Aberrant Mitochondrial Dynamics and Exacerbated Response to Neuroinflammation in a Novel Mouse Model of CMT2A
出版年份 2021 全文链接
标题
Aberrant Mitochondrial Dynamics and Exacerbated Response to Neuroinflammation in a Novel Mouse Model of CMT2A
作者
关键词
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出版物
INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES
Volume 22, Issue 21, Pages 11569
出版商
MDPI AG
发表日期
2021-10-27
DOI
10.3390/ijms222111569
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注意:仅列出部分参考文献,下载原文获取全部文献信息。- Neuronal Mitochondria Modulation of LPS-Induced Neuroinflammation
- (2020) Micah Harland et al. JOURNAL OF NEUROSCIENCE
- Degradation of engulfed mitochondria is rate-limiting in Optineurin-mediated mitophagy in neurons
- (2020) Chantell S Evans et al. eLife
- Innate Immune Functions of Astrocytes are Dependent Upon Tumor Necrosis Factor-Alpha
- (2020) Kyla R. Rodgers et al. Scientific Reports
- Sex differences of inflammatory and immune response in pups of Wistar rats with SIRS
- (2020) Anna M. Kosyreva et al. Scientific Reports
- Mitofusin 2 in Macrophages Links Mitochondrial ROS Production, Cytokine Release, Phagocytosis, Autophagy, and Bactericidal Activity
- (2020) Juan Tur et al. Cell Reports
- MFN2 mutations in Charcot-Marie-Tooth disease alter mitochondria-associated ER membrane function but do not impair bioenergetics
- (2019) Delfina Larrea et al. HUMAN MOLECULAR GENETICS
- Altered interplay between endoplasmic reticulum and mitochondria in Charcot–Marie–Tooth type 2A neuropathy
- (2019) Nathalie Bernard-Marissal et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Restoring mitofusin balance prevents axonal degeneration in a Charcot-Marie-Tooth type 2A model
- (2019) Yueqin Zhou et al. JOURNAL OF CLINICAL INVESTIGATION
- Mitofusin 2 Participates in Mitophagy and Mitochondrial Fusion Against Angiotensin II-Induced Cardiomyocyte Injury
- (2019) Wenjun Xiong et al. Frontiers in Physiology
- Mutation spectrum of Charcot‐Marie‐Tooth disease among the Han Chinese in Taiwan
- (2019) Yun‐Hsin Hsu et al. Annals of Clinical and Translational Neurology
- Neuroinflammation induced by lipopolysaccharide causes cognitive impairment in mice
- (2019) Jiayi Zhao et al. Scientific Reports
- Prevalence of Charcot-Marie-Tooth disease across the lifespan: a population-based epidemiological study
- (2019) Alice Theadom et al. BMJ Open
- Structural insights of human mitofusin-2 into mitochondrial fusion and CMT2A onset
- (2019) Yu-Jie Li et al. Nature Communications
- The Charcot–Marie Tooth Disease Mutation R94Q in MFN2 Decreases ATP Production but Increases Mitochondrial Respiration under Conditions of Mild Oxidative Stress
- (2019) Christina Wolf et al. Cells
- Dual microglia effects on blood brain barrier permeability induced by systemic inflammation
- (2019) Koichiro Haruwaka et al. Nature Communications
- Intrathecal gene therapy in mouse models expressing CMT1X mutations
- (2018) A Kagiava et al. HUMAN MOLECULAR GENETICS
- Structural basis for GTP hydrolysis and conformational change of MFN1 in mediating membrane fusion
- (2018) Liming Yan et al. NATURE STRUCTURAL & MOLECULAR BIOLOGY
- Structural basis for GTP hydrolysis and conformational change of MFN1 in mediating membrane fusion
- (2018) Liming Yan et al. NATURE STRUCTURAL & MOLECULAR BIOLOGY
- Clinical and genetic diversities of Charcot-Marie-Tooth disease with MFN2 mutations in a large case study
- (2017) Masahiro Ando et al. JOURNAL OF THE PERIPHERAL NERVOUS SYSTEM
- Human biallelic MFN2 mutations induce mitochondrial dysfunction, upper body adipose hyperplasia, and suppression of leptin expression
- (2017) Nuno Rocha et al. eLife
- Age and sex differences in immune response following LPS treatment in mice
- (2016) Kyle Chiman Cai et al. BRAIN BEHAVIOR AND IMMUNITY
- Correcting mitochondrial fusion by manipulating mitofusin conformations
- (2016) Antonietta Franco et al. NATURE
- Systemic inflammation disrupts oligodendrocyte gap junctions and induces ER stress in a model of CNS manifestations of X-linked Charcot-Marie-Tooth disease
- (2016) Margarita Olympiou et al. Acta Neuropathologica Communications
- Gender Difference in Bacteria Endotoxin-Induced Inflammatory and Anorexic Responses
- (2016) Shiu-Ming Kuo PLoS One
- Mice Hemizygous for a Pathogenic Mitofusin-2 Allele Exhibit Hind Limb/Foot Gait Deficits and Phenotypic Perturbations in Nerve and Muscle
- (2016) Peter Bannerman et al. PLoS One
- Sirtuin 1 suppresses mitochondrial dysfunction of ischemic mouse livers in a mitofusin 2-dependent manner
- (2015) T G Biel et al. CELL DEATH AND DIFFERENTIATION
- Homozygous mutations inMFN2cause multiple symmetric lipomatosis associated with neuropathy
- (2015) Sarah L. Sawyer et al. HUMAN MOLECULAR GENETICS
- Early onset Charcot-Marie-Tooth neuropathy type 2A and severe developmental delay: expanding the clinical phenotype of MFN2-related neuropathy
- (2015) Maria Tufano et al. JOURNAL OF THE PERIPHERAL NERVOUS SYSTEM
- A cohort study ofMFN2mutations and phenotypic spectrums in Charcot-Marie-Tooth disease 2A patients
- (2014) B.-O. Choi et al. CLINICAL GENETICS
- Characterization of the mitofusin 2 R94W mutation in a knock-in mouse model
- (2014) Alleene V. Strickland et al. JOURNAL OF THE PERIPHERAL NERVOUS SYSTEM
- Systemic injection of LPS induces region-specific neuroinflammation and mitochondrial dysfunction in normal mouse brain
- (2014) Haneul Noh et al. NEUROCHEMISTRY INTERNATIONAL
- Assessing Functional Performance in the Mdx Mouse Model
- (2014) Annemieke Aartsma-Rus et al. Jove-Journal of Visualized Experiments
- Mitochondrial dynamics modulate the expression of pro-inflammatory mediators in microglial cells
- (2013) Junghyung Park et al. JOURNAL OF NEUROCHEMISTRY
- Mitofusin 2 mutations affect mitochondrial function by mitochondrial DNA depletion
- (2012) Stefan Vielhaber et al. ACTA NEUROPATHOLOGICA
- Spatial Parkin Translocation and Degradation of Damaged Mitochondria via Mitophagy in Live Cortical Neurons
- (2012) Qian Cai et al. CURRENT BIOLOGY
- The MFN2 gene is responsible for mitochondrial DNA instability and optic atrophy 'plus' phenotype
- (2011) C. Rouzier et al. BRAIN
- Charcot–Marie–Tooth disease in Northern England: Figure 1
- (2011) Charlotte Foley et al. JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY
- Expression of mitofusin 2R94Q in a transgenic mouse leads to Charcot–Marie–Tooth neuropathy type 2A
- (2010) Romain Cartoni et al. BRAIN
- Genetic and clinical aspects of Charcot-Marie-Tooth's disease
- (2010) H. Skre CLINICAL GENETICS
- Mitofusin 2 Is Necessary for Transport of Axonal Mitochondria and Interacts with the Miro/Milton Complex
- (2010) A. Misko et al. JOURNAL OF NEUROSCIENCE
- Interleukin-6 Released from Fibroblasts Is Essential for Up-regulation of Matrix Metalloproteinase-1 Expression by U937 Macrophages in Coculture
- (2009) Kamala P. Sundararaj et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Rod-Shaped Monocytes Patrol the Brain Vasculature and Give Rise to Perivascular Macrophages under the Influence of Proinflammatory Cytokines and Angiopoietin-2
- (2008) J. Audoy-Remus et al. JOURNAL OF NEUROSCIENCE
- Mitofusin 2 tethers endoplasmic reticulum to mitochondria
- (2008) Olga Martins de Brito et al. NATURE
- Mutated mitofusin 2 presents with intrafamilial variability and brain mitochondrial dysfunction
- (2008) R. D. Bo et al. NEUROLOGY
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