The Wobbler Mouse Model of Amyotrophic Lateral Sclerosis (ALS) Displays Hippocampal Hyperexcitability, and Reduced Number of Interneurons, but No Presynaptic Vesicle Release Impairments

Motor neurone disease: a practical update on diagnosis and management

(2013) P. J. Shaw et al.   CLINICAL MEDICINE

Loss of Vps54 Function Leads to Vesicle Traffic Impairment, Protein Mis-Sorting and Embryonic Lethality

(2013) Páll Karlsson et al.   INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES

The wobbler mouse, an ALS animal model

(2013) Jakob Maximilian Moser et al.   MOLECULAR GENETICS AND GENOMICS

Embryonic alteration of motoneuronal morphology induces hyperexcitability in the mouse model of amyotrophic lateral sclerosis

(2013) Elodie Martin et al.   NEUROBIOLOGY OF DISEASE

Progesterone Attenuates Several Hippocampal Abnormalities of the Wobbler Mouse

(2012) M. Meyer et al.   JOURNAL OF NEUROENDOCRINOLOGY

GABA Signaling Promotes Synapse Elimination and Axon Pruning in Developing Cortical Inhibitory Interneurons

(2012) X. Wu et al.   JOURNAL OF NEUROSCIENCE

Decreased motor cortex  -aminobutyric acid in amyotrophic lateral sclerosis

(2012) B. R. Foerster et al.   NEUROLOGY

Enhanced Hippocampal Long-Term Potentiation and Fear Memory in Btbd9 Mutant Mice

(2012) Mark P. DeAndrade et al.   PLoS One

Interneuron networks in the hippocampus

(2011) Dimitri M Kullmann   CURRENT OPINION IN NEUROBIOLOGY

Genetic Rodent Models of Amyotrophic Lateral Sclerosis

(2011) L. Van Den Bosch   JOURNAL OF BIOMEDICINE AND BIOTECHNOLOGY

Clinical genetics of amyotrophic lateral sclerosis: what do we really know?

(2011) Peter M. Andersen et al.   Nature Reviews Neurology

Molecular pathways of motor neuron injury in amyotrophic lateral sclerosis

(2011) Laura Ferraiuolo et al.   Nature Reviews Neurology

Reduced GABAergic Inhibition Explains Cortical Hyperexcitability in the Wobbler Mouse Model of ALS

(2010) Jose Luis Nieto-Gonzalez et al.   CEREBRAL CORTEX

Neural precursor-derived astrocytes of wobbler mice induce apoptotic death of motor neurons through reduced glutamate uptake

(2010) Valentina Diana et al.   EXPERIMENTAL NEUROLOGY

Ang2/Fat-Free Is a Conserved Subunit of the Golgi-associated Retrograde Protein Complex

(2010) F. Javier Pérez-Victoria et al.   MOLECULAR BIOLOGY OF THE CELL

Structural basis for the wobbler mouse neurodegenerative disorder caused by mutation in the Vps54 subunit of the GARP complex

(2010) F. J. Perez-Victoria et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Transport according to GARP: receiving retrograde cargo at the trans-Golgi network

(2010) Juan S. Bonifacino et al.   TRENDS IN CELL BIOLOGY

Deleterious Variants of FIG4, a Phosphoinositide Phosphatase, in Patients with ALS

(2009) Clement Y. Chow et al.   AMERICAN JOURNAL OF HUMAN GENETICS

TDP-43 Redistribution is an Early Event in Sporadic Amyotrophic Lateral Sclerosis

(2009) Maria Teresa Giordana et al.   BRAIN PATHOLOGY

Defining the mechanisms that underlie cortical hyperexcitability in amyotrophic lateral sclerosis

(2009) Steve Vucic et al.   EXPERIMENTAL NEUROLOGY

Proteomic Profiling of Cervical and Lumbar Spinal Cord Reveals Potential Protective Mechanisms in the Wobbler Mouse, a Model of Motor Neuron Degeneration

(2009) Antonio Bastone et al.   JOURNAL OF PROTEOME RESEARCH

Release of [3H]d-aspartate induced by K+-stimulation is increased in the cervical spinal cord of the wobbler mouse: a model of motor neuron disease

(2009) Giambattista Bonanno et al.   NEUROCHEMISTRY INTERNATIONAL

Progression of hippocampal degeneration in amyotrophic lateral sclerosis with or without memory impairment: distinction from Alzheimer disease

(2008) Takahiro Takeda et al.   ACTA NEUROPATHOLOGICA

Role of Axonal Transport in Neurodegenerative Diseases

(2008) Kurt J. De Vos et al.   Annual Review of Neuroscience

Cortical hyperexcitability may precede the onset of familial amyotrophic lateral sclerosis

(2008) Steve Vucic et al.   BRAIN

Increased persistent sodium current determines cortical hyperexcitability in a genetic model of amyotrophic lateral sclerosis

(2008) Massimo Pieri et al.   EXPERIMENTAL NEUROLOGY

Wobbler mice modeling motor neuron disease display elevated transactive response DNA binding protein

(2008) J.S. Dennis et al.   NEUROSCIENCE

TDP-43 Mutations in Familial and Sporadic Amyotrophic Lateral Sclerosis

(2008) J. Sreedharan et al.   SCIENCE