标题
The biology of the ABCA3 lipid transporter in lung health and disease
作者
关键词
ABCA3, Pulmonary surfactant, Compound heterozygous mutations, Surfactant deficiency, Inhertited pulmonary disease
出版物
CELL AND TISSUE RESEARCH
Volume 367, Issue 3, Pages 481-493
出版商
Springer Nature
发表日期
2016-12-26
DOI
10.1007/s00441-016-2554-z
参考文献
相关参考文献
注意:仅列出部分参考文献,下载原文获取全部文献信息。- ABCA3 mutations led to pulmonary fibrosis and emphysema with pulmonary hypertension in an 8-year-old girl
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