster biogenesis and human disease
- (2008) Tracey A. Rouault et al. TRENDS IN GENETICS
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