Ku70 regulates Bax-mediated pathogenesis in laminin- 2-deficient human muscle cells and mouse models of congenital muscular dystrophy

LAMA2 gene analysis in a cohort of 26 congenital muscular dystrophy patients

(2009) J Oliveira et al.   CLINICAL GENETICS

Cyclosporine A treatment for Ullrich congenital muscular dystrophy: a cellular study of mitochondrial dysfunction and its rescue

(2008) D. Hicks et al.   BRAIN

SIRT3 Is a Stress-Responsive Deacetylase in Cardiomyocytes That Protects Cells from Stress-Mediated Cell Death by Deacetylation of Ku70

(2008) N. R. Sundaresan et al.   MOLECULAR AND CELLULAR BIOLOGY

Genetic and pharmacologic inhibition of mitochondrial-dependent necrosis attenuates muscular dystrophy

(2008) Douglas P Millay et al.   NATURE MEDICINE

Bax-inhibiting peptide protects glutamate-induced cerebellar granule cell death by blocking Bax translocation

(2008) Takayuki Iriyama et al.   NEUROSCIENCE LETTERS

Regulation of the proapoptotic factor Bax by Ku70-dependent deubiquitylation

(2008) Avigail D. Amsel et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Drug-induced readthrough of premature stop codons leads to the stabilization of laminin α2 chain mRNA in CMD myotubes

(2007) Valérie Allamand et al.   JOURNAL OF GENE MEDICINE