Nebulized Hyaluronan Ameliorates lung inflammation in cystic fibrosis mice

Tissue Transglutaminase Activation Modulates Inflammation in Cystic Fibrosis via PPAR  Down-Regulation

(2014) L. Maiuri et al.   JOURNAL OF IMMUNOLOGY

Comparative Processing and Function of Human and Ferret Cystic Fibrosis Transmembrane Conductance Regulator

(2012) John T. Fisher et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Antioxidant acitivity of low molecular weight hyaluronic acid

(2011) Chunlin Ke et al.   FOOD AND CHEMICAL TOXICOLOGY

Mouse models of cystic fibrosis: Phenotypic analysis and research applications

(2011) Martina Wilke et al.   Journal of Cystic Fibrosis

Abnormal Trafficking and Degradation of TLR4 Underlie the Elevated Inflammatory Response in Cystic Fibrosis

(2011) E. M. Bruscia et al.   JOURNAL OF IMMUNOLOGY

Therapy for Cystic Fibrosis — The End of the Beginning?

(2011) Pamela B. Davis   NEW ENGLAND JOURNAL OF MEDICINE

A CFTR Potentiator in Patients with Cystic Fibrosis and theG551DMutation

(2011) Bonnie W. Ramsey et al.   NEW ENGLAND JOURNAL OF MEDICINE

Hyaluronan as an Immune Regulator in Human Diseases

(2011) Dianhua Jiang et al.   PHYSIOLOGICAL REVIEWS

Hyaluronic acid improves “pleasantness” and tolerability of nebulized hypertonic saline in a cohort of patients with cystic fibrosis

(2010) Paolo Buonpensiero et al.   ADVANCES IN THERAPY

Defective CFTR induces aggresome formation and lung inflammation in cystic fibrosis through ROS-mediated autophagy inhibition

(2010) Alessandro Luciani et al.   NATURE CELL BIOLOGY

Emerging therapies in cystic fibrosis

(2010) Paula Anderson   Therapeutic Advances in Respiratory Disease

An overview of international literature from cystic fibrosis registries: 1. Mortality and survival studies in cystic fibrosis

(2009) R. Buzzetti et al.   Journal of Cystic Fibrosis

Airway and Lung Pathology Due to Mucosal Surface Dehydration in  -Epithelial Na+ Channel-Overexpressing Mice: Role of TNF-  and IL-4R  Signaling, Influence of Neonatal Development, and Limited Efficacy of Glucocorticoid Treatment

(2009) A. Livraghi et al.   JOURNAL OF IMMUNOLOGY

SUMOylation of Tissue Transglutaminase as Link between Oxidative Stress and Inflammation

(2009) A. Luciani et al.   JOURNAL OF IMMUNOLOGY

CD44 Costimulation Promotes FoxP3+ Regulatory T Cell Persistence and Function via Production of IL-2, IL-10, and TGF- 

(2009) P. L. Bollyky et al.   JOURNAL OF IMMUNOLOGY

Cystic fibrosis

(2009) Brian P O'Sullivan et al.   LANCET

CFTR Is a Negative Regulator of NFκB Mediated Innate Immune Response

(2009) Neeraj Vij et al.   PLoS One

Cystic Fibrosis: Pathogenesis and Future Treatment Strategies

(2009) Felix A Ratjen   Respiratory Care

Macrophages Directly Contribute to the Exaggerated Inflammatory Response in Cystic Fibrosis Transmembrane Conductance Regulator−/−Mice

(2008) Emanuela M. Bruscia et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Production of CFTR-null and CFTR-ΔF508 heterozygous pigs by adeno-associated virus–mediated gene targeting and somatic cell nuclear transfer

(2008) Christopher S. Rogers et al.   JOURNAL OF CLINICAL INVESTIGATION

Disruption of the CFTR Gene Produces a Model of Cystic Fibrosis in Newborn Pigs

(2008) C. S. Rogers et al.   SCIENCE