Journal
JOURNAL OF CLINICAL IMMUNOLOGY
Volume 28, Issue -, Pages S20-S28Publisher
SPRINGER/PLENUM PUBLISHERS
DOI: 10.1007/s10875-007-9161-4
Keywords
autoimmune lymphoproliferative syndrome; caspases; mitochondria; death receptors
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A number of primary immunodeficiency diseases represent a paradox of immunodeficiency and autoimmunity. In this minireview, we present basic concepts of apoptosis and disorder of apoptosis as one of the mechanisms to explain such a paradox between immunodeficiency and autoimmunity, which is exemplified by autoimmune lympho-proliferative syndrome (ALPS).
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