Neutrophilic panniculitis associated with alpha-1-antitrypsin deficiency: an update

α-1-Antitrypsin variants and the proteinase/antiproteinase imbalance in chronic obstructive pulmonary disease

(2015) Nicola J. Sinden et al.   AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

Scavenger receptor class B, type I-mediated uptake of A1AT by pulmonary endothelial cells

(2015) Angelia D. Lockett et al.   AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

Immune Activation in α1-Antitrypsin-Deficiency Emphysema. Beyond the Protease–Antiprotease Paradigm

(2015) Simonetta Baraldo et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

Alpha-1-antitrypsin deficiency panniculitis presenting with severe anasarca, pulmonary embolus and hypogammaglobulinaemia

(2015) A.N. Elsensohn et al.   BRITISH JOURNAL OF DERMATOLOGY

Immune protective effect of human alpha-1-antitrypsin gene during β cell transplantation in diabetic mice

(2015) Lu Yang et al.   IMMUNOLOGIC RESEARCH

Pannikulitis des Oberschenkels und Lungenemphysem bei einem 54-jährigen Patienten

(2015) M. Eckhard et al.   INTERNIST

Severe postoperative wound healing disturbance in a patient with alpha-1-antitrypsin deficiency: the impact of augmentation therapy

(2015) Marionna Cathomas et al.   International Wound Journal

Neutrophilic Panniculitis: Algorithmic Approach to a Heterogeneous Group of Disorders

(2014) May P. Chan   ARCHIVES OF PATHOLOGY & LABORATORY MEDICINE

Serum concentration of alpha-1 antitrypsin is significantly higher in colorectal cancer patients than in healthy controls

(2014) Sergio Pérez-Holanda et al.   BMC CANCER

Alpha-1-antitrypsin inhibits acute liver failure in mice

(2014) Nils Jedicke et al.   HEPATOLOGY

Alpha-1 Antitrypsin Augmentation Therapy Corrects Accelerated Neutrophil Apoptosis in Deficient Individuals

(2014) Killian Hurley et al.   JOURNAL OF IMMUNOLOGY

Role of alpha-1 antitrypsin in human health and disease

(2014) F. de Serres et al.   JOURNAL OF INTERNAL MEDICINE

The Circulating Proteinase Inhibitor  -1 Antitrypsin Regulates Neutrophil Degranulation and Autoimmunity

(2014) D. A. Bergin et al.   Science Translational Medicine

α1-Antitrypsin Modulates Lung Endothelial Cell Inflammatory Responses to TNF-α

(2013) Angelia D. Lockett et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Anti-inflammatory and immunomodulatory properties of  1-antitrypsin without inhibition of elastase

(2013) D. Jonigk et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Alpha-1 Antitrypsin: A Potent Anti-Inflammatory and Potential Novel Therapeutic Agent

(2012) David A. Bergin et al.   ARCHIVUM IMMUNOLOGIAE ET THERAPIAE EXPERIMENTALIS

Revascularization of Pancreatic Islet Allografts is Enhanced by α-1-Antitrypsin under Anti-Inflammatory Conditions

(2012) Keren Bellacen et al.   CELL TRANSPLANTATION

Panniculitis in alpha-1 antitrypsin deficiency treated with enzyme replacement

(2012) Jonathan M. Olson et al.   JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY

Inhibition of IL-32 activation by  -1 antitrypsin suppresses alloreactivity and increases survival in an allogeneic murine marrow transplantation model

(2011) A. M. Marcondes et al.   BLOOD

Alpha-1 antitrypsin inhibits caspase-1 and protects from acute myocardial ischemia–reperfusion injury

(2011) Stefano Toldo et al.   JOURNAL OF MOLECULAR AND CELLULAR CARDIOLOGY

Severe ulcerative panniculitis caused by alpha 1-antitrypsin deficiency: Remission induced and maintained with intravenous alpha 1-antitrypsin

(2011) Firas Al-Niaimi et al.   JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY

Alpha-1 antitrypsin protein and gene therapies decrease autoimmunity and delay arthritis development in mouse model

(2011) Christian Grimstein et al.   Journal of Translational Medicine

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(2011) Galit Shahaf et al.   MOLECULAR MEDICINE

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(2011) Mariam Al-Omari et al.   MOLECULAR MEDICINE

Efficacy of alpha1-antitrypsin augmentation therapy in conditions other than pulmonary emphysema

(2011) Ignacio Blanco et al.   Orphanet Journal of Rare Diseases

Alpha-1-antitrypsin monotherapy reduces graft-versus-host disease after experimental allogeneic bone marrow transplantation

(2011) I. Tawara et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

The discovery of α1-antitrypsin and its role in health and disease

(2011) Sabina M. Janciauskiene et al.   RESPIRATORY MEDICINE

Anakinra for Difficult-to-Treat Neutrophilic Panniculitis: IL-1 Blockade as a Promising Treatment Option for Neutrophil-Mediated Inflammatory Skin Disease

(2010) Dan Lipsker et al.   DERMATOLOGY

A case of systemic nodular panniculitis associated with M1 (Val213) Z phenotype of α1-protease inhibitor

(2010) Marie-Christine Gaillard et al.   INTERNATIONAL JOURNAL OF DERMATOLOGY

α-1 Antitrypsin regulates human neutrophil chemotaxis induced by soluble immune complexes and IL-8

(2010) David A. Bergin et al.   JOURNAL OF CLINICAL INVESTIGATION

New Findings in PiZZ α1-Antitrypsin Deficiency-Related Panniculitis

(2009) B. Gross et al.   DERMATOLOGY

α-1-Antitrypsin is an endogenous inhibitor of proinflammatory cytokine production in whole blood

(2009) Gregory B. Pott et al.   JOURNAL OF LEUKOCYTE BIOLOGY

Alfa-1-antitrypsin deficiency panniculitis acquired after liver transplant and successfully treated with retransplant

(2009) Rosa Fernández-Torres et al.   JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY

Alpha-1-Antitrypsin Deficiency Panniculitis

(2008) Ricardo Valverde et al.   DERMATOLOGIC CLINICS

Curative and   cell regenerative effects of  1-antitrypsin treatment in autoimmune diabetic NOD mice

(2008) M. Koulmanda et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

TNF-α-induced self expression in human lung endothelial cells is inhibited by native and oxidized α1-antitrypsin

(2007) Devipriya Subramaniyam et al.   INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY