Withdrawal of dornase alfa increases ventilation inhomogeneity in children with cystic fibrosis

Lung clearance index-triggered intervention in children with cystic fibrosis – A randomised pilot study

(2020) Christian Voldby et al.   Journal of Cystic Fibrosis

Abnormal preschool Lung Clearance Index (LCI) reflects clinical status and predicts lower spirometry later in childhood in cystic fibrosis

(2019) K.M. Hardaker et al.   Journal of Cystic Fibrosis

Cystic fibrosis - an example of personalized and precision medicine

(2019) Marianne Skov et al.   APMIS

Inhaled hypertonic saline in preschool children with cystic fibrosis (SHIP): a multicentre, randomised, double-blind, placebo-controlled trial

(2019) Felix Ratjen et al.   Lancet Respiratory Medicine

Integrating the multiple breath washout test into international multicentre trials

(2019) Clare Saunders et al.   Journal of Cystic Fibrosis

Normative data for multiple breath washout outcomes in school-aged Caucasian children

(2019) Pinelopi Anagnostopoulou et al.   EUROPEAN RESPIRATORY JOURNAL

ECFS best practice guidelines: the 2018 revision

(2018) Carlo Castellani et al.   Journal of Cystic Fibrosis

Elevated lung clearance index in infants with cystic fibrosis shortly after birth

(2017) Elisabeth Kieninger et al.   EUROPEAN RESPIRATORY JOURNAL

Progressive ventilation inhomogeneity in infants with cystic fibrosis after pulmonary infection

(2015) Shannon J. Simpson et al.   EUROPEAN RESPIRATORY JOURNAL

Consensus statement for inert gas washout measurement using multiple- and single- breath tests

(2013) Paul D. Robinson et al.   EUROPEAN RESPIRATORY JOURNAL

Lung clearance index: Evidence for use in clinical trials in cystic fibrosis

(2013) L. Kent et al.   Journal of Cystic Fibrosis

Multi-ethnic reference values for spirometry for the 3–95-yr age range: the global lung function 2012 equations

(2012) Philip H. Quanjer et al.   EUROPEAN RESPIRATORY JOURNAL

Erratum to: Psychometric evaluation of the Cystic Fibrosis Questionnaire-Revised in a national, US sample

(2012) Alexandra L. Quittner et al.   QUALITY OF LIFE RESEARCH

Improved treatment response to dornase alfa in cystic fibrosis patients using controlled inhalation

(2011) E. M. Bakker et al.   EUROPEAN RESPIRATORY JOURNAL

Pulmonary exacerbation: Towards a definition for use in clinical trials. Report from the EuroCareCF Working Group on outcome parameters in clinical trials

(2011) D. Bilton et al.   Journal of Cystic Fibrosis

The effect of dornase alfa on ventilation inhomogeneity in patients with cystic fibrosis

(2010) R. Amin et al.   EUROPEAN RESPIRATORY JOURNAL

Cystic fibrosis lung disease starts in the small airways: Can we treat it more effectively?

(2010) Harm A.W.M. Tiddens et al.   PEDIATRIC PULMONOLOGY

Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function

(2010) R. Amin et al.   THORAX

Inert Gas Washout: Theoretical Background and Clinical Utility in Respiratory Disease

(2009) Paul D. Robinson et al.   RESPIRATION