Early Alterations of Brain Cellular Energy Homeostasis in Huntington Disease Models

Dysregulated brain creatine kinase is associated with hearing impairment in mouse models of Huntington disease

(2011) Yow-Sien Lin et al.   JOURNAL OF CLINICAL INVESTIGATION

Energy deficit in Huntington disease: why it matters

(2011) Fanny Mochel et al.   JOURNAL OF CLINICAL INVESTIGATION

Quantification of Age-Dependent Somatic CAG Repeat Instability in Hdh CAG Knock-In Mice Reveals Different Expansion Dynamics in Striatum and Liver

(2011) Jong-Min Lee et al.   PLoS One

Reduced creatine kinase as a central and peripheral biomarker in Huntington's disease

(2010) Jinho Kim et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Cell loss in the motor and cingulate cortex correlates with symptomatology in Huntington’s disease

(2010) Doris C. V. Thu et al.   BRAIN

Impaired Brain Creatine Kinase Activity in Huntington’s Disease

(2010) S.F. Zhang et al.   Neurodegenerative Diseases

Detection of early behavioral markers of Huntington's disease in R6/2 mice employing an automated social home cage

(2009) Olga Rudenko et al.   BEHAVIOURAL BRAIN RESEARCH

Combination therapy with Coenzyme Q10and creatine produces additive neuroprotective effects in models of Parkinson’s and Huntington’s Diseases

(2009) Lichuan Yang et al.   JOURNAL OF NEUROCHEMISTRY

Increased glucose metabolism and ATP level in brain tissue of Huntington’s disease transgenic mice

(2008) Judit Oláh et al.   FEBS Journal

AMP-activated protein kinase phosphorylation in brain is dependent on method of killing and tissue preparation

(2008) Matthew T. Scharf et al.   JOURNAL OF NEUROCHEMISTRY

Paradoxical delay in the onset of disease caused by super-long CAG repeat expansions in R6/2 mice

(2008) A Jennifer Morton et al.   NEUROBIOLOGY OF DISEASE

Intergenerational and striatal CAG repeat instability in Huntington's disease knock-in mice involve different DNA repair genes

(2008) Ella Dragileva et al.   NEUROBIOLOGY OF DISEASE

Measurement of sarcoplasmic reticulum Ca2+ ATPase activity using high-performance liquid chromatography

(2007) Jay H. Williams et al.   ANALYTICAL BIOCHEMISTRY

Increased metabolism in the R6/2 mouse model of Huntington’s disease

(2007) Jorien M.M. van der Burg et al.   NEUROBIOLOGY OF DISEASE