LRP130 Protein Remodels Mitochondria and Stimulates Fatty Acid Oxidation

Coordination of cytochrome c oxidase gene expression in the remodelling of skeletal muscle

(2011) A. T. Duggan et al.   JOURNAL OF EXPERIMENTAL BIOLOGY

Progressive adaptation of hepatic ketogenesis in mice fed a high-fat diet

(2010) Nishanth E. Sunny et al.   AMERICAN JOURNAL OF PHYSIOLOGY-ENDOCRINOLOGY AND METABOLISM

LRPPRC is a mitochondrial matrix protein that is conserved in metazoans

(2010) Fredrik H. Sterky et al.   BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS

Leucine-Rich Pentatricopeptide-Repeat Containing Protein Regulates Mitochondrial Transcription

(2010) Neal Sondheimer et al.   BIOCHEMISTRY

Mitochondrial and Nuclear Genomic Responses to Loss ofLRPPRCExpression

(2010) Vishal M. Gohil et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

LRPPRC and SLIRP Interact in a Ribonucleoprotein Complex That Regulates Posttranscriptional Gene Expression in Mitochondria

(2010) Florin Sasarman et al.   MOLECULAR BIOLOGY OF THE CELL

Overexpression of mitochondrial transcription factor A (TFAM) ameliorates delayed neuronal death due to transient forebrain ischemia in mice

(2010) Masaaki Hokari et al.   NEUROPATHOLOGY

Gene Expression Patterns of Oxidative Phosphorylation Complex I Subunits Are Organized in Clusters

(2010) Yael Garbian et al.   PLoS One

Core human mitochondrial transcription apparatus is a regulated two-component system in vitro

(2010) T. E. Shutt et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Connecting Variability in Global Transcription Rate to Mitochondrial Variability

(2010) Ricardo Pires das Neves et al.   PLOS BIOLOGY

Structure and Organization of Mitochondrial Respiratory Complexes: A New Understanding of an Old Subject

(2009) Giorgio Lenaz et al.   ANTIOXIDANTS & REDOX SIGNALING

TFB2 Is a Transient Component of the Catalytic Site of the Human Mitochondrial RNA Polymerase

(2009) Marina Sologub et al.   CELL

RETRACTED: mTERF2 Regulates Oxidative Phosphorylation by Modulating mtDNA Transcription

(2009) Tina Wenz et al.   Cell Metabolism

Molecular dissection of the eukaryotic initiation factor 4E (eIF4E) export-competent RNP

(2009) Ivan Topisirovic et al.   EMBO JOURNAL

The pathophysiology of mitochondrial disease as modeled in the mouse

(2009) D. C. Wallace et al.   GENES & DEVELOPMENT

Elucidation of separate, but collaborative functions of the rRNA methyltransferase-related human mitochondrial transcription factors B1 and B2 in mitochondrial biogenesis reveals new insight into maternally inherited deafness

(2009) Justin Cotney et al.   HUMAN MOLECULAR GENETICS

Energetics, epigenetics, mitochondrial genetics

(2009) Douglas C. Wallace et al.   MITOCHONDRION

Increased muscle PGC-1  expression protects from sarcopenia and metabolic disease during aging

(2009) T. Wenz et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Expression and Maintenance of Mitochondrial DNA

(2008) Gerald S. Shadel   AMERICAN JOURNAL OF PATHOLOGY

Supramolecular organization of protein complexes in the mitochondrial inner membrane

(2008) Janet Vonck et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

Modulation of PGC-1 Coactivator Pathways in Brown Fat Differentiation through LRP130

(2008) Marcus P. Cooper et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Mitochondrial nucleoids undergo remodeling in response to metabolic cues

(2008) M. Kucej et al.   JOURNAL OF CELL SCIENCE

Over-expression of the catalytic core of mitochondrial DNA (mtDNA) polymerase in the nervous system of Drosophila melanogaster reduces median life span by inducing mtDNA depletion

(2008) Francisco Martínez-Azorín et al.   JOURNAL OF NEUROCHEMISTRY

Respiratory Active Mitochondrial Supercomplexes

(2008) Rebeca Acín-Pérez et al.   MOLECULAR CELL