Dystrophins, Utrophins, and Associated Scaffolding Complexes: Role in Mammalian Brain and Implications for Therapeutic Strategies
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Title
Dystrophins, Utrophins, and Associated Scaffolding Complexes: Role in Mammalian Brain and Implications for Therapeutic Strategies
Authors
Keywords
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Journal
JOURNAL OF BIOMEDICINE AND BIOTECHNOLOGY
Volume 2010, Issue -, Pages 1-19
Publisher
Hindawi Limited
Online
2010-06-17
DOI
10.1155/2010/849426
References
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Note: Only part of the references are listed.- Dystrophin Gene Mutation Location and the Risk of Cognitive Impairment in Duchenne Muscular Dystrophy
- (2010) Peter J. Taylor et al. PLoS One
- Parvalbumin-positive GABAergic interneurons are increased in the dorsal hippocampus of the dystrophic mdx mouse
- (2009) Claudia Del Tongo et al. ACTA NEUROPATHOLOGICA
- Mass spectrometry imaging of rat brain sections: nanomolar sensitivity with MALDI versus nanometer resolution by TOF–SIMS
- (2009) Farida Benabdellah et al. ANALYTICAL AND BIOANALYTICAL CHEMISTRY
- The neurobiology of the dystrophin-associated glycoprotein complex
- (2009) Adrian Waite et al. ANNALS OF MEDICINE
- Peptide-Morpholino Conjugate: A Promising Therapeutic for Duchenne Muscular Dystrophy
- (2009) Hong M. Moulton et al. Annals of the New York Academy of Sciences
- Utrophins compensate for Dp71 absence in mdx3cv in adhered platelets
- (2009) Doris Cerecedo et al. BLOOD COAGULATION & FIBRINOLYSIS
- Differential Expression of Utrophin-A and -B Promoters in the Central Nervous System (CNS) of Normal and DystrophicmdxMice
- (2009) Santhosh M. Baby et al. BRAIN PATHOLOGY
- Neurobehavioral Characteristics of Children with Duchenne Muscular Dystrophy
- (2009) Jacobus Donders et al. CHILD NEUROPSYCHOLOGY
- Emerging genetic therapies to treat Duchenne muscular dystrophy
- (2009) Stanley F Nelson et al. CURRENT OPINION IN NEUROLOGY
- Analysis of Dp71 contribution in the severity of mental retardation through comparison of Duchenne and Becker patients differing by mutation consequences on Dp71 expression
- (2009) F. Daoud et al. HUMAN MOLECULAR GENETICS
- Pharmacological activation of PPAR / stimulates utrophin A expression in skeletal muscle fibers and restores sarcolemmal integrity in mature mdx mice
- (2009) P. Miura et al. HUMAN MOLECULAR GENETICS
- Theoretic applicability of antisense-mediated exon skipping for Duchenne muscular dystrophy mutations
- (2009) Annemieke Aartsma-Rus et al. HUMAN MUTATION
- Nonaminoglycoside compounds induce readthrough of nonsense mutations
- (2009) Liutao Du et al. JOURNAL OF EXPERIMENTAL MEDICINE
- A deficit of brain dystrophin 71 impairs hypothalamic osmostat
- (2009) Roza Benabdesselam et al. JOURNAL OF NEUROSCIENCE RESEARCH
- Nitric oxide generated by muscle corrects defects in hippocampal neurogenesis and neural differentiation caused by muscular dystrophy
- (2009) Bo Deng et al. JOURNAL OF PHYSIOLOGY-LONDON
- Local restoration of dystrophin expression with the morpholino oligomer AVI-4658 in Duchenne muscular dystrophy: a single-blind, placebo-controlled, dose-escalation, proof-of-concept study
- (2009) Maria Kinali et al. LANCET NEUROLOGY
- The Roles of the Dystrophin-Associated Glycoprotein Complex at the Synapse
- (2009) Gonneke S. K. Pilgram et al. MOLECULAR NEUROBIOLOGY
- Enhanced Exon-skipping Induced by U7 snRNA Carrying a Splicing Silencer Sequence: Promising Tool for DMD Therapy
- (2009) Aurélie Goyenvalle et al. MOLECULAR THERAPY
- Enhanced homosynaptic LTD in cerebellar Purkinje cells of the dystrophicMDXmouse
- (2009) Jennifer L. Anderson et al. MUSCLE & NERVE
- Direct interaction of Dysbindin with the AP-3 complex via its μ subunit
- (2009) Setsuko Taneichi-Kuroda et al. NEUROCHEMISTRY INTERNATIONAL
- AQP4 gene deletion in mice does not alter blood–brain barrier integrity or brain morphology
- (2009) S. Saadoun et al. NEUROSCIENCE
- Clinical Heterogeneity of Duchenne Muscular Dystrophy (DMD): Definition of Sub-Phenotypes and Predictive Criteria by Long-Term Follow-Up
- (2009) Isabelle Desguerre et al. PLoS One
- Role of Mental Retardation-Associated Dystrophin-Gene Product Dp71 in Excitatory Synapse Organization, Synaptic Plasticity and Behavioral Functions
- (2009) Fatma Daoud et al. PLoS One
- Functional Implication of Dp71 in Osmoregulation and Vascular Permeability of the Retina
- (2009) Abdoulaye Sene et al. PLoS One
- Dystrophin and utrophin have distinct effects on the structural dynamics of actin
- (2009) E. Prochniewicz et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- l-Arginine Decreases Inflammation and Modulates the Nuclear Factor-κB/Matrix Metalloproteinase Cascade in Mdx Muscle Fibers
- (2008) Karim Hnia et al. AMERICAN JOURNAL OF PATHOLOGY
- Genes, plasticity and mental retardation
- (2008) Cyrille Vaillend et al. BEHAVIOURAL BRAIN RESEARCH
- A deficit of brain dystrophin impairs specific amygdala GABAergic transmission and enhances defensive behaviour in mice
- (2008) Masayuki Sekiguchi et al. BRAIN
- Reorganization of Inhibitory Synapses and Increased PSD Length of Perforated Excitatory Synapses in Hippocampal Area CA1 of Dystrophin-Deficient mdx Mice
- (2008) R. Miranda et al. CEREBRAL CORTEX
- Kir4.1 and AQP4 associate with Dp71- and utrophin-DAPs complexes in specific and defined microdomains of Müller retinal glial cell membrane
- (2008) Patrice E. Fort et al. GLIA
- Dystrophin-dependent and -independent AQP4 pools are expressed in the mouse brain
- (2008) Grazia Paola Nicchia et al. GLIA
- Sarcospan reduces dystrophic pathology: stabilization of the utrophin–glycoprotein complex
- (2008) Angela K. Peter et al. JOURNAL OF CELL BIOLOGY
- Neuropsychiatric Disorders in Males With Duchenne Muscular Dystrophy: Frequency Rate of Attention-Deficit Hyperactivity Disorder (ADHD), Autism Spectrum Disorder, and Obsessive—Compulsive Disorder
- (2008) Joseph G. M. Hendriksen et al. JOURNAL OF CHILD NEUROLOGY
- Microutrophin Delivery Through rAAV6 Increases Lifespan and Improves Muscle Function in Dystrophic Dystrophin/Utrophin-deficient Mice
- (2008) Guy L Odom et al. MOLECULAR THERAPY
- Gentamicin treatment in exercised mdx mice: Identification of dystrophin-sensitive pathways and evaluation of efficacy in work-loaded dystrophic muscle
- (2008) Annamaria De Luca et al. NEUROBIOLOGY OF DISEASE
- GABAergic miniature spontaneous activity is increased in the CA1 hippocampal region of dystrophic mdx mice
- (2008) Laura Graciotti et al. NEUROMUSCULAR DISORDERS
- Duchenne muscular dystrophy: A cerebellar disorder?
- (2007) Shana E. Cyrulnik et al. NEUROSCIENCE AND BIOBEHAVIORAL REVIEWS
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