Strain Specific Resistance to Murine Scrapie Associated with a Naturally Occurring Human Prion Protein Polymorphism at Residue 171

Heterozygosity at Polymorphic Codon 219 in Variant Creutzfeldt-Jakob Disease

(2010) Ana Lukic et al.   ARCHIVES OF NEUROLOGY

Prospective 10-year surveillance of human prion diseases in Japan

(2010) I. Nozaki et al.   BRAIN

D178N, 129Val and N171S, 129Val Genotype in a Family with Creutzfeldt-Jakob Disease

(2010) Brian S. Appleby et al.   DEMENTIA AND GERIATRIC COGNITIVE DISORDERS

PRNP allelic series from 19 years of prion protein gene sequencing at the MRC Prion Unit

(2010) Jon A. Beck et al.   HUMAN MUTATION

A molecular switch controls interspecies prion disease transmission in mice

(2010) Christina J. Sigurdson et al.   JOURNAL OF CLINICAL INVESTIGATION

Review: Contribution of transgenic models to understanding human prion disease

(2010) J. D. F. Wadsworth et al.   NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY

Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties

(2010) M. T. Bishop et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Genetics and molecular pathogenesis of sporadic and hereditary cerebral amyloid angiopathies

(2009) Tamas Revesz et al.   ACTA NEUROPATHOLOGICA

Getting a Grip on Prions: Oligomers, Amyloids, and Pathological Membrane Interactions

(2009) Byron Caughey et al.   Annual Review of Biochemistry

The Unfolding of the Prion Protein Sheds Light on the Mechanisms of Prion Susceptibility and Species Barrier

(2009) Philip J. Robinson et al.   BIOCHEMISTRY

Prion protein misfolding and disease

(2009) Roger A Moore et al.   CURRENT OPINION IN STRUCTURAL BIOLOGY

A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP

(2009) W. Yang et al.   JOURNAL OF NEUROSCIENCE

Spontaneous Generation of Prion Infectivity in Fatal Familial Insomnia Knockin Mice

(2009) Walker S. Jackson et al.   NEURON

A Novel Protective Prion Protein Variant that Colocalizes with Kuru Exposure

(2009) Simon Mead et al.   NEW ENGLAND JOURNAL OF MEDICINE

Crossing the Species Barrier by PrPSc Replication In Vitro Generates Unique Infectious Prions

(2008) Joaquín Castilla et al.   CELL

Transmissible spongiform encephalopathies

(2008) James J. Sejvar et al.   JAVMA-JOURNAL OF THE AMERICAN VETERINARY MEDICAL ASSOCIATION

Human Prion Protein (PrP) 219K Is Converted to PrPScbut Shows Heterozygous Inhibition in Variant Creutzfeldt-Jakob Disease Infection

(2008) Masaki Hizume et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

In vitro amplification of PrPSc derived from the brain and blood of sheep infected with scrapie

(2008) L. Thorne et al.   JOURNAL OF GENERAL VIROLOGY

NMR Structure of the Bank Vole Prion Protein at 20 °C Contains a Structured Loop of Residues 165–171

(2008) Barbara Christen et al.   JOURNAL OF MOLECULAR BIOLOGY

Mutant Prion Protein Expression Causes Motor and Memory Deficits and Abnormal Sleep Patterns in a Transgenic Mouse Model

(2008) Sara Dossena et al.   NEURON

De novo generation of a transmissible spongiform encephalopathy by mouse transgenesis

(2008) C. J. Sigurdson et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

Atypical/Nor98 scrapie: properties of the agent, genetics, and epidemiology

(2008) Sylvie L. Benestad et al.   VETERINARY RESEARCH

In vitro strain adaptation of CWD prions by serial protein misfolding cyclic amplification

(2008) Crystal Meyerett et al.   VIROLOGY