The cytochrome b p.278Y>C mutation causative of a multisystem disorder enhances superoxide production and alters supramolecular interactions of respiratory chain complexes

Mechanism of tiron as scavenger of superoxide ions and free electrons

(2012) Fatai A. Taiwo   SPECTROSCOPY-AN INTERNATIONAL JOURNAL

The effects of idebenone on mitochondrial bioenergetics

(2011) Valentina Giorgio et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Searching for a needle in the haystack: Comparing six methods to evaluate heteroplasmy in difficult sequence context

(2011) Ivana Kurelac et al.   BIOTECHNOLOGY ADVANCES

Arrangement of electron transport chain components in bovine mitochondrial supercomplex I1III2IV1

(2011) Thorsten Althoff et al.   EMBO JOURNAL

Mitochondrial complex III stabilizes complex I in the absence of NDUFS4 to provide partial activity

(2011) M. A. Calvaruso et al.   HUMAN MOLECULAR GENETICS

Loss of a Conserved Tyrosine Residue of CytochromebInduces Reactive Oxygen Species Production by Cytochromebc1

(2011) Dong-Woo Lee et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Complex III staining in blue native polyacrylamide gels

(2011) Joél Smet et al.   JOURNAL OF INHERITED METABOLIC DISEASE

Structure and Organization of Mitochondrial Respiratory Complexes: A New Understanding of an Old Subject

(2009) Giorgio Lenaz et al.   ANTIOXIDANTS & REDOX SIGNALING

Mitochondrial DNA mutations and human disease

(2009) Helen A.L. Tuppen et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

Mitochondrial Disorders in the Nervous System

(2008) Salvatore DiMauro et al.   Annual Review of Neuroscience

Respiratory-chain diseases related to complex III deficiency

(2008) Paule Bénit et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

The antioxidant function of Bcl-2 preserves cytoskeletal stability of cells with defective respiratory complex I

(2008) A. M. Porcelli et al.   CELLULAR AND MOLECULAR LIFE SCIENCES

Respiratory Complex I Dysfunction Due to Mitochondrial DNA Mutations Shifts the Voltage Threshold for Opening of the Permeability Transition Pore toward Resting Levels

(2008) Anna Maria Porcelli et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Electrophoresis techniques to investigate defects in oxidative phosphorylation

(2008) Maria Antonietta Calvaruso et al.   METHODS

Respiratory Active Mitochondrial Supercomplexes

(2008) Rebeca Acín-Pérez et al.   MOLECULAR CELL