The post-transcriptional life of mammalian mitochondrial RNA

C7orf30 specifically associates with the large subunit of the mitochondrial ribosome and is involved in translation

(2012) Bas F. J. Wanschers et al.   NUCLEIC ACIDS RESEARCH

C7orf30 is necessary for biogenesis of the large subunit of the mitochondrial ribosome

(2012) Joanna Rorbach et al.   NUCLEIC ACIDS RESEARCH

Human Mitochondrial tRNAs: Biogenesis, Function, Structural Aspects, and Diseases

(2011) Tsutomu Suzuki et al.   Annual Review of Genetics

The human Suv3 helicase interacts with replication protein A and flap endonuclease 1 in the nucleus

(2011) Susanne T. Venø et al.   BIOCHEMICAL JOURNAL

LRPPRC mutation suppresses cytochrome oxidase activity by altering mitochondrial RNA transcript stability in a mouse model

(2011) Fenghao Xu et al.   BIOCHEMICAL JOURNAL

The role of mammalian PPR domain proteins in the regulation of mitochondrial gene expression

(2011) Oliver Rackham et al.   Biochimica et Biophysica Acta-Gene Regulatory Mechanisms

PNPASE and RNA trafficking into mitochondria

(2011) Geng Wang et al.   Biochimica et Biophysica Acta-Gene Regulatory Mechanisms

Contacts between mammalian mitochondrial translational initiation factor 3 and ribosomal proteins in the small subunit

(2011) Md. Emdadul Haque et al.   BIOCHIMICA ET BIOPHYSICA ACTA-PROTEINS AND PROTEOMICS

The Human Mitochondrial Transcriptome

(2011) Tim R. Mercer et al.   CELL

RNA processing in human mitochondria

(2011) Maria I.G. Lopez Sanchez et al.   CELL CYCLE

MTERF4 Regulates Translation by Targeting the Methyltransferase NSUN4 to the Mammalian Mitochondrial Ribosome

(2011) Yolanda Cámara et al.   Cell Metabolism

LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAs

(2011) Benedetta Ruzzenente et al.   EMBO JOURNAL

Uncoupling the Roles of the SUV3 Helicase in Maintenance of Mitochondrial Genome Stability and RNA Degradation

(2011) Xuning Emily Guo et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Apoptosis Induced by Persistent Single-strand Breaks in Mitochondrial Genome

(2011) Anne W. Tann et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Pentatricopeptide Repeat Proteins Stimulate mRNA Adenylation/Uridylation to Activate Mitochondrial Translation in Trypanosomes

(2011) Inna Aphasizheva et al.   MOLECULAR CELL

TEFM (c17orf42) is necessary for transcription of human mtDNA

(2011) Michal Minczuk et al.   NUCLEIC ACIDS RESEARCH

PDE12 removes mitochondrial RNA poly(A) tails and controls translation in human mitochondria

(2011) Joanna Rorbach et al.   NUCLEIC ACIDS RESEARCH

Human 2′-phosphodiesterase localizes to the mitochondrial matrix with a putative function in mitochondrial RNA turnover

(2011) Jesper Buchhave Poulsen et al.   NUCLEIC ACIDS RESEARCH

Localization of Human RNase Z Isoforms: Dual Nuclear/Mitochondrial Targeting of the ELAC2 Gene Product by Alternative Translation Initiation

(2011) Walter Rossmanith   PLoS One

The eukaryotic RNA exosome: Same scaffold but variable catalytic subunits

(2011) Søren Lykke-Andersen et al.   RNA Biology

Involvement of human ELAC2 gene product in 3' end processing of mitochondrial tRNAs

(2011) Lien K. Brzezniak et al.   RNA Biology

Long noncoding RNAs are generated from the mitochondrial genome and regulated by nuclear-encoded proteins

(2011) O. Rackham et al.   RNA

RNA nucleotide methylation

(2011) Yuri Motorin et al.   Wiley Interdisciplinary Reviews-RNA

Defective Mitochondrial mRNA Maturation Is Associated with Spastic Ataxia

(2010) Andrew H. Crosby et al.   AMERICAN JOURNAL OF HUMAN GENETICS

LRPPRC is a mitochondrial matrix protein that is conserved in metazoans

(2010) Fredrik H. Sterky et al.   BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS

Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit

(2010) Sven Dennerlein et al.   BIOCHEMICAL JOURNAL

Leucine-Rich Pentatricopeptide-Repeat Containing Protein Regulates Mitochondrial Transcription

(2010) Neal Sondheimer et al.   BIOCHEMISTRY

Site-Directed Mutants of 16S rRNA Reveal Important RNA Domains for KsgA Function and 30S Subunit Assembly

(2010) Pooja M. Desai et al.   BIOCHEMISTRY

Human mitochondrial mRNAs—like members of all families, similar but different

(2010) Richard J. Temperley et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

RNA turnover in human mitochondria: More questions than answers?

