Defective mitochondrial disulfide relay system, altered mitochondrial morphology and function in Huntington's disease

Mitophagy, mitochondrial dynamics and the general stress response in yeast

(2012) Matthias Müller et al.   BIOCHEMICAL SOCIETY TRANSACTIONS

Mitochondrial DNA damage Is associated with reduced mitochondrial bioenergetics in Huntington's disease

(2012) Almas Siddiqui et al.   FREE RADICAL BIOLOGY AND MEDICINE

Mechanisms of Protein Sorting in Mitochondria

(2012) D. Stojanovski et al.   Cold Spring Harbor Perspectives in Biology

A scaffold of accessory subunits links the peripheral arm and the distal proton-pumping module of mitochondrial complex I

(2011) Heike Angerer et al.   BIOCHEMICAL JOURNAL

Cyclin D1 Inhibits Mitochondrial Activity in B Cells

(2011) G. Tchakarska et al.   CANCER RESEARCH

Mutant huntingtin's interaction with mitochondrial protein Drp1 impairs mitochondrial biogenesis and causes defective axonal transport and synaptic degeneration in Huntington's disease

(2011) U. P. Shirendeb et al.   HUMAN MOLECULAR GENETICS

During autophagy mitochondria elongate, are spared from degradation and sustain cell viability

(2011) Ligia C. Gomes et al.   NATURE CELL BIOLOGY

Mutant huntingtin binds the mitochondrial fission GTPase dynamin-related protein-1 and increases its enzymatic activity

(2011) Wenjun Song et al.   NATURE MEDICINE

A new role of NUAK1: directly phosphorylating p53 and regulating cell proliferation

(2011) X Hou et al.   ONCOGENE

Functional annotation of heart enriched mitochondrial genes GBAS and CHCHD10 through guilt by association

(2010) Ruben S.R.M. Martherus et al.   BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS

Mitochondrial matters of the brain: the role in Huntington’s disease

(2010) C. Turner et al.   JOURNAL OF BIOENERGETICS AND BIOMEMBRANES

ChChd3, an Inner Mitochondrial Membrane Protein, Is Essential for Maintaining Crista Integrity and Mitochondrial Function

(2010) Manjula Darshi et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Genome-wide analysis of eukaryotic twin CX9C proteins

(2010) Gabriele Cavallaro   Molecular BioSystems

PINK1 Is Selectively Stabilized on Impaired Mitochondria to Activate Parkin

(2010) Derek P. Narendra et al.   PLOS BIOLOGY

The Mitochondrial Disulfide Relay System Protein GFER Is Mutated in Autosomal-Recessive Myopathy with Cataract and Combined Respiratory-Chain Deficiency

(2009) Alessio Di Fonzo et al.   AMERICAN JOURNAL OF HUMAN GENETICS

Nitration of tyrosine residues 368 and 345 in the β-subunit elicits FoF1-ATPase activity loss

(2009) Yasuko Fujisawa et al.   BIOCHEMICAL JOURNAL

Genetic causes of mitochondrial DNA depletion in humans

(2009) Agnès Rötig et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Complex II inhibition by 3-NP causes mitochondrial fragmentation and neuronal cell death via an NMDA- and ROS-dependent pathway

(2009) G Liot et al.   CELL DEATH AND DIFFERENTIATION

Impaired PGC-1α function in muscle in Huntington's disease

(2009) Rajnish K. Chaturvedi et al.   HUMAN MOLECULAR GENETICS

A novel intermembrane space–targeting signal docks cysteines onto Mia40 during mitochondrial oxidative folding

(2009) Dionisia P. Sideris et al.   JOURNAL OF CELL BIOLOGY

Polymorphism of HD and UCHL-1 genes in Huntington’s disease

(2009) Er-he Xu et al.   JOURNAL OF CLINICAL NEUROSCIENCE

IF1: setting the pace of the F1Fo-ATP synthase

(2009) Michelangelo Campanella et al.   TRENDS IN BIOCHEMICAL SCIENCES

Mitochondrial Disorders in the Nervous System

(2008) Salvatore DiMauro et al.   Annual Review of Neuroscience

The Erv1–Mia40 disulfide relay system in the intermembrane space of mitochondria

(2008) Kai Hell   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH