标题
Protein-mediated assembly of succinate dehydrogenase and its cofactors
作者
关键词
-
出版物
CRITICAL REVIEWS IN BIOCHEMISTRY AND MOLECULAR BIOLOGY
Volume 50, Issue 2, Pages 168-180
出版商
Informa UK Limited
发表日期
2014-12-09
DOI
10.3109/10409238.2014.990556
参考文献
相关参考文献
注意:仅列出部分参考文献,下载原文获取全部文献信息。- The LYR Factors SDHAF1 and SDHAF3 Mediate Maturation of the Iron-Sulfur Subunit of Succinate Dehydrogenase
- (2014) Un Na et al. Cell Metabolism
- SDHAF4 Promotes Mitochondrial Succinate Dehydrogenase Activity and Prevents Neurodegeneration
- (2014) Jonathan G. Van Vranken et al. Cell Metabolism
- Cochaperone Binding to LYR Motifs Confers Specificity of Iron Sulfur Cluster Delivery
- (2014) Nunziata Maio et al. Cell Metabolism
- Analysis of covalent flavinylation using thermostable succinate dehydrogenase fromThermus thermophilusandSulfolobus tokodaiilacking SdhE homologs
- (2014) Asako Kounosu FEBS LETTERS
- The 2-Oxoacid Dehydrogenase Complexes in Mitochondria Can Produce Superoxide/Hydrogen Peroxide at Much Higher Rates Than Complex I
- (2014) Casey L. Quinlan et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- [2Fe-2S] cluster transfer in iron-sulfur protein biogenesis
- (2014) L. Banci et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Complex II deficiency-A case report and review of the literature
- (2013) Shailly Jain-Ghai et al. AMERICAN JOURNAL OF MEDICAL GENETICS PART A
- Emerging concepts in the flavinylation of succinate dehydrogenase
- (2013) Hyung J. Kim et al. BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS
- Variant non ketotic hyperglycinemia is caused by mutations in LIAS, BOLA3 and the novel gene GLRX5
- (2013) Peter R. Baker et al. BRAIN
- Analysis of all subunits, SDHA, SDHB, SDHC, SDHD, of the succinate dehydrogenase complex in KIT/PDGFRA wild-type GIST
- (2013) Maria A Pantaleo et al. EUROPEAN JOURNAL OF HUMAN GENETICS
- Mutations in LYRM4, encoding iron–sulfur cluster biogenesis factor ISD11, cause deficiency of multiple respiratory chain complexes
- (2013) Sze Chern Lim et al. HUMAN MOLECULAR GENETICS
- Mutation of the iron-sulfur cluster assembly gene IBA57 causes severe myopathy and encephalopathy
- (2013) Nikhita Ajit Bolar et al. HUMAN MOLECULAR GENETICS
- Frataxin Directly Stimulates Mitochondrial Cysteine Desulfurase by Exposing Substrate-binding Sites, and a Mutant Fe-S Cluster Scaffold Protein with Frataxin-bypassing Ability Acts Similarly
- (2013) Alok Pandey et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Binding of the Chaperone Jac1 Protein and Cysteine Desulfurase Nfs1 to the Iron-Sulfur Cluster Scaffold Isu Protein Is Mutually Exclusive
- (2013) Julia Majewska et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Mutations inSDHDlead to autosomal recessive encephalomyopathy and isolated mitochondrial complex II deficiency
- (2013) Christopher Benjamin Jackson et al. JOURNAL OF MEDICAL GENETICS
- The mitochondrial Hsp70 chaperone Ssq1 facilitates Fe/S cluster transfer from Isu1 to Grx5 by complex formation
- (2013) Marta A. Uzarska et al. MOLECULAR BIOLOGY OF THE CELL
- Persulfide formation on mitochondrial cysteine desulfurase: enzyme activation by a eukaryote-specific interacting protein and Fe–S cluster synthesis
- (2012) Alok Pandey et al. BIOCHEMICAL JOURNAL
- Solution NMR Structure of Yeast Succinate Dehydrogenase Flavinylation Factor Sdh5 Reveals a Putative Sdh1 Binding Site
- (2012) Alexander Eletsky et al. BIOCHEMISTRY
- Monothiol CGFS Glutaredoxins and BolA-like Proteins: [2Fe-2S] Binding Partners in Iron Homeostasis
- (2012) Haoran Li et al. BIOCHEMISTRY
- The role of complex II in disease
- (2012) Attje S. Hoekstra et al. BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS
- The role of mitochondria in cellular iron–sulfur protein biogenesis and iron metabolism
- (2012) Roland Lill et al. BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH
- Mitochondrial protein import: Common principles and physiological networks
- (2012) Jan Dudek et al. BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH
- Flavinylation and Assembly of Succinate Dehydrogenase Are Dependent on the C-terminal Tail of the Flavoprotein Subunit
- (2012) Hyung J. Kim et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Tissue Specificity of a Human Mitochondrial Disease
- (2012) Daniel R. Crooks et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Protein expression profiles in patients carrying NFU1 mutations. Contribution to the pathophysiology of the disease
- (2012) Xènia Ferrer-Cortès et al. JOURNAL OF INHERITED METABOLIC DISEASE
