A novel bile acid biosynthesis defect due to a deficiency of peroxisomal ABCD3

Impaired Very Long-chain Acyl-CoA β-Oxidation in Human X-linked Adrenoleukodystrophy Fibroblasts Is a Direct Consequence of ABCD1 Transporter Dysfunction

(2013) Christoph Wiesinger et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Intrinsic acyl-CoA thioesterase activity of a peroxisomal ATP binding cassette transporter is required for transport and metabolism of fatty acids

(2013) Carine De Marcos Lousa et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

The emerging role of acyl-CoA thioesterases and acyltransferases in regulating peroxisomal lipid metabolism

(2012) Mary C. Hunt et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Peroxisomal ABC transporters: Structure, function and role in disease

(2012) Masashi Morita et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

X-linked adrenoleukodystrophy: Clinical, metabolic, genetic and pathophysiological aspects

(2012) Stephan Kemp et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Peroxisomal Fatty Acid Uptake Mechanism inSaccharomyces cerevisiae

(2012) Carlo W. T. van Roermund et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Mammalian peroxisomal ABC transporters: from endogenous substrates to pathology and clinical significance

(2011) Stephan Kemp et al.   BRITISH JOURNAL OF PHARMACOLOGY

Differential substrate specificities of human ABCD1 and ABCD2 in peroxisomal fatty acid β-oxidation

(2010) Carlo W.T. van Roermund et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR AND CELL BIOLOGY OF LIPIDS

Toxicity of peroxisomal C27-bile acid intermediates

(2009) Sacha Ferdinandusse et al.   MOLECULAR GENETICS AND METABOLISM

Pxmp2 Is a Channel-Forming Protein in Mammalian Peroxisomal Membrane

(2009) Aare Rokka et al.   PLoS One

The human peroxisomal ABC half transporter ALDP functions as a homodimer and accepts acyl-CoA esters

(2008) Carlo W. T. van Roermund et al.   FASEB JOURNAL

RNAi-mediated silencing of ABCD3 gene expression in rat C6 glial cells: A model system to study PMP70 function

(2007) Rita Di Benedetto et al.   NEUROCHEMISTRY INTERNATIONAL