Primary and secondary hemophagocytic lymphohistiocytosis: clinical features, pathogenesis and therapy

Dramatic efficacy of antithymocyte globulins in childhood EBV-associated haemophagocytic syndrome

(2010) Y Perel et al.   ACTA PAEDIATRICA

Chediak-Higashi syndrome

(2009) Jerry Kaplan et al.   CURRENT OPINION IN HEMATOLOGY

Successful use of the anti-CD25 antibody daclizumab in an adult patient with hemophagocytic lymphohistiocytosis

(2008) Rebecca L. Olin et al.   AMERICAN JOURNAL OF HEMATOLOGY

Genetic loci contributing to hemophagocytic lymphohistiocytosis do not confer susceptibility to systemic-onset juvenile idiopathic arthritis

(2008) Rachelle Donn et al.   ARTHRITIS AND RHEUMATISM

Mutations of the hemophagocytic lymphohistiocytosis–associated geneUNC13D in a patient with systemic juvenile idiopathic arthritis

(2008) Melissa M. Hazen et al.   ARTHRITIS AND RHEUMATISM

Macrophage activation syndrome in rheumatic disease: What is the role of the antigen presenting cell?

(2008) Edward M. Behrens   AUTOIMMUNITY REVIEWS

Functional assessment of perforin C2 domain mutations illustrates the critical role for calcium-dependent lipid binding in perforin cytotoxic function

(2008) R. Urrea Moreno et al.   BLOOD

The role of BMT in childhood histiocytoses

(2008) D Caselli et al.   BONE MARROW TRANSPLANTATION

Frequency and spectrum of central nervous system involvement in 193 children with haemophagocytic lymphohistiocytosis

(2008) AnnaCarin Horne et al.   BRITISH JOURNAL OF HAEMATOLOGY

Membrane traffic in the secretory pathway

(2008) M. Fukuda   CELLULAR AND MOLECULAR LIFE SCIENCES

Relationship between CD107a expression and cytotoxic activity

(2008) Esin Aktas et al.   CELLULAR IMMUNOLOGY

Flow cytometric detection of perforin upregulation in human CD8 T cells

(2008) Adam R. Hersperger et al.   CYTOMETRY PART A

A Griscelli syndrome type 2 murine model of hemophagocytic lymphohistiocytosis (HLH)

(2008) Jana Pachlopnik Schmid et al.   EUROPEAN JOURNAL OF IMMUNOLOGY

The membrane repair response masks membrane disturbances caused by cell-penetrating peptide uptake

(2008) Caroline Palm-Apergi et al.   FASEB JOURNAL

Mutations affecting mRNA splicing are the most common molecular defect in patients with familial hemophagocytic lymphohistiocytosis type 3

(2008) A. Santoro et al.   HAEMATOLOGICA

The Early Kinetics of Cytomegalovirus-Specific CD8+ T-Cell Responses Are Not Affected by Antigen Load or the Absence of Perforin or Gamma Interferon

(2008) D. M. Andrews et al.   JOURNAL OF VIROLOGY

Distinguishing hemophagocytic lymphohistiocytosis from hemochromatosis in patients with hyperferritinemia

(2008) Shailendra Kapoor   PEDIATRIC BLOOD & CANCER

Familial hemophagocytic lymphohistiocytosis in two brothers with X-linked agammaglobulinemia

(2008) Kris Ann P. Schultz et al.   PEDIATRIC BLOOD & CANCER

Increased serum monocyte chemoattractant protein-1, macrophage inflammatory protein-1β, and interleukin-8 concentrations in hemophagocytic lymphohistiocytosis

(2008) Kazushi Tamura et al.   PEDIATRIC BLOOD & CANCER

High elevated ferritin levels and the diagnosis of HLH/Sepsis/SIRS/MODS/MAS

(2008) Leticia Castillo   PEDIATRIC BLOOD & CANCER

The role of the initial bone marrow aspirate in the diagnosis of hemophagocytic lymphohistiocytosis

(2008) Abha Gupta et al.   PEDIATRIC BLOOD & CANCER

Treatment of the X-linked lymphoproliferative, Griscelli and Chédiak-Higashi syndromes by HLH directed therapy

(2008) Helena Trottestam et al.   PEDIATRIC BLOOD & CANCER

A case of macrophage activation syndrome successfully treated with anakinra

(2008) Alison Kelly et al.   Nature clinical practice. Rheumatology

Highly elevated ferritin levels and the diagnosis of hemophagocytic lymphohistiocytosis

(2007) Carl E. Allen et al.   PEDIATRIC BLOOD & CANCER