Ube3a reinstatement mitigates epileptogenesis in Angelman syndrome model mice

Effect of epilepsy on autism symptoms in Angelman syndrome

(2018) Kristin A. Bakke et al.   Molecular Autism

Strain-dependence of the Angelman Syndrome phenotypes in Ube3a maternal deficiency mice

(2017) Heather A. Born et al.   Scientific Reports

Eight Flurothyl-Induced Generalized Seizures Lead to the Rapid Evolution of Spontaneous Seizures in Mice: A Model of Epileptogenesis with Seizure Remission

(2016) S. B. Kadiyala et al.   JOURNAL OF NEUROSCIENCE

Casting a Wide Net: Role of Perineuronal Nets in Neural Plasticity

(2016) Barbara A. Sorg et al.   JOURNAL OF NEUROSCIENCE

Protein Delivery of an Artificial Transcription Factor Restores Widespread Ube3a Expression in an Angelman Syndrome Mouse Brain

(2016) Barbara J Bailus et al.   MOLECULAR THERAPY

Angelman syndrome — insights into a rare neurogenetic disorder

(2016) Karin Buiting et al.   Nature Reviews Neurology

GABAergic Neuron-Specific Loss of Ube3a Causes Angelman Syndrome-Like EEG Abnormalities and Enhances Seizure Susceptibility

(2016) Matthew C. Judson et al.   NEURON

Perineuronal net degradation in epilepsy

(2015) Elyse K. Rankin-Gee et al.   EPILEPSIA

Spatiotemporal differences in the c-fos pathway between C57BL/6J and DBA/2J mice following flurothyl-induced seizures: A dissociation of hippocampal Fos from seizure activity

(2015) Sridhar B. Kadiyala et al.   EPILEPSY RESEARCH

Ube3a reinstatement identifies distinct developmental windows in a murine Angelman syndrome model

(2015) Sara Silva-Santos et al.   JOURNAL OF CLINICAL INVESTIGATION

Seizure-like activity in a juvenile Angelman syndrome mouse model is attenuated by reducingArcexpression

(2015) Caleigh Mandel-Brehm et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Towards a therapy for Angelman syndrome by targeting a long non-coding RNA

(2014) Linyan Meng et al.   NATURE

Advantages of Repeated Low Dose against Single High Dose of Kainate in C57BL/6J Mouse Model of Status Epilepticus: Behavioral and Electroencephalographic Studies

(2014) Karen Tse et al.   PLoS One

Modeling Transformations of Neurodevelopmental Sequences across Mammalian Species

(2013) A. D. Workman et al.   JOURNAL OF NEUROSCIENCE

Persistent decrease in multiple components of the perineuronal net following status epilepticus

(2012) Paulette A. McRae et al.   EUROPEAN JOURNAL OF NEUROSCIENCE

The perineuronal net component of the extracellular matrix in plasticity and epilepsy

(2012) Paulette A. McRae et al.   NEUROCHEMISTRY INTERNATIONAL

Topoisomerase inhibitors unsilence the dormant allele of Ube3a in neurons

(2011) Hsien-Sung Huang et al.   NATURE

Adeno-Associated Virus-Mediated Rescue of the Cognitive Defects in a Mouse Model for Angelman Syndrome

(2011) Jennifer L. Daily et al.   PLoS One

Clinical and genetic aspects of Angelman syndrome

(2010) Charles A Williams et al.   GENETICS IN MEDICINE

Aggrecan expression, a component of the inhibitory interneuron perineuronal net, is altered following an early-life seizure

(2010) Paulette A. McRae et al.   NEUROBIOLOGY OF DISEASE

Epilepsy in Angelman syndrome: A questionnaire-based assessment of the natural history and current treatment options

(2009) Ronald L. Thibert et al.   EPILEPSIA

Seizures Beget Seizures in Temporal Lobe Epilepsies: The Boomerang Effects of Newly Formed Aberrant Kainatergic Synapses

(2008) Yehezkel Ben-Ari et al.   Epilepsy Currents

E/I balance and GABAA receptor plasticity

(2008) Jean-Marc Fritschy   Frontiers in Molecular Neuroscience