Bezafibrate activation of PPAR drives disturbances in mitochondrial redox bioenergetics and decreases the viability of cells from patients with VLCAD deficiency
出版年份 2021 全文链接
标题
Bezafibrate activation of PPAR drives disturbances in mitochondrial redox bioenergetics and decreases the viability of cells from patients with VLCAD deficiency
作者
关键词
Mitochondria, Glutathione, Thiols, Bezafibrate, PPAR, Oxidative stress, ROS, VLCAD, VLCAD deficiency, Inborn errors of metabolism, Fatty acids oxidation deficiency
出版物
BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE
Volume 1867, Issue 6, Pages 166100
出版商
Elsevier BV
发表日期
2021-02-06
DOI
10.1016/j.bbadis.2021.166100
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