Characterization of inclusion bodies with cytoprotective properties formed by seipinopathy-linked mutant seipin

Inclusion bodies and autophagosomes: Are ER-derived protective organelles different than classical autophagosomes?

(2014) Susana Granell et al.   Autophagy

N88S seipin mutant transgenic mice develop features of seipinopathy/BSCL2-related motor neuron disease via endoplasmic reticulum stress

(2011) Takuya Yagi et al.   HUMAN MOLECULAR GENETICS

Seipin ablation in mice results in severe generalized lipodystrophy

(2011) X. Cui et al.   HUMAN MOLECULAR GENETICS

Role of calnexin in the ER quality control and productive folding of CFTR; differential effect of calnexin knockout on wild-type and ΔF508 CFTR

(2008) Tsukasa Okiyoneda et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

Seipinopathy: a novel endoplasmic reticulum stress-associated disease

(2008) Daisuke Ito et al.   BRAIN

Characterization of seipin/BSCL2, a protein associated with spastic paraplegia 17

(2008) Daisuke Ito et al.   NEUROBIOLOGY OF DISEASE

Sequestration of Mutated α1-Antitrypsin into Inclusion Bodies Is a Cell-protective Mechanism to Maintain Endoplasmic Reticulum Function

(2007) Susana Granell et al.   MOLECULAR BIOLOGY OF THE CELL

Development and Characterisation of a Glutamate-Sensitive Motor Neurone Cell Line

(2003) Christopher J. Eggett et al.   JOURNAL OF NEUROCHEMISTRY