Ultrastructural Characterization of the Lower Motor System in a Mouse Model of Krabbe Disease
出版年份 2016 全文链接
标题
Ultrastructural Characterization of the Lower Motor System in a Mouse Model of Krabbe Disease
作者
关键词
-
出版物
Scientific Reports
Volume 6, Issue 1, Pages -
出版商
Springer Nature
发表日期
2016-11-11
DOI
10.1038/s41598-016-0001-8
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注意:仅列出部分参考文献,下载原文获取全部文献信息。- Pervasive supply of therapeutic lysosomal enzymes in the CNS of normal and Krabbe‐affected non‐human primates by intracerebral lentiviral gene therapy
- (2016) Vasco Meneghini et al. EMBO Molecular Medicine
- RP-CARS reveals molecular spatial order anomalies in myelin of an animal model of Krabbe disease
- (2016) Giuseppe de Vito et al. Journal of Biophotonics
- Altered Trafficking and Processing of GALC Mutants Correlates with Globoid Cell Leukodystrophy Severity
- (2016) D. Shin et al. JOURNAL OF NEUROSCIENCE
- Endothelial cell dysfunction in globoid cell leukodystrophy
- (2016) Mirella Belleri et al. JOURNAL OF NEUROSCIENCE RESEARCH
- Mitochondria and endoplasmic reticulum crosstalk in amyotrophic lateral sclerosis
- (2016) Giovanni Manfredi et al. NEUROBIOLOGY OF DISEASE
- History, genetic, and recent advances on Krabbe disease
- (2015) Adriana Carol Eleonora Graziano et al. GENE
- Combined gene/cell therapies provide long-term and pervasive rescue of multiple pathological symptoms in a murine model of globoid cell leukodystrophy
- (2015) A. Ricca et al. HUMAN MOLECULAR GENETICS
- Mechanism of Neuromuscular Dysfunction in Krabbe Disease
- (2015) L. Cantuti-Castelvetri et al. JOURNAL OF NEUROSCIENCE
- Mechanism-Based Combination Treatment Dramatically Increases Therapeutic Efficacy in Murine Globoid Cell Leukodystrophy
- (2015) J. A. Hawkins-Salsbury et al. JOURNAL OF NEUROSCIENCE
- Long-term Improvements in Lifespan and Pathology in CNS and PNS After BMT Plus One Intravenous Injection of AAVrh10-GALC in Twitcher Mice
- (2015) Mohammad A Rafi et al. MOLECULAR THERAPY
- Pharmacological chaperones increase residual β-galactocerebrosidase activity in fibroblasts from Krabbe patients
- (2014) Anna Sara Berardi et al. MOLECULAR GENETICS AND METABOLISM
- Early axonal loss accompanied by impaired endocytosis, abnormal axonal transport, and decreased microtubule stability occur in the model of Krabbe's disease
- (2014) Carla Andreia Teixeira et al. NEUROBIOLOGY OF DISEASE
- Role of extracellular calcium and mitochondrial oxygen species in psychosine-induced oligodendrocyte cell death
- (2014) V Voccoli et al. Cell Death & Disease
- Deficient nitric oxide signalling impairs skeletal muscle growth and performance: involvement of mitochondrial dysregulation
- (2014) Clara De Palma et al. Skeletal Muscle
- Inhibition of angiogenesis by β-galactosylceramidase deficiency in globoid cell leukodystrophy
- (2013) Mirella Belleri et al. BRAIN
- Region- and Age-Dependent Alterations of Glial-Neuronal Metabolic Interactions Correlate with CNS Pathology in a Mouse Model of Globoid Cell Leukodystrophy
- (2013) Tore Wergeland Meisingset et al. JOURNAL OF CEREBRAL BLOOD FLOW AND METABOLISM
- The Sphingolipid Psychosine Inhibits Fast Axonal Transport in Krabbe Disease by Activation of GSK3 and Deregulation of Molecular Motors
- (2013) L. Cantuti Castelvetri et al. JOURNAL OF NEUROSCIENCE
- Oxidative stress as a therapeutic target in globoid cell leukodystrophy
- (2012) Jacqueline A. Hawkins-Salsbury et al. EXPERIMENTAL NEUROLOGY
- Analysis of neuromuscular junctions and effects of anabolic steroid administration in the SOD1G93A mouse model of ALS
- (2012) Valentina Cappello et al. MOLECULAR AND CELLULAR NEUROSCIENCE
- A role for Schwann cell–derived neuregulin-1 in remyelination
- (2012) Ruth M Stassart et al. NATURE NEUROSCIENCE
- Psychosine induces the dephosphorylation of neurofilaments by deregulation of PP1 and PP2A phosphatases
- (2012) Ludovico Cantuti-Castelvetri et al. NEUROBIOLOGY OF DISEASE
- Axonopathy is a compounding factor in the pathogenesis of Krabbe disease
- (2011) Ludovico Cantuti Castelvetri et al. ACTA NEUROPATHOLOGICA
- Peripheral Neuropathy in the Twitcher Mouse Involves the Activation of Axonal Caspase 3
- (2011) Benjamin Smith et al. ASN Neuro
- The Myelin Mutants as Models to Study Myelin Repair in the Leukodystrophies
- (2011) Ian D. Duncan et al. Neurotherapeutics
- SMN Requirement for Synaptic Vesicle, Active Zone and Microtubule Postnatal Organization in Motor Nerve Terminals
- (2011) Laura Torres-Benito et al. PLoS One
- The short-time structural plasticity of dendritic spines is altered in a model of Rett syndrome
- (2011) Silvia Landi et al. Scientific Reports
- Motor Neuron Diversity in Development and Disease
- (2010) Kevin C. Kanning et al. Annual Review of Neuroscience
- Sustained Axon-Glial Signaling Induces Schwann Cell Hyperproliferation, Remak Bundle Myelination, and Tumorigenesis
- (2009) J. A. Gomez-Sanchez et al. JOURNAL OF NEUROSCIENCE
- Psychosine Accumulates in Membrane Microdomains in the Brain of Krabbe Patients, Disrupting the Raft Architecture
- (2009) A. B. White et al. JOURNAL OF NEUROSCIENCE
- Biology and pathology of nonmyelinating Schwann cells
- (2008) John W. Griffin et al. GLIA
- Negative regulation of myelination: Relevance for development, injury, and demyelinating disease
- (2008) Kristján R. Jessen et al. GLIA
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