Syndrome of Combined Pulmonary Fibrosis and Emphysema: An Official ATS/ERS/JRS/ALAT Research Statement

Recommandations pratiques pour le diagnostic et la prise en charge de la fibrose pulmonaire idiopathique – Actualisation 2021. Version courte

(2022) V. Cottin et al.   REVUE DES MALADIES RESPIRATOIRES

Inhaled Treprostinil in Pulmonary Hypertension Due to Interstitial Lung Disease

(2021) Aaron Waxman et al.   NEW ENGLAND JOURNAL OF MEDICINE

Group 3 Pulmonary Hypertension

(2021) Andrea M. Shioleno et al.   CLINICS IN CHEST MEDICINE

Impact of lung morphology on clinical outcomes with riociguat in patients with pulmonary hypertension and idiopathic interstitial pneumonia: A post hoc subgroup analysis of the RISE-IIP study

(2021) Steven D. Nathan et al.   JOURNAL OF HEART AND LUNG TRANSPLANTATION

Cardiopulmonary Exercise Testing in Combined Pulmonary Fibrosis and Emphysema

(2021) Michael Westhoff et al.   RESPIRATION

Tobacco smoking and risk for pulmonary fibrosis: A prospective cohort study in UK Biobank

(2021) Vanesa Bellou et al.   CHEST

Pirfenidone in patients with progressive fibrotic interstitial lung diseases other than idiopathic pulmonary fibrosis (RELIEF): a double-blind, randomised, placebo-controlled, phase 2b trial

(2021) Jürgen Behr et al.   Lancet Respiratory Medicine

Small Airway Reduction and Fibrosis is an Early Pathologic Feature of Idiopathic Pulmonary Fibrosis

(2021) Kohei Ikezoe et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Diagnostic Accuracy of Endobronchial Optical Coherence Tomography for the Microscopic Diagnosis of Usual Interstitial Pneumonia

(2021) Sreyankar Nandy et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Clinical Features and Outcomes of Combined Pulmonary Fibrosis and Emphysema After Lung Transplantation

(2021) Tsuyoshi Takahashi et al.   CHEST

Lung cancer

(2021) Alesha A Thai et al.   LANCET

Combined Pulmonary Fibrosis Emphysema: Role of Cigarette Smoking and Pulmonary Hypertension in a Rural Cohort

(2021) Rahul Sangani et al.   International Journal of Chronic Obstructive Pulmonary Disease

Inhaled treprostinil and forced vital capacity in patients with interstitial lung disease and associated pulmonary hypertension: a post-hoc analysis of the INCREASE study

(2021) Steven D Nathan et al.   Lancet Respiratory Medicine

Differential Genomic Profile in TERT, DSP, and FAM13A Between COPD Patients With Emphysema, IPF, and CPFE Syndrome

(2021) Javier Guzmán-Vargas et al.   Frontiers in Medicine

Prognostic Significance of Pulmonary Artery to Aorta Ratio and Other CT Markers in Pulmonary Fibrosis With and Without Emphysema

(2021) F. Zeba et al.   LUNG

Imaging intact human organs with local resolution of cellular structures using hierarchical phase-contrast tomography

(2021) C. L. Walsh et al.   NATURE METHODS

The disconnect between visual assessment of air trapping and lung physiology for assessment of small airway disease in scleroderma-related interstitial lung disease: An observation from the Scleroderma Lung Study II Cohort

(2021) Sangmee Sharon Bae et al.   Journal of Scleroderma and Related Disorders

Prolidase deficiency: a new genetic cause of combined pulmonary fibrosis and emphysema syndrome in the adult

(2020) Vincent Cottin et al.   EUROPEAN RESPIRATORY JOURNAL

Nintedanib in patients with progressive fibrosing interstitial lung diseases—subgroup analyses by interstitial lung disease diagnosis in the INBUILD trial: a randomised, double-blind, placebo-controlled, parallel-group trial

(2020) Athol U Wells et al.   Lancet Respiratory Medicine

Risk prediction model in rheumatoid arthritis‐associated interstitial lung disease

(2020) Ho Cheol Kim et al.   RESPIROLOGY

Prognosis of patients with acute exacerbation of combined pulmonary fibrosis and emphysema: a retrospective single-centre study

(2020) Yuichi Ikuyama et al.   BMC Pulmonary Medicine

Diagnosis of Hypersensitivity Pneumonitis in Adults. An Official ATS/JRS/ALAT Clinical Practice Guideline

(2020) Ganesh Raghu et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Progressive fibrosing interstitial lung disease: treatable traits and therapeutic strategies

(2020) Amornpun Wongkarnjana et al.   CURRENT OPINION IN PULMONARY MEDICINE

Occupational and environmental risk factors for idiopathic pulmonary fibrosis in Australia: case–control study

(2020) Michael J Abramson et al.   THORAX

The Gly82Ser mutation in AGER contributes to pathogenesis of pulmonary fibrosis in combined pulmonary fibrosis and emphysema (CPFE) in Japanese patients

(2020) Takumi Kinjo et al.   Scientific Reports

Interstitial lung abnormalities detected incidentally on CT: a Position Paper from the Fleischner Society

(2020) Hiroto Hatabu et al.   Lancet Respiratory Medicine

Relationship Between Combination of Pulmonary Fibrosis and Emphysema, ANCA, and Vasculitis

(2020) David Blanco Alba et al.   CHEST

Prognostic significance of red cell distribution width in idiopathic pulmonary fibrosis and combined pulmonary fibrosis emphysema

(2020) Aslıhan Gürün Kaya et al.   MEDICAL PRINCIPLES AND PRACTICE

Spectrum of Fibrotic Lung Diseases

(2020) Marlies Wijsenbeek et al.   NEW ENGLAND JOURNAL OF MEDICINE

Telomere length and risk of idiopathic pulmonary fibrosis and chronic obstructive pulmonary disease: a mendelian randomisation study

(2020) Anna Duckworth et al.   Lancet Respiratory Medicine

Therapeutic effects of nintedanib are not influenced by emphysema in the INPULSIS trials

(2019) Vincent Cottin et al.   EUROPEAN RESPIRATORY JOURNAL

Interstitial lung abnormalities: erecting fences in the path towards advanced pulmonary fibrosis

(2019) Gary M Hunninghake   THORAX

Experimental and quantitative imaging techniques in interstitial lung disease

(2019) Nicholas D Weatherley et al.   THORAX

Genetic landscape of chronic obstructive pulmonary disease identifies heterogeneous cell-type and phenotype associations

(2019) Phuwanat Sakornsakolpat et al.   NATURE GENETICS

Distribution of emphysema and fibrosis in idiopathic pulmonary fibrosis with coexisting emphysema

(2019) Yoshiaki Kinoshita et al.   HISTOPATHOLOGY

Design of IPF Clinical Trials in the Era of Approved Therapies

(2019) Robert J Kaner et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Exploring the cross-phenotype network region of disease modules reveals concordant and discordant pathways between chronic obstructive pulmonary disease and idiopathic pulmonary fibrosis

(2019) Arda Halu et al.   HUMAN MOLECULAR GENETICS

Airway Microstructure in Idiopathic Pulmonary Fibrosis: Assessment at Hyperpolarized 3He Diffusion-weighted MRI

(2019) Ho-Fung Chan et al.   RADIOLOGY

Lung function trajectories in health and disease

(2019) Alvar Agusti et al.   Lancet Respiratory Medicine

Surgical and endoscopic interventions that reduce lung volume for emphysema: a systemic review and meta-analysis

(2019) Wouter H van Geffen et al.   Lancet Respiratory Medicine

Rare Protein-altering Telomere-related Gene Variants in Patients with Chronic Hypersensitivity Pneumonitis

(2019) Brett Ley et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Fibrocyte accumulation in the airway walls of COPD patients

(2019) Isabelle Dupin et al.   EUROPEAN RESPIRATORY JOURNAL

The Role of Telomerase and Telomeres in Interstitial Lung Diseases: From Molecules to Clinical Implications

(2019) Nissim Arish et al.   INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES

Clinical features and prognosis of patients with idiopathic pulmonary fibrosis and chronic obstructive pulmonary disease

(2019) S. H. Lee et al.   INTERNATIONAL JOURNAL OF TUBERCULOSIS AND LUNG DISEASE

Predicting clinical outcome with phenotypic clusters using quantitative CT fibrosis and emphysema features in patients with idiopathic pulmonary fibrosis

(2019) So Hyeon Bak et al.   PLoS One

Combined pulmonary fibrosis and emphysema: How does cohabitation affect respiratory functions?

(2019) Fatma Çiftci et al.   Advances in Medical Sciences

Update on the Pathogenesis of Chronic Obstructive Pulmonary Disease

(2019) Alvar Agustí et al.   NEW ENGLAND JOURNAL OF MEDICINE

Nintedanib in Progressive Fibrosing Interstitial Lung Diseases

(2019) Kevin R. Flaherty et al.   NEW ENGLAND JOURNAL OF MEDICINE

Riociguat for idiopathic interstitial pneumonia-associated pulmonary hypertension (RISE-IIP): a randomised, placebo-controlled phase 2b study

(2019) Steven D Nathan et al.   Lancet Respiratory Medicine

Pirfenidone in patients with unclassifiable progressive fibrosing interstitial lung disease: a double-blind, randomised, placebo-controlled, phase 2 trial

(2019) Toby M Maher et al.   Lancet Respiratory Medicine

Progression of probable UIP and UIP on HRCT

(2019) Mary Salvatore et al.   CLINICAL IMAGING

Uncovering the mechanisms of exertional dyspnoea in combined pulmonary fibrosis and emphysema

