A Little CFTR Goes a Long Way: CFTR-Dependent Sweat Secretion from G551D and R117H-5T Cystic Fibrosis Subjects Taking Ivacaftor
出版年份 2014 全文链接
标题
A Little CFTR Goes a Long Way: CFTR-Dependent Sweat Secretion from G551D and R117H-5T Cystic Fibrosis Subjects Taking Ivacaftor
作者
关键词
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出版物
PLoS One
Volume 9, Issue 2, Pages e88564
出版商
Public Library of Science (PLoS)
发表日期
2014-02-11
DOI
10.1371/journal.pone.0088564
参考文献
相关参考文献
注意:仅列出部分参考文献,下载原文获取全部文献信息。- Role of Tyrosine Phosphorylation in the Muscarinic Activation of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)
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- In Vivo Readout of CFTR Function: Ratiometric Measurement of CFTR-Dependent Secretion by Individual, Identifiable Human Sweat Glands
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- Vx-770 potentiates CFTR function by promoting decoupling between the gating cycle and ATP hydrolysis cycle
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- Role of Cystic Fibrosis Transmembrane Conductance Regulator in Patients With Chronic Sinopulmonary Disease
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- Ivacaftor potentiation of multiple CFTR channels with gating mutations
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- (2011) Hyung-Ju Cho et al. PLoS One
- Mucin Variable Number Tandem Repeat Polymorphisms and Severity of Cystic Fibrosis Lung Disease: Significant Association with MUC5AC
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- Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis
- (2010) Xingshen Sun et al. JOURNAL OF CLINICAL INVESTIGATION
- Hyposecretion of fluid from tracheal submucosal glands of CFTR-deficient pigs
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- Effect of VX-770 in Persons with Cystic Fibrosis and the G551D-CFTRMutation
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- Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770
- (2009) F. Van Goor et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
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