Poly (A) tail length of human mitochondrial mRNAs is tissue-specific and a mutation in LRPPRC results in transcript-specific patterns of deadenylation

Structural basis of mitochondrial translation

(2020) Shintaro Aibara et al.   eLife

Loss of hepatic LRPPRC alters mitochondrial bioenergetics, regulation of permeability transition and trans-membrane ROS diffusion

(2017) Alexanne Cuillerier et al.   HUMAN MOLECULAR GENETICS

FASTKD1 and FASTKD4 have opposite effects on expression of specific mitochondrial RNAs, depending upon their endonuclease-like RAP domain

(2017) Erik Boehm et al.   NUCLEIC ACIDS RESEARCH

LRPPRC-mediated folding of the mitochondrial transcriptome

(2017) Stefan J. Siira et al.   Nature Communications

SLIRP stabilizes LRPPRC via an RRM–PPR protein interface

(2016) Henrik Spåhr et al.   NUCLEIC ACIDS RESEARCH

LRPPRCmutations cause early-onset multisystem mitochondrial disease outside of the French-Canadian population

(2015) Monika Oláhová et al.   BRAIN

Tissue-specific responses to the LRPPRC founder mutation in French Canadian Leigh Syndrome

(2014) F. Sasarman et al.   HUMAN MOLECULAR GENETICS

A human mitochondrial poly(A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression

(2014) William C. Wilson et al.   HUMAN MOLECULAR GENETICS

GRSF1 Regulates RNA Processing in Mitochondrial RNA Granules

(2013) Alexis A. Jourdain et al.   Cell Metabolism

The Mitochondrial RNA-Binding Protein GRSF1 Localizes to RNA Granules and Is Required for Posttranscriptional Mitochondrial Gene Expression

(2013) Hana Antonicka et al.   Cell Metabolism

Organelle transcriptomes: products of a deconstructed genome

(2013) Ian D Small et al.   CURRENT OPINION IN MICROBIOLOGY

LRPPRC/SLIRP suppresses PNPase-mediated mRNA decay and promotes polyadenylation in human mitochondria

(2012) Takeshi Chujo et al.   NUCLEIC ACIDS RESEARCH

Human mitochondrial RNA decay mediated by PNPase–hSuv3 complex takes place in distinct foci

(2012) Lukasz S. Borowski et al.   NUCLEIC ACIDS RESEARCH

LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAs

(2011) Benedetta Ruzzenente et al.   EMBO JOURNAL

Human mitochondrial mRNAs—like members of all families, similar but different

(2010) Richard J. Temperley et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

LRPPRC and SLIRP Interact in a Ribonucleoprotein Complex That Regulates Posttranscriptional Gene Expression in Mitochondria

(2010) Florin Sasarman et al.   MOLECULAR BIOLOGY OF THE CELL