(2019) Camila M. Costa et al.   EUROPEAN RESPIRATORY JOURNAL

Combined pulmonary fibrosis and emphysema and idiopathic pulmonary fibrosis in non-small cell lung cancer: impact on survival and acute exacerbation

(2019) Sung Woo Moon et al.   BMC Pulmonary Medicine

The effect of emphysema on survival in patients with idiopathic pulmonary fibrosis

(2019) Ruay-Sheng Lai et al.   Journal of the Chinese Medical Association

Upregulation and Nuclear Location of MMP28 in Alveolar Epithelium of Idiopathic Pulmonary Fibrosis

(2018) Mariel Maldonado et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Pulmonary phenotypes associated with genetic variation in telomere-related genes

(2018) Thijs W. Hoffman et al.   CURRENT OPINION IN PULMONARY MEDICINE

Combined pulmonary fibrosis and emphysema predicts recurrence following surgery in patients with stage I non-small cell lung cancer

(2018) Ryo Maeda et al.   MEDICAL ONCOLOGY

Interstitial Features at Chest CT Enhance the Deleterious Effects of Emphysema in the COPDGene Cohort

(2018) Samuel Y. Ash et al.   RADIOLOGY

Functional associations of pleuroparenchymal fibroelastosis and emphysema with hypersensitivity pneumonitis

(2018) Joseph Jacob et al.   RESPIRATORY MEDICINE

Emphysematous change with scleroderma-associated interstitial lung disease: the potential contribution of vasculopathy?

(2018) Hideaki Yamakawa et al.   BMC Pulmonary Medicine

Prevalence and Effects of Emphysema in Never-Smokers with Rheumatoid Arthritis Interstitial Lung Disease

(2018) Joseph Jacob et al.   EBioMedicine

Diagnosis of Idiopathic Pulmonary Fibrosis. An Official ATS/ERS/JRS/ALAT Clinical Practice Guideline

(2018) Ganesh Raghu et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Why an Aging Smoker Lung Develops IPF and Not COPD?

(2018) Moisés Selman et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Presence of lung cancer and high gender, age, and physiology score as predictors of acute exacerbation in combined pulmonary fibrosis and emphysema

(2018) Jee Youn Oh et al.   MEDICINE

Nintedanib plus Sildenafil in Patients with Idiopathic Pulmonary Fibrosis

(2018) Martin Kolb et al.   NEW ENGLAND JOURNAL OF MEDICINE

Identification of MMP28 as a biomarker for the differential diagnosis of idiopathic pulmonary fibrosis

(2018) Mariel Maldonado et al.   PLoS One

Effects of emphysema on physiological and prognostic characteristics of lung function in idiopathic pulmonary fibrosis

(2018) Hee-Young Yoon et al.   RESPIROLOGY

Pulmonary hypertension in chronic lung disease and hypoxia

(2018) Steven D. Nathan et al.   EUROPEAN RESPIRATORY JOURNAL

Combined pulmonary fibrosis and emphysema as a clinicoradiologic entity: Characterization of presenting lung fibrosis and implications for survival

(2018) Mohammad Alsumrain et al.   RESPIRATORY MEDICINE

Combined pulmonary fibrosis and emphysema in systemic sclerosis: A syndrome associated with heavy morbidity and mortality

(2018) N. Champtiaux et al.   SEMINARS IN ARTHRITIS AND RHEUMATISM

Combined pulmonary fibrosis and emphysema: bad and ugly all the same?

(2017) Vincent Cottin   EUROPEAN RESPIRATORY JOURNAL

Shared genetic predisposition in rheumatoid arthritis-interstitial lung disease and familial pulmonary fibrosis

(2017) Pierre-Antoine Juge et al.   EUROPEAN RESPIRATORY JOURNAL

Functional and prognostic effects when emphysema complicates idiopathic pulmonary fibrosis

(2017) Joseph Jacob et al.   EUROPEAN RESPIRATORY JOURNAL

Histological analysis of vasculopathy associated with pulmonary hypertension in combined pulmonary fibrosis and emphysema: comparison with idiopathic pulmonary fibrosis or emphysema alone

(2017) Nobuyasu Awano et al.   HISTOPATHOLOGY

Genetic polymorphism in matrix metalloproteinase-9 and transforming growth factor-β1 and susceptibility to combined pulmonary fibrosis and emphysema in a Chinese population

(2017) Ling Xu et al.   KAOHSIUNG JOURNAL OF MEDICAL SCIENCES

Genetic loci associated with chronic obstructive pulmonary disease overlap with loci for lung function and pulmonary fibrosis

(2017) Brian D Hobbs et al.   NATURE GENETICS

Urinary desmosine is associated with emphysema severity and frequent exacerbation in patients with COPD

(2017) Changhwan Kim et al.   RESPIROLOGY

Likelihood of pulmonary hypertension in patients with idiopathic pulmonary fibrosis and emphysema

(2017) Joseph Jacob et al.   RESPIROLOGY

French practical guidelines for the diagnosis and management of idiopathic pulmonary fibrosis – 2017 update. Full-length version

(2017) V. Cottin et al.   REVUE DES MALADIES RESPIRATOIRES

The prognostic impact of combined pulmonary fibrosis and emphysema in patients with clinical stage IA non-small cell lung cancer

(2017) Tomoyoshi Takenaka et al.   SURGERY TODAY

Cáncer de pulmón en pacientes con combinación de fibrosis pulmonar y enfisema y fibrosis pulmonar idiopática. Estudio descriptivo en una serie española

(2017) Karina Portillo et al.   ARCHIVOS DE BRONCONEUMOLOGIA

Serial changes and prognostic implications of CT findings in combined pulmonary fibrosis and emphysema: comparison with fibrotic idiopathic interstitial pneumonias alone

(2016) Geewon Lee et al.   ACTA RADIOLOGICA

Gene expression profiling of epigenetic chromatin modification enzymes and histone marks by cigarette smoke: implications for COPD and lung cancer

(2016) Isaac K. Sundar et al.   AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

Integrated Genomics Reveals Convergent Transcriptomic Networks Underlying Chronic Obstructive Pulmonary Disease and Idiopathic Pulmonary Fibrosis

(2016) Rebecca L. Kusko et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Surgical Outcomes of Lung Cancer Patients with Combined Pulmonary Fibrosis and Emphysema and Those with Idiopathic Pulmonary Fibrosis without Emphysema

(2016) Seijiro Sato et al.   Annals of Thoracic and Cardiovascular Surgery

Impact of Thin-Section Computed Tomography-Determined Combined Pulmonary Fibrosis and Emphysema on Outcomes Among Patients With Resected Lung Cancer

(2016) Naozumi Hashimoto et al.   ANNALS OF THORACIC SURGERY

Lung cancer in patients with combined pulmonary fibrosis and emphysema revisited with the 2015 World Health Organization classification of lung tumors

(2016) Li Gao et al.   Clinical Respiratory Journal

Telomere-related lung fibrosis is diagnostically heterogeneous but uniformly progressive

(2016) Chad A. Newton et al.   EUROPEAN RESPIRATORY JOURNAL

Treatable traits: toward precision medicine of chronic airway diseases

(2016) Alvar Agusti et al.   EUROPEAN RESPIRATORY JOURNAL

Identification of Clinical Phenotypes in Idiopathic Interstitial Pneumonia with Pulmonary Emphysema

(2016) Suguru Sato et al.   INTERNAL MEDICINE

Association Between Interstitial Lung Abnormalities and All-Cause Mortality

(2016) Rachel K. Putman et al.   JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION

ABCA3 mutations led to pulmonary fibrosis and emphysema with pulmonary hypertension in an 8-year-old girl

(2016) Chiharu Ota et al.   PEDIATRIC PULMONOLOGY

Differentiating Smoking-Related Interstitial Fibrosis (SRIF) from Usual Interstitial Pneumonia (UIP) with Emphysema Using CT Features Based on Pathologically Proven Cases

(2016) Kum Ju Chae et al.   PLoS One

Loss-of-function mutations in the RNA biogenesis factor NAF1 predispose to pulmonary fibrosis–emphysema

(2016) Susan E. Stanley et al.   Science Translational Medicine

Internal migration and maternal health service utilisation in Jiangsu, China

(2016) Hai Gu et al.   TROPICAL MEDICINE & INTERNATIONAL HEALTH

Combined pulmonary fibrosis and emphysema: a retrospective analysis of clinical characteristics, treatment and prognosis

(2016) Lijuan Zhang et al.   BMC Pulmonary Medicine

Combined Pulmonary Fibrosis and Emphysema in Scleroderma-Related Lung Disease Has a Major Confounding Effect on Lung Physiology and Screening for Pulmonary Hypertension

(2016) K. M. Antoniou et al.   Arthritis & Rheumatology

The histological characteristics and clinical outcomes of lung cancer in patients with combined pulmonary fibrosis and emphysema

(2016) Meng Zhang et al.   Cancer Medicine

Lung Cancer in Combined Pulmonary Fibrosis and Emphysema: A Systematic Review and Meta-Analysis

(2016) Hyun Jung Koo et al.   PLoS One

Quantitative CT Evaluation in Patients with Combined Pulmonary Fibrosis and Emphysema

(2015) Shin Matsuoka et al.   ACADEMIC RADIOLOGY

Detection of Rheumatoid Arthritis–Interstitial Lung Disease Is Enhanced by Serum Biomarkers

(2015) Tracy J. Doyle et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Fibrocytes Contribute to Inflammation and Fibrosis in Chronic Hypersensitivity Pneumonitis through Paracrine Effects

