Small Ruminant Nor98 Prions Share Biochemical Features with Human Gerstmann-Sträussler-Scheinker Disease and Variably Protease-Sensitive Prionopathy

Glycoform-Selective Prion Formation in Sporadic and Familial Forms of Prion Disease

(2013) Xiangzhu Xiao et al.   PLoS One

All major prion types recognised by a multiplex immunofluorometric assay for disease screening and confirmation in sheep

(2012) Yue Tang et al.   JOURNAL OF IMMUNOLOGICAL METHODS

Allelic Origin of Protease-Sensitive and Protease-Resistant Prion Protein Isoforms in Gerstmann-Sträussler-Scheinker Disease with the P102L Mutation

(2012) Salvatore Monaco et al.   PLoS One

Effect of PrP genotype and route of inoculation on the ability of discriminatory Western blot to distinguish scrapie from sheep bovine spongiform encephalopathy

(2011) S. Migliore et al.   JOURNAL OF GENERAL VIROLOGY

Variably Protease-Sensitive Prionopathy: a Novel Disease of the Prion Protein

(2011) Pierluigi Gambetti et al.   JOURNAL OF MOLECULAR NEUROSCIENCE

Nor98 Scrapie Identified in the United States

(2011) Christie M. Loiacono et al.   JOURNAL OF VETERINARY DIAGNOSTIC INVESTIGATION

Identification of Atypical Scrapie in Canadian Sheep

(2011) Gordon B. Mitchell et al.   JOURNAL OF VETERINARY DIAGNOSTIC INVESTIGATION

Atypical Scrapie/Nor98 in a Sheep from New Zealand

(2011) Reinhold Kittelberger et al.   JOURNAL OF VETERINARY DIAGNOSTIC INVESTIGATION

Atypical Scrapie Isolates Involve a Uniform Prion Species with a Complex Molecular Signature

(2011) Dorothea R. Götte et al.   PLoS One

Protease-Sensitive Conformers in Broad Spectrum of Distinct PrPSc Structures in Sporadic Creutzfeldt-Jakob Disease Are Indicator of Progression Rate

(2011) Chae Kim et al.   PLoS Pathogens

Atypical/Nor98 Scrapie Infectivity in Sheep Peripheral Tissues

(2011) Olivier Andréoletti et al.   PLoS Pathogens

Dissociation of Infectivity from Seeding Ability in Prions with Alternate Docking Mechanism

(2011) Michael B. Miller et al.   PLoS Pathogens

Variably protease-sensitive prionopathy: A new sporadic disease of the prion protein

(2010) Wen-Quan Zou et al.   ANNALS OF NEUROLOGY

The prevalence of atypical scrapie in sheep from positive flocks is not higher than in the general sheep population in 11 European countries

(2010) Alexandre Fediaevsky et al.   BMC Veterinary Research

Agent strain variation in human prion disease: insights from a molecular and pathological review of the National Institutes of Health series of experimentally transmitted disease

(2010) P. Parchi et al.   BRAIN

Atypical Prion Protein Conformation in Familial Prion Disease with PRNP P105T Mutation

(2010) Magdalini Polymenidou et al.   BRAIN PATHOLOGY

PrP Conformational Transitions Alter Species Preference of a PrP-specific Antibody

(2010) Wen-Quan Zou et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Characterization of atypical scrapie cases from Great Britain in transgenic ovine PrP mice

(2010) P. C. Griffiths et al.   JOURNAL OF GENERAL VIROLOGY

Distinct Stability States of Disease-Associated Human Prion Protein Identified by Conformation-Dependent Immunoassay

(2010) Y. P. Choi et al.   JOURNAL OF VIROLOGY

A New Method for the Characterization of Strain-Specific Conformational Stability of Protease-Sensitive and Protease-Resistant PrPSc

(2010) Laura Pirisinu et al.   PLoS One

Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties

(2010) M. T. Bishop et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Similarities between Forms of Sheep Scrapie and Creutzfeldt-Jakob Disease Are Encoded by Distinct Prion Types

(2009) Wiebke M. Wemheuer et al.   AMERICAN JOURNAL OF PATHOLOGY

Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt–Jakob disease: its effect on the phenotype and prion-type characteristics

(2009) Ignazio Cali et al.   BRAIN

Transmissibility of Atypical Scrapie in Ovine Transgenic Mice: Major Effects of Host Prion Protein Expression and Donor Prion Genotype

(2009) Jean-Noël Arsac et al.   PLoS One

Co-existence of classical scrapie and Nor98 in a sheep from an Italian outbreak

(2009) M. Mazza et al.   RESEARCH IN VETERINARY SCIENCE

A novel human disease with abnormal prion protein sensitive to protease

(2008) Pierluigi Gambetti et al.   ANNALS OF NEUROLOGY

No temporal trends in the prevalence of atypical scrapie in British sheep, 2002–2006

(2008) K Marie McIntyre et al.   BMC Veterinary Research

A descriptive study of the prevalence of atypical and classical scrapie in sheep in 20 European countries

(2008) Alexandre Fediaevsky et al.   BMC Veterinary Research

Accessibility of a critical prion protein region involved in strain recognition and its implications for the early detection of prions

(2008) J. Yuan et al.   CELLULAR AND MOLECULAR LIFE SCIENCES

Histidine at codon 154 of the prion protein gene is a risk factor for Nor98 scrapie in goats

(2008) S. Colussi et al.   JOURNAL OF GENERAL VIROLOGY

High-resolution differentiation of transmissible spongiform encephalopathy strains by quantitative N-terminal amino acid profiling (N-TAAP) of PK-digested abnormal prion protein

(2008) Adriana Gielbert et al.   JOURNAL OF MASS SPECTROMETRY

Atypical/Nor98 scrapie: properties of the agent, genetics, and epidemiology

(2008) Sylvie L. Benestad et al.   VETERINARY RESEARCH