Intracellular mechanisms of molecular recognition and sorting for transport of large extracellular matrix molecules

Mutants of collagen-specific molecular chaperone Hsp47 causing osteogenesis imperfecta are structurally unstable with weak binding affinity to collagen

(2016) Shinya Ito et al.   BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS

The Pathway of Collagen Secretion

(2015) Vivek Malhotra et al.   Annual Review of Cell and Developmental Biology

Mechanisms for exporting large-sized cargoes from the endoplasmic reticulum

(2015) Kota Saito et al.   CELLULAR AND MOLECULAR LIFE SCIENCES

Molecular Consequences of theSERPINH1/HSP47 Mutation in the Dachshund Natural Model of Osteogenesis Imperfecta

(2015) Uschi Lindert et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Recurrent turnover of senescent cells during regeneration of a complex structure

(2015) Maximina H Yun et al.   eLife

Osteogenesis imperfecta due to mutations in non-collagenous genes

(2014) Joan C. Marini et al.   CURRENT OPINION IN PEDIATRICS

Connective tissue alterations in Fkbp10−/− mice

(2014) Caressa D. Lietman et al.   HUMAN MOLECULAR GENETICS

A Substrate Preference for the Rough Endoplasmic Reticulum Resident Protein FKBP22 during Collagen Biosynthesis

(2014) Yoshihiro Ishikawa et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

SLY1 and Syntaxin 18 specify a distinct pathway for procollagen VII export from the endoplasmic reticulum

(2014) Cristina Nogueira et al.   eLife

The endoplasmic reticulum and junctional membrane communication during calcium signaling

(2013) Andy K.M. Lam et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

Vesicle-mediated export from the ER: COPII coat function and regulation

(2013) Jennifer G. D'Arcangelo et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

N-linked protein glycosylation in the ER

(2013) Markus Aebi   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

A molecular ensemble in the rER for procollagen maturation

(2013) Yoshihiro Ishikawa et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

COPII — a flexible vesicle formation system

(2013) Elizabeth A Miller et al.   CURRENT OPINION IN CELL BIOLOGY

Trafficking mechanisms of extracellular matrix macromolecules: Insights from vertebrate development and human diseases

(2013) Gokhan Unlu et al.   INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY

SH3 domain ligand binding: What's the consensus and where's the specificity?

(2012) Kalle Saksela et al.   FEBS LETTERS

Ubiquitin-dependent regulation of COPII coat size and function

(2012) Lingyan Jin et al.   NATURE

Molecular basis for the action of the collagen-specific chaperone Hsp47/SERPINH1 and its structure-specific client recognition

(2012) C. Widmer et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Sedlin Controls the ER Export of Procollagen by Regulating the Sar1 Cycle

(2012) R. Venditti et al.   SCIENCE

Global defects in collagen secretion in aMia3/TANGO1knockout mouse

(2011) Deanna G. Wilson et al.   JOURNAL OF CELL BIOLOGY

cTAGE5 mediates collagen secretion through interaction with TANGO1 at endoplasmic reticulum exit sites

(2011) Kota Saito et al.   MOLECULAR BIOLOGY OF THE CELL

Homozygosity for a Missense Mutation in SERPINH1, which Encodes the Collagen Chaperone Protein HSP47, Results in Severe Recessive Osteogenesis Imperfecta

(2010) Helena E. Christiansen et al.   AMERICAN JOURNAL OF HUMAN GENETICS

Prolyl 3-Hydroxylase 1 Null Mice Display Abnormalities in Fibrillar Collagen-rich Tissues Such as Tendons, Skin, and Bones

(2010) Janice A. Vranka et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

The Collagen Family

(2010) S. Ricard-Blum   Cold Spring Harbor Perspectives in Biology

TANGO1 Facilitates Cargo Loading at Endoplasmic Reticulum Exit Sites

(2009) Kota Saito et al.   CELL

Genetic diseases of connective tissues: cellular and extracellular effects of ECM mutations

(2009) John F. Bateman et al.   NATURE REVIEWS GENETICS

A Missense Mutation in the SERPINH1 Gene in Dachshunds with Osteogenesis Imperfecta

(2009) Cord Drögemüller et al.   PLoS Genetics

The Rough Endoplasmic Reticulum-resident FK506-binding Protein FKBP65 Is a Molecular Chaperone That Interacts with Collagens

(2008) Yoshihiro Ishikawa et al.   JOURNAL OF BIOLOGICAL CHEMISTRY