Lifting the Nebula: Novel Insights into Skeletal Muscle Contractility

Differential splicing of the large sarcomeric protein nebulin during skeletal muscle development

(2010) Danielle Buck et al.   JOURNAL OF STRUCTURAL BIOLOGY

Reduced thin filament length in nebulin-knockout skeletal muscle alters isometric contractile properties

(2009) David S. Gokhin et al.   AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY

A Nebulin Ruler Does Not Dictate Thin Filament Lengths

(2009) Angelica Castillo et al.   BIOPHYSICAL JOURNAL

Nebulin plays a direct role in promoting strong actin-myosin interactions

(2009) Marie-Louise Bang et al.   FASEB JOURNAL

Thin filament length dysregulation contributes to muscle weakness in nemaline myopathy patients with nebulin deficiency

(2009) C. A.C. Ottenheijm et al.   HUMAN MOLECULAR GENETICS

Nebulin Alters Cross-bridge Cycling Kinetics and Increases Thin Filament Activation

(2009) Murali Chandra et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Altered myofilament function depresses force generation in patients with nebulin-based nemaline myopathy (NEM2)

(2009) Coen A.C. Ottenheijm et al.   JOURNAL OF STRUCTURAL BIOLOGY

Peripheral muscle dysfunction in idiopathic pulmonary arterial hypertension

(2009) V. Mainguy et al.   THORAX

Sarcoplasmic reticulum calcium uptake and speed of relaxation are depressed in nebulin-free skeletal muscle

(2008) Coen A. C. Ottenheijm et al.   FASEB JOURNAL

A Myopathy-linked Desmin Mutation Perturbs Striated Muscle Actin Filament Architecture

(2008) Gloria M. Conover et al.   MOLECULAR BIOLOGY OF THE CELL

Thin filament length regulation in striated muscle sarcomeres: Pointed-end dynamics go beyond a nebulin ruler

(2008) R LITTLEFIELD et al.   SEMINARS IN CELL & DEVELOPMENTAL BIOLOGY