Frataxin Directly Stimulates Mitochondrial Cysteine Desulfurase by Exposing Substrate-binding Sites, and a Mutant Fe-S Cluster Scaffold Protein with Frataxin-bypassing Ability Acts Similarly

(IscS-IscU)2Complex Structures Provide Insights into Fe2S2Biogenesis and Transfer

(2012) Elodie N. Marinoni et al.   ANGEWANDTE CHEMIE-INTERNATIONAL EDITION

Persulfide formation on mitochondrial cysteine desulfurase: enzyme activation by a eukaryote-specific interacting protein and Fe–S cluster synthesis

(2012) Alok Pandey et al.   BIOCHEMICAL JOURNAL

The role of mitochondria in cellular iron–sulfur protein biogenesis and iron metabolism

(2012) Roland Lill et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

Biogenesis of iron-sulfur clusters in mammalian cells: new insights and relevance to human disease

(2012) T. A. Rouault   Disease Models & Mechanisms

Mammalian Frataxin Controls Sulfur Production and Iron Entry during de Novo Fe4S4 Cluster Assembly

(2012) Florent Colin et al.   JOURNAL OF THE AMERICAN CHEMICAL SOCIETY

Identification of a Nfs1p-bound persulfide intermediate in Fe–S cluster synthesis by intact mitochondria

(2012) Alok Pandey et al.   MITOCHONDRION

Iron–sulfur cluster synthesis, iron homeostasis and oxidative stress in Friedreich ataxia

(2012) Rachael A. Vaubel et al.   MOLECULAR AND CELLULAR NEUROSCIENCE

Identification of nonferritin mitochondrial iron deposits in a mouse model of Friedreich ataxia

(2012) M. Whitnall et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Mutation in the Fe–S scaffold protein Isu bypasses frataxin deletion

(2011) Heeyong Yoon et al.   BIOCHEMICAL JOURNAL

Mammalian Frataxin: An Essential Function for Cellular Viability through an Interaction with a Preformed ISCU/NFS1/ISD11 Iron-Sulfur Assembly Complex

(2011) Stéphane Schmucker et al.   PLoS One

Molecular Details of the Yeast Frataxin−Isu1 Interaction during Mitochondrial Fe−S Cluster Assembly

(2010) Jeremy D. Cook et al.   BIOCHEMISTRY

Human Frataxin Is an Allosteric Switch That Activates the Fe−S Cluster Biosynthetic Complex

(2010) Chi-Lin Tsai et al.   BIOCHEMISTRY

Proteomic approaches to the characterization of protein thiol modification

(2010) Edward T Chouchani et al.   CURRENT OPINION IN CHEMICAL BIOLOGY

Mitochondrial NADH Kinase, Pos5p, Is Required for Efficient Iron-Sulfur Cluster Biogenesis inSaccharomyces cerevisiae

(2010) Jayashree Pain et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Frataxin and Mitochondrial FeS Cluster Biogenesis

(2010) Timothy L. Stemmler et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Pharmacotherapy for Friedreich Ataxia

(2009) Amy Y. Tsou et al.   CNS DRUGS

Dual Targeting of Nfs1 and Discovery of Its Novel Processing Enzyme, Icp55

(2009) Adi Naamati et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

H2S Signals Through Protein S-Sulfhydration

(2009) A. K. Mustafa et al.   Science Signaling

DrosophilaFrataxin: An Iron Chaperone during Cellular Fe−S Cluster Bioassembly†

(2008) Kalyan C. Kondapalli et al.   BIOCHEMISTRY

Binding of Yeast Frataxin to the Scaffold for Fe-S Cluster Biogenesis, Isu

(2008) Tao Wang et al.   JOURNAL OF BIOLOGICAL CHEMISTRY