Emerging therapies for cystic fibrosis lung disease

Clinical evaluation of VX-809, a novel investigational oral F508del-CFTR corrector, in subjects with cystic fibrosis homozygous for the F508del–CFTR mutation

(2010) J.P. Clancy et al.   Journal of Cystic Fibrosis

Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function

(2010) R. Amin et al.   THORAX

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

(2009) F. Van Goor et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Cystic fibrosis gene therapy: successes, failures and hopes for the future

(2009) Uta Griesenbach et al.   Expert Review of Respiratory Medicine

Preventive but Not Late Amiloride Therapy Reduces Morbidity and Mortality of Lung Disease in βENaC-overexpressing Mice

(2008) Zhe Zhou et al.   AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE

CFTR Function and Prospects for Therapy

(2008) John R. Riordan   Annual Review of Biochemistry

Inhaled Mannitol Improves Lung Function in Cystic Fibrosis

(2008) Anna Jaques et al.   CHEST

Plant host and sugar alcohol induced exopolysaccharide biosynthesis in the Burkholderia cepacia complex

(2008) S. J. Bartholdson et al.   MICROBIOLOGY-SGM

Denufosol: A review of studies with inhaled P2Y2 agonists that led to Phase 3

(2008) Donald Kellerman et al.   PULMONARY PHARMACOLOGY & THERAPEUTICS