Tackling the increasing complexity of CF care

Future trends in cystic fibrosis demography in 34 European countries

(2015) Pierre-Régis Burgel et al.   EUROPEAN RESPIRATORY JOURNAL

Randomized trial of efficacy and safety of dornase alfa delivered by eRapid nebulizer in cystic fibrosis patients

(2015) Gregory S. Sawicki et al.   Journal of Cystic Fibrosis

Opportunities for cystic fibrosis care teams to support treatment adherence

(2015) Kristin A. Riekert et al.   Journal of Cystic Fibrosis

Pulmonary Hypertension in Cystic Fibrosis with Advanced Lung Disease

(2014) Don Hayes et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Longevity of Patients With Cystic Fibrosis in 2000 to 2010 and Beyond: Survival Analysis of the Cystic Fibrosis Foundation Patient Registry

(2014) Todd MacKenzie et al.   ANNALS OF INTERNAL MEDICINE

Pulmonary Medication Adherence and Health-care Use in Cystic Fibrosis

(2014) Alexandra L. Quittner et al.   CHEST

Depression and anxiety in adolescents and adults with cystic fibrosis in the UK: A cross-sectional study

(2014) Alistair J.A. Duff et al.   Journal of Cystic Fibrosis

Motivating adherence among adolescents with cystic fibrosis: Youth and parent perspectives

(2014) Gregory S. Sawicki et al.   PEDIATRIC PULMONOLOGY

Accelerating the rate of improvement in cystic fibrosis care: contributions and insights of the learning and leadership collaborative

(2014) Marjorie M Godfrey et al.   BMJ Quality & Safety

The impact of transforming healthcare delivery on cystic fibrosis outcomes: a decade of quality improvement at Cincinnati Children’s Hospital

(2014) Christopher M Siracusa et al.   BMJ Quality & Safety

A CFTR corrector (lumacaftor) and a CFTR potentiator (ivacaftor) for treatment of patients with cystic fibrosis who have a phe508del CFTR mutation: a phase 2 randomised controlled trial

(2014) Michael P Boyle et al.   Lancet Respiratory Medicine

User Preferences and Design Recommendations for an mHealth App to Promote Cystic Fibrosis Self-Management

(2014) Marisa E Hilliard et al.   JMIR mHealth and uHealth

Cystic Fibrosis Pulmonary Guidelines

(2013) Peter J. Mogayzel et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Comparative Effectiveness Research: A Report From the Institute of Medicine

(2013) Harold C. Sox   ANNALS OF INTERNAL MEDICINE

Rationale and design of a randomized trial of home electronic symptom and lung function monitoring to detect cystic fibrosis pulmonary exacerbations: The early intervention in cystic fibrosis exacerbation (eICE) trial

(2013) N. Lechtzin et al.   Contemporary Clinical Trials

Treatment complexity in cystic fibrosis: Trends over time and associations with site-specific outcomes

(2013) Gregory S. Sawicki et al.   Journal of Cystic Fibrosis

The Randomized Registry Trial — The Next Disruptive Technology in Clinical Research?

(2013) Michael S. Lauer et al.   NEW ENGLAND JOURNAL OF MEDICINE

Inhaled aztreonam lysine vs. inhaled tobramycin in cystic fibrosis: A comparative efficacy trial

(2012) Baroukh M. Assael et al.   Journal of Cystic Fibrosis

Managing treatment complexity in cystic fibrosis: Challenges and Opportunities

(2012) Gregory S. Sawicki et al.   PEDIATRIC PULMONOLOGY

Comparative Effectiveness Research

(2011) Christopher H. Goss   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Con: Comparative Effectiveness Research

(2011) Jerry A. Krishnan   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Comparative Efficacy and Safety of 4 Randomized Regimens to Treat Early Pseudomonas aeruginosa Infection in Children With Cystic Fibrosis

(2011) Miriam M. Treggiari   ARCHIVES OF PEDIATRICS & ADOLESCENT MEDICINE

Accurate Assessment of Adherence

(2011) Tracey Daniels et al.   CHEST

A Tutorial on Methods to Estimating Clinically and Policy-Meaningful Measures of Treatment Effects in Prospective Observational Studies: A Review

(2011) Peter C Austin et al.  

A Comparison of Amount and Speed of Deposition Between the PARI LC STAR® Jet Nebulizer and an Investigational eFlow® Nebulizer

(2011) Allan L. Coates et al.   Journal of Aerosol Medicine and Pulmonary Drug Delivery

Development of an Inhaled Dry-Powder Formulation of Tobramycin Using PulmoSphere™ Technology

(2011) David E. Geller et al.   Journal of Aerosol Medicine and Pulmonary Drug Delivery

Longitudinal association between medication adherence and lung health in people with cystic fibrosis

(2011) Michelle N. Eakin et al.   Journal of Cystic Fibrosis

Anxiety, depression, and life satisfaction in parents caring for children with cystic fibrosis

(2011) Tanja Besier et al.   PEDIATRIC PULMONOLOGY

Psychometric evaluation of the Cystic Fibrosis Questionnaire-Revised in a national sample

(2011) Alexandra L. Quittner et al.   QUALITY OF LIFE RESEARCH

Adherence with tobramycin inhaled solution and health care utilization

(2011) Becky A Briesacher et al.   BMC Pulmonary Medicine

Prevalence of Symptoms of Anxiety and Depression in German Patients With Cystic Fibrosis

(2010) Lutz Goldbeck et al.   CHEST

Lung deposition of inhaled tobramycin with eFlow rapid/LC Plus jet nebuliser in healthy and cystic fibrosis subjects

(2010) Warren Lenney et al.   Journal of Cystic Fibrosis

Safety, efficacy and convenience of tobramycin inhalation powder in cystic fibrosis patients: The EAGER trial

(2010) Michael W. Konstan et al.   Journal of Cystic Fibrosis

Evaluation of a home telemonitoring service for adult patients with cystic fibrosis: a pilot study

(2010) Gianluigi Grzincich et al.   JOURNAL OF TELEMEDICINE AND TELECARE

Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTRMutation

(2010) Frank J. Accurso et al.   NEW ENGLAND JOURNAL OF MEDICINE

Tobramycin inhalation powder for P. aeruginosa infection in cystic fibrosis: The EVOLVE trial

(2010) Michael W. Konstan et al.   PEDIATRIC PULMONOLOGY

An 18-month study of the safety and efficacy of repeated courses of inhaled aztreonam lysine in cystic fibrosis

(2010) Christopher M. Oermann et al.   PEDIATRIC PULMONOLOGY

A pragmatic-explanatory continuum indicator summary (PRECIS): a tool to help trial designers

(2009) K. E. Thorpe et al.   CANADIAN MEDICAL ASSOCIATION JOURNAL

Efficacy and Safety of Inhaled Aztreonam Lysine for Airway Pseudomonas in Cystic Fibrosis

(2009) George Z. Retsch-Bogart et al.   CHEST

Early anti-pseudomonal acquisition in young patients with cystic fibrosis: Rationale and design of the EPIC clinical trial and observational study,

(2009) Miriam M. Treggiari et al.   Contemporary Clinical Trials

Fostering implementation of health services research findings into practice: a consolidated framework for advancing implementation science

(2009) Laura J Damschroder et al.   Implementation Science

Inhaled Aztreonam Lysine for Chronic AirwayPseudomonas aeruginosain Cystic Fibrosis

(2008) Karen S. McCoy et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

High treatment burden in adults with cystic fibrosis: Challenges to disease self-management

(2008) Gregory S. Sawicki et al.   Journal of Cystic Fibrosis