Effect of genetic background on onset and disease progression in the SOD1-G93A model of amyotrophic lateral sclerosis

Effect of genetic background on phenotype variability in transgenic mouse models of amyotrophic lateral sclerosis: A window of opportunity in the search for genetic modifiers

(2011) Terry D. Heiman-Patterson et al.   Amyotrophic Lateral Sclerosis

Electrophysiological analysis of a murine model of motoneuron disease

(2011) Renzo Mancuso et al.   CLINICAL NEUROPHYSIOLOGY

A comprehensive assessment of the SOD1G93A low-copy transgenic mouse, which models human amyotrophic lateral sclerosis

(2011) A. Acevedo-Arozena et al.   Disease Models & Mechanisms

Corticospinal Motor Neurons and Related Subcerebral Projection Neurons Undergo Early and Specific Neurodegeneration in hSOD1G93A Transgenic ALS Mice

(2011) P. H. Ozdinler et al.   JOURNAL OF NEUROSCIENCE

Expanded GGGGCC Hexanucleotide Repeat in Noncoding Region of C9ORF72 Causes Chromosome 9p-Linked FTD and ALS

(2011) Mariely DeJesus-Hernandez et al.   NEURON

A Hexanucleotide Repeat Expansion in C9ORF72 Is the Cause of Chromosome 9p21-Linked ALS-FTD

(2011) Alan E. Renton et al.   NEURON

Outbred ICR/CD1 mice display more severe neuroinflammation mediated by microglial TLR4/CD14 activation than inbred C57Bl/6 mice

(2011) M. Nikodemova et al.   NEUROSCIENCE

Astroglial Inhibition of NF-κB Does Not Ameliorate Disease Onset and Progression in a Mouse Model for Amyotrophic Lateral Sclerosis (ALS)

(2011) Claudia Crosio et al.   PLoS One

Guidelines for preclinical animal research in ALS/MND: A consensus meeting

(2010) Albert C. Ludolph et al.   Amyotrophic Lateral Sclerosis

Energy metabolism in amyotrophic lateral sclerosis

(2010) Luc Dupuis et al.   LANCET NEUROLOGY

Wild-type and mutant SOD1 share an aberrant conformation and a common pathogenic pathway in ALS

(2010) Daryl A Bosco et al.   NATURE NEUROSCIENCE

Genetic background and gender effects on gross phenotypes in congenic lines of ALS2/alsin-deficient mice

(2010) Shinji Hadano et al.   NEUROSCIENCE RESEARCH

Neuromuscular junction destruction during amyotrophic lateral sclerosis: insights from transgenic models

(2009) Luc Dupuis et al.   CURRENT OPINION IN PHARMACOLOGY

An ENU-induced mutation in mouse glycyl-tRNA synthetase (GARS) causes peripheral sensory and motor phenotypes creating a model of Charcot-Marie-Tooth type 2D peripheral neuropathy

(2009) F. Achilli et al.   Disease Models & Mechanisms

Fragment C of tetanus toxin, more than a carrier. Novel perspectives in non-viral ALS gene therapy

(2009) María Moreno-Igoa et al.   JOURNAL OF MOLECULAR MEDICINE-JMM

Cytoskeletal and Activity-Related Changes in Spinal Motoneurons after Root Avulsion

(2009) Clara Penas et al.   JOURNAL OF NEUROTRAUMA

Motoneuron survival is promoted by specific exercise in a mouse model of amyotrophic lateral sclerosis

(2009) Séverine Deforges et al.   JOURNAL OF PHYSIOLOGY-LONDON

Tests to assess motor phenotype in mice: a user's guide

(2009) Simon P. Brooks et al.   NATURE REVIEWS NEUROSCIENCE

Amyotrophic lateral sclerosis

(2009) Lokesh C Wijesekera et al.   Orphanet Journal of Rare Diseases

Review: Evidence-based drug treatment in amyotrophic lateral sclerosis and upcoming clinical trials

(2009) Albert C. Ludolph et al.   Therapeutic Advances in Neurological Disorders

Human mesenchymal stem cell transplantation extends survival, improves motor performance and decreases neuroinflammation in mouse model of amyotrophic lateral sclerosis

(2008) A. Vercelli et al.   NEUROBIOLOGY OF DISEASE

Transgenics, toxicity and therapeutics in rodent models of mutant SOD1-mediated familial ALS

(2008) B TURNER et al.   PROGRESS IN NEUROBIOLOGY