Rescue of Cystathionine β-Synthase (CBS) Mutants with Chemical Chaperones

Activation of Mutant Enzyme Function In Vivo by Proteasome Inhibitors and Treatments that Induce Hsp70

(2010) Laishram R. Singh et al.   PLoS Genetics

Modulation of the heme electronic structure and cystathionine β-synthase activity by second coordination sphere ligands: The role of heme ligand switching in redox regulation

(2009) Sangita Singh et al.   JOURNAL OF INORGANIC BIOCHEMISTRY

Converging concepts of protein folding in vitro and in vivo

(2009) F Ulrich Hartl et al.   NATURE STRUCTURAL & MOLECULAR BIOLOGY

Lysosomal Storage Disorders in the Newborn

(2009) O. Staretz-Chacham et al.   PEDIATRICS

Chaperones in control of protein disaggregation

(2008) Krzysztof Liberek et al.   EMBO JOURNAL

Functional Rescue of Mutant Human Cystathionine β-Synthase by Manipulation of Hsp26 and Hsp70 Levels inSaccharomyces cerevisiae

(2008) Laishram R. Singh et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Active Cystathionine β-Synthase Can Be Expressed in Heme-free Systems in the Presence of Metal-substituted Porphyrins or a Chemical Chaperone

(2008) Tomas Majtan et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Protein Misfolding in Conformational Disorders: Rescue of Folding Defects and Chemical Chaperoning

(2008) Paula Leandro et al.   MINI-REVIEWS IN MEDICINAL CHEMISTRY

Modulation of the Activity of Newly Synthesized Human Phenylalanine Hydroxylase Mutant Proteins by Low-Molecular-Weight Compounds

(2008) Cátia Nascimento et al.   PROTEIN JOURNAL

Purification and characterization of the wild type and truncated human cystathionine β-synthase enzymes expressed in E. coli

(2007) Nina Frank et al.   ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS