Modeling of Antigenomic Therapy of Mitochondrial Diseases by Mitochondrially Addressed RNA Targeting a Pathogenic Point Mutation in Mitochondrial DNA

Characterization of chemically modified oligonucleotides targeting a pathogenic mutation in human mitochondrial DNA

(2013) Yann Tonin et al.   BIOCHIMIE

Crystal structure of the entire respiratory complex I

(2013) Rozbeh Baradaran et al.   NATURE

Induced tRNA Import into Human Mitochondria: Implication of a Host Aminoacyl-tRNA-Synthetase

(2013) Ali Gowher et al.   PLoS One

The coupling mechanism of respiratory complex I — A structural and evolutionary perspective

(2012) Rouslan G. Efremov et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

EPR detection of two protein-associated ubiquinone components (SQNf and SQNs) in the membrane in situ and in proteoliposomes of isolated bovine heart complex I

(2012) Tomoko Ohnishi et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

RNA-Based Therapeutics: Current Progress and Future Prospects

(2012) John C. Burnett et al.   CHEMISTRY & BIOLOGY

NIH Image to ImageJ: 25 years of image analysis

(2012) Caroline A Schneider et al.   NATURE METHODS

Mitochondrial targeting of recombinant RNAs modulates the level of a heteroplasmic mutation in human mitochondrial DNA associated with Kearns Sayre Syndrome

(2012) Caroline Comte et al.   NUCLEIC ACIDS RESEARCH

Mitochondrial tRNA Import and Its Consequences for Mitochondrial Translation

(2011) André Schneider   Annual Review of Biochemistry

Structure of the membrane domain of respiratory complex I

(2011) Rouslan G. Efremov et al.   NATURE

Correction of the consequences of mitochondrial 3243A>G mutation in the MT-TL1 gene causing the MELAS syndrome by tRNA import into mitochondria

(2011) O. Z. Karicheva et al.   NUCLEIC ACIDS RESEARCH

Organ-specific shifts in mtDNA heteroplasmy following systemic delivery of a mitochondria-targeted restriction endonuclease

(2010) S R Bacman et al.   GENE THERAPY

Allotopic expression of mitochondrial-encoded genes in mammals: achieved goal, undemonstrated mechanism or impossible task?

(2010) Ester Perales-Clemente et al.   NUCLEIC ACIDS RESEARCH

Parkin overexpression selects against a deleterious mtDNA mutation in heteroplasmic cybrid cells

(2010) D.-F. Suen et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Selection of RNA aptamers imported into yeast and human mitochondria

(2010) O. Kolesnikova et al.   RNA

Recent advances in quantitative colocalization analysis: Focus on neuroscience

(2009) Vadim Zinchuk et al.   PROGRESS IN HISTOCHEMISTRY AND CYTOCHEMISTRY

The mitochondrial 13513G>A mutation is associated with Leigh disease phenotypes independent of complex I deficiency in muscle

(2008) Ariel Brautbar et al.   MOLECULAR GENETICS AND METABOLISM

Two distinct structural elements of 5S rRNA are needed for its import into human mitochondria

(2008) A. Smirnov et al.   RNA