(2015) Carolina García de Alba et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Usual interstitial pneumonia end-stage features from explants with radiologic and pathological correlations

(2015) Maud Rabeyrin et al.   Annals of Diagnostic Pathology

Surgical Outcomes of Lung Cancer in Patients with Combined Pulmonary Fibrosis and Emphysema

(2015) Takahiro Mimae et al.   ANNALS OF SURGICAL ONCOLOGY

Relationship between fibroblastic foci profusion and high resolution CT morphology in fibrotic lung disease

(2015) Simon L F Walsh et al.   BMC Medicine

Visually stratified CT honeycombing as a survival predictor in combined pulmonary fibrosis and emphysema

(2015) Yong Seek Kim et al.   BRITISH JOURNAL OF RADIOLOGY

Telomere Length in Interstitial Lung Diseases

(2015) Reinier Snetselaar et al.   CHEST

Prevalence and progression of combined pulmonary fibrosis and emphysema in asymptomatic smokers: A case-control study

(2015) Kum Ju Chae et al.   EUROPEAN RADIOLOGY

2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension

(2015) Nazzareno Galiè et al.   EUROPEAN RESPIRATORY JOURNAL

Morphological Disease Progression of Combined Pulmonary Fibrosis and Emphysema

(2015) Shin Matsuoka et al.   JOURNAL OF COMPUTER ASSISTED TOMOGRAPHY

Neutrophil elastase promotes myofibroblast differentiation in lung fibrosis

(2015) Alyssa D. Gregory et al.   JOURNAL OF LEUKOCYTE BIOLOGY

Matrix metalloproteinases in destructive lung disease

(2015) A. McGarry Houghton   MATRIX BIOLOGY

Forced Vital Capacity in Idiopathic Pulmonary Fibrosis — FDA Review of Pirfenidone and Nintedanib

(2015) Banu A. Karimi-Shah et al.   NEW ENGLAND JOURNAL OF MEDICINE

CT-Definable Subtypes of Chronic Obstructive Pulmonary Disease: A Statement of the Fleischner Society

(2015) David A. Lynch et al.   RADIOLOGY

Outcomes of lung cancer resection for patients with combined pulmonary fibrosis and emphysema

(2015) Mariko Fukui et al.   SURGERY TODAY

Interobserver agreement for the ATS/ERS/JRS/ALAT criteria for a UIP pattern on CT

(2015) Simon L F Walsh et al.   THORAX

Mice with Pulmonary Fibrosis Driven by Telomere Dysfunction

(2015) Juan M. Povedano et al.   Cell Reports

Global and regional estimates of COPD prevalence: Systematic review and meta–analysis

(2015) Davies Adeloye et al.   Journal of Global Health

Pulmonary Hypertension in Patients with Chronic Fibrosing Idiopathic Interstitial Pneumonias

(2015) Marius M. Hoeper et al.   PLoS One

Is Telomeropathy the Explanation for Combined Pulmonary Fibrosis and Emphysema Syndrome?: Report of a Family with TERT Mutation

(2014) Hilario Nunes et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Reply: Telomerase Makes Connections between Pulmonary Fibrosis and Emphysema

(2014) Mary Armanios   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Association between Occupational Exposure and Lung Function, Respiratory Symptoms, and High-Resolution Computed Tomography Imaging in COPDGene

(2014) Nathaniel Marchetti et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Revealing the Pathogenic and Aging-related Mechanisms of the Enigmatic Idiopathic Pulmonary Fibrosis. An Integral Model

(2014) Moisés Selman et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Prognostic significance of combined pulmonary fibrosis and emphysema in patients with resected non-small-cell lung cancer: a retrospective cohort study

(2014) S. Kumagai et al.   EUROPEAN JOURNAL OF CARDIO-THORACIC SURGERY

Telomerase mutations in smokers with severe emphysema

(2014) Susan E. Stanley et al.   JOURNAL OF CLINICAL INVESTIGATION

Lung Cancer in Combined Pulmonary Fibrosis and Emphysema: A Series of 47 Western Patients

(2014) Nicolas Girard et al.   Journal of Thoracic Oncology

Clinical features, anti-cancer treatments and outcomes of lung cancer patients with combined pulmonary fibrosis and emphysema

(2014) Yuji Minegishi et al.   LUNG CANCER

A Phase 3 Trial of Pirfenidone in Patients with Idiopathic Pulmonary Fibrosis

(2014) Talmadge E. King et al.   NEW ENGLAND JOURNAL OF MEDICINE

Efficacy and Safety of Nintedanib in Idiopathic Pulmonary Fibrosis

(2014) Luca Richeldi et al.   NEW ENGLAND JOURNAL OF MEDICINE

The Value of CT for Disease Detection and Prognosis Determination in Combined Pulmonary Fibrosis and Emphysema (CPFE)

(2014) Seung Hee Choi et al.   PLoS One

Idiopathic Pulmonary Fibrosis With Emphysema: Evidence of Synergy Among Emphysema and Idiopathic Pulmonary Fibrosis in Smokers

