1H magnetic resonance spectroscopy of neurodegeneration in a mouse model of niemann-pick type C1 disease

Function of the Niemann–Pick type C proteins and their bypass by cyclodextrin

(2011) Jean E Vance et al.   CURRENT OPINION IN LIPIDOLOGY

In vivo monitoring of recovery from neurodegeneration in conditional transgenic SCA1 mice

(2011) Gülin Öz et al.   EXPERIMENTAL NEUROLOGY

A novel mouse model of Niemann–Pick type C disease carrying a D1005G-Npc1 mutation comparable to commonly observed human mutations

(2011) Robert A. Maue et al.   HUMAN MOLECULAR GENETICS

In vivo MRS study of intraventricular tumors

(2011) Tariq Shah et al.   JOURNAL OF MAGNETIC RESONANCE IMAGING

In vivo assessment of neurodegeneration in niemann-pick type C mice by quantitative T2 mapping and diffusion tensor imaging

(2011) John W. Totenhagen et al.   JOURNAL OF MAGNETIC RESONANCE IMAGING

Magnetic resonance spectroscopy,  -amyloid load, and cognition in a population-based sample of cognitively normal older adults

(2011) K. Kantarci et al.   NEUROLOGY

Adipose tissue-derived stem cells rescue Purkinje neurons and alleviate inflammatory responses in Niemann-Pick disease type C mice

(2010) Jae-sung Bae et al.   CELL AND TISSUE RESEARCH

Study of the features of proton MR spectroscopy (1H-MRS) on amyotrophic lateral sclerosis

(2010) Jing Han et al.   JOURNAL OF MAGNETIC RESONANCE IMAGING

Weekly Cyclodextrin Administration Normalizes Cholesterol Metabolism in Nearly Every Organ of the Niemann-Pick Type C1 Mouse and Markedly Prolongs Life

(2010) Charina M Ramirez et al.   PEDIATRIC RESEARCH

Quantitation of magnetic resonance spectroscopy signals: the jMRUI software package

(2009) D Stefan et al.   MEASUREMENT SCIENCE and TECHNOLOGY

Chronic Cyclodextrin Treatment of Murine Niemann-Pick C Disease Ameliorates Neuronal Cholesterol and Glycosphingolipid Storage and Disease Progression

(2009) Cristin D. Davidson et al.   PLoS One

Reversal of defective lysosomal transport in NPC disease ameliorates liver dysfunction and neurodegeneration in the npc1-/- mouse

(2009) B. Liu et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Metabolic changes detected by proton magnetic resonance spectroscopy in vivo and in vitro in a murin model of Parkinson’s disease, the MPTP-intoxicated mouse

(2008) Carine Chassain et al.   JOURNAL OF NEUROCHEMISTRY

MRI detects therapeutic effects in weanling Niemann-Pick type C mice

(2008) Silvia Lope-Piedrafita et al.   JOURNAL OF NEUROSCIENCE RESEARCH

24 month-treatment with miglustat of three patients with Niemann-Pick disease type C: Follow up using brain spectroscopy

(2008) Damien Galanaud et al.   MOLECULAR GENETICS AND METABOLISM