期刊
CLINICAL REVIEWS IN ALLERGY & IMMUNOLOGY
卷 40, 期 2, 页码 104-116出版社
HUMANA PRESS INC
DOI: 10.1007/s12016-009-8194-2
关键词
Scleroderma; Scleroderma lung disease; Pulmonary arterial hypertension; Interstitial lung disease; Scleroderma-related pulmonary arterial hypertension
Pulmonary involvement is second in frequency only to esophageal involvement as a visceral complication of systemic sclerosis (SSc) and has surpassed renal involvement as the most common cause of death. Interstitial lung disease and pulmonary vascular disease, particularly pulmonary arterial hypertension, are the most commonly encountered types of lung involvement. Chronic aspiration, airway disease, neuromuscular weakness, extrinsic pulmonary restrictive pathology, pleural effusions, pneumothorax, and lung cancer cause clinically significant disease and occur commonly enough to be routinely considered in the assessment of the SSc patient with respiratory symptoms. Affected patients have a significantly worse prognosis than patients with SSc who are free of pulmonary involvement.
作者
我是这篇论文的作者
点击您的名字以认领此论文并将其添加到您的个人资料中。
推荐
暂无数据