☆ 4.5 Article

Associated disorders of Chiari Type I malformations: a review

NEUROSURGICAL FOCUS (2011)

Journal

NEUROSURGICAL FOCUS

Volume 31, Issue 3, Pages -

Publisher

AMER ASSOC NEUROLOGICAL SURGEONS

DOI: 10.3171/2011.6.FOCUS11112

Keywords

hindbrain; herniation; tonsillar ectopia; Chiari malformation

Categories

Clinical Neurology Surgery

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Abstract

A single pathophysiological mechanism of Chiari Type I malformations (CM-I) has been a topic of debate. To help better understand CM-I, the authors review disorders known to be associated with CM-I. The primary methodology found among most of them is deformation of the posterior cranial fossa, usually with subsequent decrease in volume. Other mechanisms exist as well, which can be categorized as either congenital or acquired. In understanding the relationship of such disorders with CM-I, we may gain further insight into the process by which cerebellar tonsillar herniation occurs. Some of these pathologies appear to be true associations, but many appear to be spurious. (DOI: 10.3171/2011.6.FOCUS11112)

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