Does the ΔF508-CFTR mutation induce a proinflammatory response in human airway epithelial cells?

A novel approach to analyze gene expression data demonstrates that the ΔF508 mutation in CFTR downregulates the antigen presentation pathway

(2010) Thomas H. Hampton et al.   AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

Specific Resistance to Pseudomonas aeruginosa Infection in Zebrafish Is Mediated by the Cystic Fibrosis Transmembrane Conductance Regulator

(2010) R. T. Phennicie et al.   INFECTION AND IMMUNITY

Defective CFTR induces aggresome formation and lung inflammation in cystic fibrosis through ROS-mediated autophagy inhibition

(2010) Alessandro Luciani et al.   NATURE CELL BIOLOGY

Tobramycin and FDA-Approved Iron Chelators EliminatePseudomonas aeruginosaBiofilms on Cystic Fibrosis Cells

(2009) Sophie Moreau-Marquis et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

TLR-4–Mediated Innate Immunity Is Reduced in Cystic Fibrosis Airway Cells

(2009) Gerrit John et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

AMPK Agonists Ameliorate Sodium and Fluid Transport and Inflammation in Cystic Fibrosis Airway Epithelial Cells

(2009) Michael M. Myerburg et al.   AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY

Cystic fibrosis

(2009) Brian P O'Sullivan et al.   LANCET

CFTR Is a Negative Regulator of NFκB Mediated Innate Immune Response

(2009) Neeraj Vij et al.   PLoS One

Pseudomonas aeruginosa Exploits Lipid A and Muropeptides Modification as a Strategy to Lower Innate Immunity during Cystic Fibrosis Lung Infection

(2009) Cristina Cigana et al.   PLoS One

The Role of Inhaled Corticosteroids in the Management of Cystic Fibrosis

(2009) Kristie R. Ross et al.   PEDIATRIC DRUGS

CFTR Function and Prospects for Therapy

(2008) John R. Riordan   Annual Review of Biochemistry

The Role of SGK and CFTR in Acute Adaptation to Seawater in Fundulus Heteroclitus

(2008) Joseph Shaw et al.   CELLULAR PHYSIOLOGY AND BIOCHEMISTRY

Airway Inflammation in Cystic Fibrosis

(2008) Arnon Elizur et al.   CHEST

In Vitro Analysis of Tobramycin-Treated Pseudomonas aeruginosa Biofilms on Cystic Fibrosis-Derived Airway Epithelial Cells

(2008) G. G. Anderson et al.   INFECTION AND IMMUNITY

NCBI GEO: archive for high-throughput functional genomic data

(2008) T. Barrett et al.   NUCLEIC ACIDS RESEARCH

Pseudomonas aeruginosa biofilm formation in the cystic fibrosis airway

(2007) Sophie Moreau-Marquis et al.   PULMONARY PHARMACOLOGY & THERAPEUTICS