(2010) Lukasz S. Borowski et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

PNPASE Regulates RNA Import into Mitochondria

(2010) Geng Wang et al.   CELL

The human core exosome interacts with differentially localized processive RNases: hDIS3 and hDIS3L

(2010) Rafal Tomecki et al.   EMBO JOURNAL

Dis3-like 1: a novel exoribonuclease associated with the human exosome

(2010) Raymond H J Staals et al.   EMBO JOURNAL

Members of the YjgF/YER057c/UK114 Family of Proteins Inhibit Phosphoribosylamine Synthesisin Vitro

(2010) Jennifer A. Lambrecht et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

LRPPRC and SLIRP Interact in a Ribonucleoprotein Complex That Regulates Posttranscriptional Gene Expression in Mitochondria

(2010) Florin Sasarman et al.   MOLECULAR BIOLOGY OF THE CELL

NOA1 is an essential GTPase required for mitochondrial protein synthesis

(2010) Mateusz Kolanczyk et al.   MOLECULAR BIOLOGY OF THE CELL

ERAL1 is associated with mitochondrial ribosome and elimination of ERAL1 leads to mitochondrial dysfunction and growth retardation

(2010) Takeshi Uchiumi et al.   NUCLEIC ACIDS RESEARCH

Targeting of the cytosolic poly(A) binding protein PABPC1 to mitochondria causes mitochondrial translation inhibition

(2010) Mateusz Wydro et al.   NUCLEIC ACIDS RESEARCH

Unique features of animal mitochondrial translation systems

(2010) Kimitsuna WATANABE   PROCEEDINGS OF THE JAPAN ACADEMY SERIES B-PHYSICAL AND BIOLOGICAL SCIENCES

Modification of 16S ribosomal RNA by the KsgA methyltransferase restructures the 30S subunit to optimize ribosome function

(2010) H. Demirci et al.   RNA

Hungry Codons Promote Frameshifting in Human Mitochondrial Ribosomes

(2010) R. Temperley et al.   SCIENCE

Exonucleases and endonucleases involved in polyadenylation- assisted RNA decay

(2010) Shimyn Slomovic et al.   Wiley Interdisciplinary Reviews-RNA

RETRACTED: mTERF2 Regulates Oxidative Phosphorylation by Modulating mtDNA Transcription

(2009) Tina Wenz et al.   Cell Metabolism

Methylation of 12S rRNA Is Necessary for In Vivo Stability of the Small Subunit of the Mammalian Mitochondrial Ribosome

(2009) Metodi D. Metodiev et al.   Cell Metabolism

Pentatricopeptide repeat domain protein 3 associates with the mitochondrial small ribosomal subunit and regulates translation

(2009) Stefan M.K. Davies et al.   FEBS LETTERS

Evidence for a degradosome-like complex in the mitochondria ofTrypanosoma brucei

(2009) Jonelle L. Mattiacio et al.   FEBS LETTERS

Human Mitochondrial SUV3 and Polynucleotide Phosphorylase Form a 330-kDa Heteropentamer to Cooperatively Degrade Double-stranded RNA with a 3′-to-5′ Directionality

(2009) Dennis Ding-Hwa Wang et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Disruption of Supv3L1 damages the skin and causes sarcopenia, loss of fat, and death

(2009) Erin Paul et al.   MAMMALIAN GENOME

Mutation in TACO1, encoding a translational activator of COX I, results in cytochrome c oxidase deficiency and late-onset Leigh syndrome

(2009) Woranontee Weraarpachai et al.   NATURE GENETICS

Pentatricopeptide repeat domain protein 1 lowers the levels of mitochondrial leucine tRNAs in cells

(2009) Oliver Rackham et al.   NUCLEIC ACIDS RESEARCH

Fine-tuning of the ribosomal decoding center by conserved methyl-modifications in the Escherichia coli 16S rRNA

(2009) Satoshi Kimura et al.   NUCLEIC ACIDS RESEARCH

Human mitochondrial RNA turnover caught in flagranti: involvement of hSuv3p helicase in RNA surveillance

(2009) Roman J. Szczesny et al.   NUCLEIC ACIDS RESEARCH

How Do Human Cells React to the Absence of Mitochondrial DNA?

(2009) Rossana Mineri et al.   PLoS One

Polyadenylation-assisted RNA degradation processes in plants

(2009) Heike Lange et al.   TRENDS IN PLANT SCIENCE

A Computational Screen for Regulators of Oxidative Phosphorylation Implicates SLIRP in Mitochondrial RNA Homeostasis

(2009) Joshua M. Baughman et al.   PLoS Genetics

A Mitochondrial Protein Compendium Elucidates Complex I Disease Biology

(2008) David J. Pagliarini et al.   CELL

RNase P without RNA: Identification and Functional Reconstitution of the Human Mitochondrial tRNA Processing Enzyme

(2008) Johann Holzmann et al.   CELL

3′ adenylation determines mRNA abundance and monitors completion of RNA editing in T. brucei mitochondria

(2008) Ronald D Etheridge et al.   EMBO JOURNAL

Modulation of PGC-1 Coactivator Pathways in Brown Fat Differentiation through LRP130

(2008) Marcus P. Cooper et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Native R-loops Persist throughout the Mouse Mitochondrial DNA Genome

(2008) Timothy A. Brown et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Role of SUV3 Helicase in Maintaining Mitochondrial Homeostasis in Human Cells

(2008) Lily Khidr et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

The 3′ Ends of Mature Transcripts Are Generated by a Processosome Complex in Fission Yeast Mitochondria

(2008) Bastian Hoffmann et al.   JOURNAL OF MOLECULAR BIOLOGY

A conserved rRNA methyltransferase regulates ribosome biogenesis

(2008) Zhili Xu et al.   NATURE STRUCTURAL & MOLECULAR BIOLOGY

The exonuclease ERI-1 has a conserved dual role in 5.8S rRNA processing and RNAi

(2008) Harrison W Gabel et al.   NATURE STRUCTURAL & MOLECULAR BIOLOGY

EXOG, a novel paralog of Endonuclease G in higher eukaryotes

(2008) Iwona A. Cymerman et al.   NUCLEIC ACIDS RESEARCH

Pentatricopeptide repeat proteins: a socket set for organelle gene expression

(2008) C SCHMITZLINNEWEBER et al.   TRENDS IN PLANT SCIENCE