(2014) P. D. Mitchell et al.   Respiratory Care

Lung cancer risk among patients with combined pulmonary fibrosis and emphysema

(2014) Nakwon Kwak et al.   RESPIRATORY MEDICINE

Haemodynamic changes in pulmonary hypertension in patients with interstitial lung disease treated with PDE-5 inhibitors

(2014) Gregor S. Zimmermann et al.   RESPIROLOGY

An autopsy study of combined pulmonary fibrosis and emphysema: correlations among clinical, radiological, and pathological features

(2014) Minoru Inomata et al.   BMC Pulmonary Medicine

Effects of smoking, gender and occupational exposure on the risk of severe pulmonary fibrosis: a population-based case-control study

(2014) Magnus Ekström et al.   BMJ Open

Pulmonary function impairment in patients with combined pulmonary fibrosis and emphysema with and without airflow obstruction

(2014) Yoshiaki Kitaguchi et al.   International Journal of Chronic Obstructive Pulmonary Disease

SFTPCMutations in Patients with Familial Pulmonary Fibrosis: Combined with Emphysema?

(2013) Vincent Cottin et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

An Official American Thoracic Society/European Respiratory Society Statement: Update of the International Multidisciplinary Classification of the Idiopathic Interstitial Pneumonias

(2013) William D. Travis et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Treatment of Idiopathic Pulmonary Fibrosis With Ambrisentan

(2013) Ganesh Raghu   ANNALS OF INTERNAL MEDICINE

Clinical Features and Outcomes in Combined Pulmonary Fibrosis and Emphysema in Idiopathic Pulmonary Fibrosis

(2013) Christopher J. Ryerson et al.   CHEST

Combined pulmonary fibrosis and emphysema syndrome associated with ABCA3 mutations

(2013) R. Epaud et al.   EUROPEAN RESPIRATORY JOURNAL

Matrix Metalloproteinase (MMP)-1 Induces Lung Alveolar Epithelial Cell Migration and Proliferation, Protects from Apoptosis, and Represses Mitochondrial Oxygen Consumption

(2013) Iliana Herrera et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Smoking-related interstitial fibrosis (SRIF): pathologic findings and distinction from other chronic fibrosing lung diseases

(2013) Anna-Luise A Katzenstein   JOURNAL OF CLINICAL PATHOLOGY

Relationship Between Quantitative CT Metrics and Pulmonary Function in Combined Pulmonary Fibrosis and Emphysema

(2013) Katsutoshi Ando et al.   LUNG

Genome-wide association study identifies multiple susceptibility loci for pulmonary fibrosis

(2013) Tasha E Fingerlin et al.   NATURE GENETICS

Airspace enlargement with fibrosis shows characteristic histology and immunohistology different from usual interstitial pneumonia, nonspecific interstitial pneumonia and centrilobular emphysema

(2013) Tsutomu Yamada et al.   PATHOLOGY INTERNATIONAL

Interstitial Lung Abnormalities in a CT Lung Cancer Screening Population: Prevalence and Progression Rate

(2013) Gong Yong Jin et al.   RADIOLOGY

Annual changes in pulmonary function in combined pulmonary fibrosis and emphysema: Over a 5-year follow-up

(2013) Yoshiaki Kitaguchi et al.   RESPIRATORY MEDICINE

Influence of radiological emphysema on lung function test in idiopathic pulmonary fibrosis

(2013) Aline Bodlet et al.   RESPIRATORY MEDICINE

Comparison of clinical characteristics and prognostic factors of combined pulmonary fibrosis and emphysema versus idiopathic pulmonary fibrosis alone

(2013) Keishi Sugino et al.   RESPIROLOGY

Smoking-related emphysema is associated with idiopathic pulmonary fibrosis and rheumatoid lung

(2013) Katerina M. Antoniou et al.   RESPIROLOGY

Premature lung aging and cellular senescence in the pathogenesis of idiopathic pulmonary fibrosis and COPD/emphysema

(2013) Marco Chilosi et al.   Translational Research

Association of genes of protease-antiprotease balance pathway to lung function and emphysema subtypes

(2013) Mari K Kukkonen et al.   BMC Pulmonary Medicine

Increased incidence of autoimmune markers in patients with combined pulmonary fibrosis and emphysema

(2013) Argyris Tzouvelekis et al.   BMC Pulmonary Medicine

TGF-β-Smad3 signaling in emphysema and pulmonary fibrosis: an epigenetic aberration of normal development?

(2012) David Warburton et al.   AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

Abnormal Lung Aging in Chronic Obstructive Pulmonary Disease and Idiopathic Pulmonary Fibrosis

(2012) Rosa Faner et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Interstitial Lung Abnormalities and Reduced Exercise Capacity

(2012) Tracy J. Doyle et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Increased serum levels and tissue expression of matrix metalloproteinase-12 in patients with systemic sclerosis: correlation with severity of skin and pulmonary fibrosis and vascular damage

(2012) Mirko Manetti et al.   ANNALS OF THE RHEUMATIC DISEASES

Combined Pulmonary Fibrosis and Emphysema Syndrome

(2012) Matthew D. Jankowich et al.   CHEST

Combined pulmonary fibrosis and emphysema in connective tissue disease

(2012) Vincent Cottin et al.   CURRENT OPINION IN PULMONARY MEDICINE

Combined pulmonary fibrosis and emphysema associated with microscopic polyangiitis

(2012) Argyris Tzouvelekis et al.   EUROPEAN RESPIRATORY JOURNAL

Smoking-related interstitial fibrosis (SRIF), pathogenesis and treatment of usual interstitial pneumonia (UIP) and transbronchial biopsy in UIP

(2012) Anna-Luise A Katzenstein   MODERN PATHOLOGY

Respiratory mechanics measured by forced oscillation technique in combined pulmonary fibrosis and emphysema

(2012) Kazutaka Mori et al.   RESPIRATORY PHYSIOLOGY & NEUROBIOLOGY

The pathogenesis of COPD and IPF: Distinct horns of the same devil?

(2012) Marco Chilosi et al.   RESPIRATORY RESEARCH

Cytokine profile of bronchoalveolar lavage fluid in patients with combined pulmonary fibrosis and emphysema

(2012) SADATOMO TASAKA et al.   RESPIROLOGY

Syndrome emphysème – fibrose pulmonaire : histoire naturelle de la maladie. Évolution chronologique clinique, fonctionnelle respiratoire et scanographique

(2012) R. Ponçot-Mongars et al.   REVUE DES MALADIES RESPIRATOIRES

Association of circulating levels of MMP-8 with mortality from respiratory disease in patients with rheumatoid arthritis

(2012) Derek L Mattey et al.   ARTHRITIS RESEARCH & THERAPY

A cohort study of mortality predictors and characteristics of patients with combined pulmonary fibrosis and emphysema

(2012) Tomoo Kishaba et al.   BMJ Open

Telomere Length Is a Determinant of Emphysema Susceptibility

(2011) Jonathan K. Alder et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Ascertainment of Individual Risk of Mortality for Patients with Idiopathic Pulmonary Fibrosis

(2011) Roland M. du Bois et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

An Official ATS/ERS/JRS/ALAT Statement: Idiopathic Pulmonary Fibrosis: Evidence-based Guidelines for Diagnosis and Management

(2011) Ganesh Raghu et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Interstitial lung diseases in a lung cancer screening trial

(2011) N. Sverzellati et al.   EUROPEAN RESPIRATORY JOURNAL

Elevated MMP-7 levels in patients with systemic sclerosis: correlation with pulmonary involvement

(2011) Pia Moinzadeh et al.   EXPERIMENTAL DERMATOLOGY

The impact of combined pulmonary fibrosis and emphysema on mortality

(2011) C-H. Lee et al.   INTERNATIONAL JOURNAL OF TUBERCULOSIS AND LUNG DISEASE

Combined Pulmonary Fibrosis and Emphysema Syndrome in a Patient Age 28 Years with Severe Systemic Sclerosis

(2011) V. COTTIN et al.   JOURNAL OF RHEUMATOLOGY

International Association for the Study of Lung Cancer/American Thoracic Society/European Respiratory Society International Multidisciplinary Classification of Lung Adenocarcinoma

(2011) William D. Travis et al.   Journal of Thoracic Oncology

Pirfenidone in patients with idiopathic pulmonary fibrosis (CAPACITY): two randomised trials

(2011) Paul W Noble et al.   LANCET

Telomerase and idiopathic pulmonary fibrosis

(2011) Mary Armanios   MUTATION RESEARCH-FUNDAMENTAL AND MOLECULAR MECHANISMS OF MUTAGENESIS

Lung Volumes and Emphysema in Smokers with Interstitial Lung Abnormalities

(2011) George R. Washko et al.   NEW ENGLAND JOURNAL OF MEDICINE

Conditions associated with severe carbon monoxide diffusion coefficient reduction

(2011) Lize Kiakouama et al.   RESPIRATORY MEDICINE

Combined pulmonary fibrosis and emphysema syndrome associated with familial SFTPC mutation

(2011) V. Cottin et al.   THORAX

Surfactant Protein C Mutations Are the Basis of a Significant Portion of Adult Familial Pulmonary Fibrosis in a Dutch Cohort

(2010) Coline H. M. van Moorsel et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Expression of Matrix Metalloproteases by Fibrocytes

(2010) Carolina García-de-Alba et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Combined pulmonary fibrosis and emphysema syndrome in connective tissue disease

(2010) Vincent Cottin et al.   ARTHRITIS AND RHEUMATISM

Pulmonary function measures predict mortality differently in IPF versus combined pulmonary fibrosis and emphysema

(2010) S. L. Schmidt et al.   EUROPEAN RESPIRATORY JOURNAL

Pulmonary Talcosis: Imaging Findings

(2010) Edson Marchiori et al.   LUNG

Combined Pulmonary Fibrosis and Emphysema Alters Physiology but Has Similar Mortality to Pulmonary Fibrosis Without Emphysema

(2010) Matthew D. Jankowich et al.   LUNG

A Controlled Trial of Sildenafil in Advanced Idiopathic Pulmonary Fibrosis

(2010)   NEW ENGLAND JOURNAL OF MEDICINE

Combined Pulmonary Fibrosis and Emphysema: 3D Time-resolved MR Angiographic Evaluation of Pulmonary Arterial Mean Transit Time and Time to Peak Enhancement

(2010) Gianluigi Sergiacomi et al.   RADIOLOGY

The effect of emphysema on lung function and survival in patients with idiopathic pulmonary fibrosis

(2010) Kazuyoshi KURASHIMA et al.   RESPIROLOGY

The prevalence of pulmonary fibrosis combined with emphysema in patients with lung cancer

(2010) Kazuhiro USUI et al.   RESPIROLOGY

Cigarette Smoking Is Associated with Subclinical Parenchymal Lung Disease

(2009) David J. Lederer et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Pathologic and Radiologic Differences Between Idiopathic and Collagen Vascular Disease-Related Usual Interstitial Pneumonia

(2009) Jin Woo Song et al.   CHEST

Idiopathic Pulmonary Fibrosis and Emphysema

(2009) Mayra Mejía et al.   CHEST

The Syndrome of Combined Pulmonary Fibrosis and Emphysema

(2009) Vincent Cottin et al.   CHEST

Non-specific interstitial pneumonia in cigarette smokers: a CT study

(2009) Katharina Marten et al.   EUROPEAN RADIOLOGY

Pulmonary hypertension in patients with combined pulmonary fibrosis and emphysema syndrome

(2009) V. Cottin et al.   EUROPEAN RESPIRATORY JOURNAL

Anti-elastin autoantibodies are not present in combined pulmonary fibrosis and emphysema

(2009) V. Cottin et al.   EUROPEAN RESPIRATORY JOURNAL

Clinically occult interstitial fibrosis in smokers: classification and significance of a surprisingly common finding in lobectomy specimens

(2009) Anna-Luise A. Katzenstein et al.   HUMAN PATHOLOGY

Syndrome emphysème des sommets et fibrose pulmonaire des bases combinés (syndrome emphysème/fibrose) : aspects tomodensitométriques et fonctionnels

(2009) P.Y. Brillet et al.   JOURNAL DE RADIOLOGIE

Usual Interstitial Pneumonia and Nonspecific Interstitial Pneumonia with and without Concurrent Emphysema: Thin-Section CT Findings

(2009) Masanori Akira et al.   RADIOLOGY

Coexistent emphysema delays the decrease of vital capacity in idiopathic pulmonary fibrosis

(2009) Takanori Akagi et al.   RESPIRATORY MEDICINE

Clinical characteristics of combined pulmonary fibrosis and emphysema

(2009) Yoshiaki KITAGUCHI et al.   RESPIROLOGY

Smoking-related changes in the background lung of specimens resected for lung cancer: a semiquantitative study with correlation to postoperative course

(2008) Y Kawabata et al.   HISTOPATHOLOGY

Diagnosis of usual interstitial pneumonia and distinction from other fibrosing interstitial lung diseases

(2008) Anna-Luise A. Katzenstein et al.   HUMAN PATHOLOGY

Fibrocytes are a potential source of lung fibroblasts in idiopathic pulmonary fibrosis

(2008) Annika Andersson-Sjöland et al.   INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY

Fibrose pulmonar idiopática simultânea a enfisema em pacientes tabagistas

(2008) Denise Rossato Silva et al.   Jornal Brasileiro de Pneumologia

Short telomeres are a risk factor for idiopathic pulmonary fibrosis

(2008) J. K. Alder et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Fleischner Society: Glossary of Terms for Thoracic Imaging

(2008) David M. Hansell et al.   RADIOLOGY

HRCT and histopathological evaluation of fibrosis and tissue destruction in IPF associated with pulmonary emphysema

(2008) Paola Rogliani et al.   RESPIRATORY MEDICINE

MMP1 and MMP7 as Potential Peripheral Blood Biomarkers in Idiopathic Pulmonary Fibrosis

(2008) Ivan O Rosas et al.   PLOS MEDICINE

Idiopathic Pulmonary Fibrosis

(2007) Katerina M. Antoniou et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Determination of desmosine in bronchoalveolar lavage fluids by time-resolved fluoroimmunoassay

(2007) Takaji Sato et al.   CLINICA CHIMICA ACTA