- Recessive germlineSDHAandSDHBmutations causing leukodystrophy and isolated mitochondrial complex II deficiency
- (2012) Charlotte L Alston et al. JOURNAL OF MEDICAL GENETICS
- Interaction of J-Protein Co-Chaperone Jac1 with Fe–S Scaffold Isu Is Indispensable In Vivo and Conserved in Evolution
- (2012) Szymon J. Ciesielski et al. JOURNAL OF MOLECULAR BIOLOGY
- The human mitochondrial ISCA1, ISCA2, and IBA57 proteins are required for [4Fe-4S] protein maturation
- (2012) Alex D. Sheftel et al. MOLECULAR BIOLOGY OF THE CELL
- Molecular organization, biochemical function, cellular role and evolution of NfuA, an atypical Fe-S carrier
- (2012) Béatrice Py et al. MOLECULAR MICROBIOLOGY
- Leukoencephalopathy with accumulated succinate is indicative of SDHAF1 related complex II deficiency
- (2012) Andreas Ohlenbusch et al. Orphanet Journal of Rare Diseases
- Mutations in Iron-Sulfur Cluster Scaffold Genes NFU1 and BOLA3 Cause a Fatal Deficiency of Multiple Respiratory Chain and 2-Oxoacid Dehydrogenase Enzymes
- (2011) Jessie M. Cameron et al. AMERICAN JOURNAL OF HUMAN GENETICS
- A Fatal Mitochondrial Disease Is Associated with Defective NFU1 Function in the Maturation of a Subset of Mitochondrial Fe-S Proteins
- (2011) Aleix Navarro-Sastre et al. AMERICAN JOURNAL OF HUMAN GENETICS
- Specialized Function of Yeast Isa1 and Isa2 Proteins in the Maturation of Mitochondrial [4Fe-4S] Proteins
- (2011) Ulrich Mühlenhoff et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- SDHA Loss-of-Function Mutations in KIT-PDGFRA Wild-Type Gastrointestinal Stromal Tumors Identified by Massively Parallel Sequencing
- (2011) M. A. Pantaleo et al. JNCI-Journal of the National Cancer Institute
- Mammalian Frataxin: An Essential Function for Cellular Viability through an Interaction with a Preformed ISCU/NFS1/ISD11 Iron-Sulfur Assembly Complex
- (2011) Stéphane Schmucker et al. PLoS One
- Mitochondrial disorders caused by mutations in respiratory chain assembly factors
- (2011) Francisca Diaz et al. Seminars in Fetal & Neonatal Medicine
- The crystal structure of human GLRX5: iron–sulfur cluster co-ordination, tetrameric assembly and monomer activity
- (2010) Catrine Johansson et al. BIOCHEMICAL JOURNAL
- Human Frataxin Is an Allosteric Switch That Activates the Fe−S Cluster Biosynthetic Complex
- (2010) Chi-Lin Tsai et al. BIOCHEMISTRY
- Specific disintegration of complex II succinate:ubiquinone oxidoreductase links pH changes to oxidative stress for apoptosis induction
- (2010) A Lemarie et al. CELL DEATH AND DIFFERENTIATION
- SDHA is a tumor suppressor gene causing paraganglioma
- (2010) Nelly Burnichon et al. HUMAN MOLECULAR GENETICS
- Mzm1 Influences a Labile Pool of Mitochondrial Zinc Important for Respiratory Function
- (2010) Aaron Atkinson et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Succinate dehydrogenase – Assembly, regulation and role in human disease
- (2010) Jared Rutter et al. MITOCHONDRION
- Mitochondrial localization of human FAD synthetase isoform 1
- (2010) Enza Maria Torchetti et al. MITOCHONDRION
- Humans possess two mitochondrial ferredoxins, Fdx1 and Fdx2, with distinct roles in steroidogenesis, heme, and Fe/S cluster biosynthesis
- (2010) A. D. Sheftel et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Defects in succinate dehydrogenase in gastrointestinal stromal tumors lacking KIT and PDGFRA mutations
- (2010) K. A. Janeway et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- SDHAF1, encoding a LYR complex-II specific assembly factor, is mutated in SDH-defective infantile leukoencephalopathy
- (2009) Daniele Ghezzi et al. NATURE GENETICS
- SDH5, a Gene Required for Flavination of Succinate Dehydrogenase, Is Mutated in Paraganglioma
- (2009) H.-X. Hao et al. SCIENCE
- Assembly of the oxidative phosphorylation system in humans: What we have learned by studying its defects
- (2008) Erika Fernández-Vizarra et al. BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH
- Coa2 Is an Assembly Factor for Yeast Cytochrome c Oxidase Biogenesis That Facilitates the Maturation of Cox1
- (2008) F. Pierrel et al. MOLECULAR AND CELLULAR BIOLOGY
- Extra-adrenal and adrenal pheochromocytomas associated with a germline SDHC mutation
- (2008) Mariola Pęczkowska et al. Nature clinical practice. Endocrinology & metabolism
Find Funding. Review Successful Grants.
Explore over 25,000 new funding opportunities and over 6,000,000 successful grants.
ExplorePublish scientific posters with Peeref
Peeref publishes scientific posters from all research disciplines. Our Diamond Open Access policy means free access to content and no publication fees for authors.
Learn More