Regional metabolic signatures in the Ndufs4(KO) mouse brain implicate defective glutamate/α-ketoglutarate metabolism in mitochondrial disease

标题
Regional metabolic signatures in the Ndufs4(KO) mouse brain implicate defective glutamate/α-ketoglutarate metabolism in mitochondrial disease
作者
关键词
Mitochondria, Genetics, Metabolism, Rapamycin, Reactive oxygen species, Mouse, Leigh syndrome
出版物
MOLECULAR GENETICS AND METABOLISM
Volume 130, Issue 2, Pages 118-132
出版商
Elsevier BV
发表日期
2020-04-04
DOI
10.1016/j.ymgme.2020.03.007

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