Human Cockayne syndrome B protein reciprocally communicates with mitochondrial proteins and promotes transcriptional elongation

Cockayne syndrome group B protein prevents the accumulation of damaged mitochondria by promoting mitochondrial autophagy

(2012) Morten Scheibye-Knudsen et al.   JOURNAL OF EXPERIMENTAL MEDICINE

A comprehensive description of the severity groups in Cockayne syndrome

(2011) Valerie Natale   AMERICAN JOURNAL OF MEDICAL GENETICS PART A

Mechanisms of mitochondrial diseases

(2011) Emil Ylikallio et al.   ANNALS OF MEDICINE

Mitochondrial oxidative stress in cancer-associated fibroblasts drives lactate production, promoting breast cancer tumor growth

(2011) Renee M. Balliet et al.   CELL CYCLE

Human mitochondrial transcription factor A induces a U-turn structure in the light strand promoter

(2011) Anna Rubio-Cosials et al.   NATURE STRUCTURAL & MOLECULAR BIOLOGY

TEFM (c17orf42) is necessary for transcription of human mtDNA

(2011) Michal Minczuk et al.   NUCLEIC ACIDS RESEARCH

Mitochondrial Ribosomal Protein L12 selectively associates with human mitochondrial RNA polymerase to activate transcription

(2011) Y. V. Surovtseva et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Aprataxin localizes to mitochondria and preserves mitochondrial function

(2011) P. Sykora et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

The mitochondrial transcription factor A functions in mitochondrial base excision repair

(2010) Chandrika Canugovi et al.   DNA REPAIR

Cockayne syndrome group B protein promotes mitochondrial DNA stability by supporting the DNA repair association with the mitochondrial membrane

(2010) Maria D. Aamann et al.   FASEB JOURNAL

Thyrotropin powers human mitochondria

(2010) Burkhard Poeggeler et al.   FASEB JOURNAL

Identification of Multiple Rate-limiting Steps during the Human Mitochondrial Transcription Cyclein Vitro

(2010) Maria F. Lodeiro et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Human Mitochondrial Transcription Revisited

(2010) Dmitry Litonin et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Proteins of nucleotide and base excision repair pathways interact in mitochondria to protect from loss of subcutaneous fat, a hallmark of aging

(2010) York Kamenisch et al.   JOURNAL OF EXPERIMENTAL MEDICINE

Core human mitochondrial transcription apparatus is a regulated two-component system in vitro

(2010) T. E. Shutt et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Accumulation of mitochondrial DNA damage and bioenergetic dysfunction in CSB defective cells

(2009) Pia Ø. Osenbroch et al.   FEBS Journal

Cockayne Syndrome Group B Protein Stimulates Repair of Formamidopyrimidines by NEIL1 DNA Glycosylase

(2009) Meltem Muftuoglu et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Nucleic Acid Binding Activity of Human Cockayne Syndrome B Protein and Identification of Ca2+ as a Novel Metal Cofactor

(2009) Brian R. Berquist et al.   JOURNAL OF MOLECULAR BIOLOGY

Do all of the neurologic diseases in patients with DNA repair gene mutations result from the accumulation of DNA damage?

(2008) P.J. Brooks et al.   DNA REPAIR

Truncated Cockayne Syndrome B Protein Represses Elongation by RNA Polymerase I

(2008) Anton Lebedev et al.   JOURNAL OF MOLECULAR BIOLOGY

Human mitochondrial RNA polymerase primes lagging-strand DNA synthesis in vitro

(2008) S. Wanrooij et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA