Autophagy activators rescue and alleviate pathogenesis of a mouse model with proteinopathies of the TAR DNA-binding protein 43

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Rapamycin treatment augments motor neuron degeneration in SOD1G93Amouse model of amyotrophic lateral sclerosis

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Understanding the role of TDP-43 and FUS/TLS in ALS and beyond

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Regulation of Autophagy by Neuropathological Protein TDP-43

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Long pre-mRNA depletion and RNA missplicing contribute to neuronal vulnerability from loss of TDP-43

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Rapamycin promotes β-amyloid production via ADAM-10 inhibition

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TDP-43 and FUS/TLS: emerging roles in RNA processing and neurodegeneration

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Molecular Interplay between Mammalian Target of Rapamycin (mTOR), Amyloid-β, and Tau

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Elevated expression of TDP-43 in the forebrain of mice is sufficient to cause neurological and pathological phenotypes mimicking FTLD-U

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Regulation of TDP-43 aggregation by phosphorylation andp62/SQSTM1

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TAR DNA-binding protein 43 in neurodegenerative disease

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Selective Molecular Alterations in the Autophagy Pathway in Patients with Lewy Body Disease and in Models of α-Synucleinopathy

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Inhibition of mTOR by Rapamycin Abolishes Cognitive Deficits and Reduces Amyloid-β Levels in a Mouse Model of Alzheimer's Disease

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Phosphorylation of S409/410 of TDP-43 is a consistent feature in all sporadic and familial forms of TDP-43 proteinopathies

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Rapamycin Rescues TDP-43 Mislocalization and the Associated Low Molecular Mass Neurofilament Instability

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Lithium induces clearance of protease resistant prion protein in prion-infected cells by induction of autophagy

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Neuropathologic Features of Frontotemporal Lobar Degeneration With Ubiquitin-Positive Inclusions Visualized With Ubiquitin-Binding Protein p62 Immunohistochemistry

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Structural insights into TDP-43 in nucleic-acid binding and domain interactions

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Abeta42-Induced Neurodegeneration via an Age-Dependent Autophagic-Lysosomal Injury in Drosophila

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Autophagy: Basic Principles and Relevance to Disease

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Potentiation of Amyotrophic Lateral Sclerosis (ALS)-associated TDP-43 Aggregation by the Proteasome-targeting Factor, Ubiquilin 1

(2008) Sang Hwa Kim et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

TDP-43: an emerging new player in neurodegenerative diseases

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Multiple roles of TDP-43 in gene expression, splicing regulation, and human disease

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Descriptive epidemiology of amyotrophic lateral sclerosis: new evidence and unsolved issues

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