OsNDUFA9 encoding a mitochondrial complex I subunit is essential for embryo development and starch synthesis in rice

A Heterozygous NDUFV1 Variant Aggravates Mitochondrial Complex I Deficiency in a Family with a Homoplasmic ND1 Variant

(2018) Fabian Baertling et al.   JOURNAL OF PEDIATRICS

Phenotype-genotype correlations in Leigh syndrome: new insights from a multicentre study of 96 patients

(2017) Kalliopi Sofou et al.   JOURNAL OF MEDICAL GENETICS

Dek35 Encodes a PPR Protein that Affects cis -Splicing of Mitochondrial nad4 Intron 1 and Seed Development in Maize

(2017) Xinze Chen et al.   Molecular Plant

The pentatricopeptide repeat protein EMP9 is required for mitochondrial ccmB and rps4 transcript editing, mitochondrial complex biogenesis and seed development in maize

(2017) Yan-Zhuo Yang et al.   NEW PHYTOLOGIST

Emp10 encodes a mitochondrial PPR protein that affects the cis -splicing of nad2 intron 1 and seed development in maize

(2017) Manjun Cai et al.   PLANT JOURNAL

Ndufs4 related Leigh syndrome: A case report and review of the literature

(2016) Juan Darío Ortigoza-Escobar et al.   MITOCHONDRION

MEGA7: Molecular Evolutionary Genetics Analysis Version 7.0 for Bigger Datasets

(2016) Sudhir Kumar et al.   MOLECULAR BIOLOGY AND EVOLUTION

Accessory subunits are integral for assembly and function of human mitochondrial complex I

(2016) David A. Stroud et al.   NATURE

EMPTY PERICARP16 is required for mitochondrialnad2intron 4cis-splicing, complex I assembly and seed development in maize

(2016) Zhihui Xiu et al.   PLANT JOURNAL

WHITE PANICLE1, a Val-tRNA Synthetase Regulating Chloroplast Ribosome Biogenesis in Rice, Is Essential for Early Chloroplast Development

(2016) Yunlong Wang et al.   PLANT PHYSIOLOGY

FLOURY ENDOSPERM7encodes a regulator of starch synthesis and amyloplast development essential for peripheral endosperm development in rice

(2015) Long Zhang et al.   JOURNAL OF EXPERIMENTAL BOTANY

Complete Mitochondrial Complex I Deficiency Induces an Up-Regulation of Respiratory Fluxes That Is Abolished by Traces of Functional Complex I

(2015) Kristina Kühn et al.   PLANT PHYSIOLOGY

The SLOW GROWTH3 Pentatricopeptide Repeat Protein Is Required for the Splicing of MitochondrialNADH Dehydrogenase Subunit7Intron 2 in Arabidopsis

(2015) Wei-Yu Hsieh et al.   PLANT PHYSIOLOGY

ND3, ND1 and 39kDa subunits are more exposed in the de-active form of bovine mitochondrial complex I

(2014) Marion Babot et al.   BIOCHIMICA ET BIOPHYSICA ACTA-BIOENERGETICS

nMAT4, a maturase factor required fornad1pre-mRNA processing and maturation, is essential for holocomplex I biogenesis in Arabidopsis mitochondria

(2014) Sigal Cohen et al.   PLANT JOURNAL

Small kernel 1encodes a pentatricopeptide repeat protein required for mitochondrialnad7transcript editing and seed development in maize(Zea mays)and rice(Oryza sativa)

(2014) Xiao-Jie Li et al.   PLANT JOURNAL

FLOURY ENDOSPERM6encodes a CBM48 domain-containing protein involved in compound granule formation and starch synthesis in rice endosperm

(2014) Cheng Peng et al.   PLANT JOURNAL

TRANSLOCASE OF THE INNER MEMBRANE9 and 10 Are Essential for Maintaining Mitochondrial Function during Early Embryo Cell and Endosperm Free Nucleus Divisions in Arabidopsis

(2014) Y. Deng et al.   PLANT PHYSIOLOGY

Accessory subunits of mitochondrial complex I

(2013) Katarzyna Kmita et al.   BIOCHEMICAL SOCIETY TRANSACTIONS

Conformation-specific crosslinking of mitochondrial complex I

(2013) Margherita Ciano et al.   FEBS LETTERS

Alternative Oxidase: A Mitochondrial Respiratory Pathway to Maintain Metabolic and Signaling Homeostasis during Abiotic and Biotic Stress in Plants

(2013) Greg Vanlerberghe   INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES

The connection between inner membrane topology and mitochondrial function

(2013) Carmen A. Mannella et al.   JOURNAL OF MOLECULAR AND CELLULAR CARDIOLOGY

The Evolutionarily Conserved Iron-Sulfur Protein INDH Is Required for Complex I Assembly and Mitochondrial Translation in Arabidopsis

(2013) M. M. Wydro et al.   PLANT CELL

Empty Pericarp5 Encodes a Pentatricopeptide Repeat Protein That Is Required for Mitochondrial RNA Editing and Seed Development in Maize

(2013) Y.-J. Liu et al.   PLANT CELL

Mitochondrial GCD1 Dysfunction Reveals Reciprocal Cell-to-Cell Signaling during the Maturation of Arabidopsis Female Gametes

(2012) Jian-Jun Wu et al.   DEVELOPMENTAL CELL

PPR2263, a DYW-Subgroup Pentatricopeptide Repeat Protein, Is Required for Mitochondrial nad5 and cob Transcript Editing, Mitochondrion Biogenesis, and Maize Growth

(2012) D. Sosso et al.   PLANT CELL

RiceMPR25encodes a pentatricopeptide repeat protein and is essential for RNA editing ofnad5transcripts in mitochondria

(2012) Takushi Toda et al.   PLANT JOURNAL

A scaffold of accessory subunits links the peripheral arm and the distal proton-pumping module of mitochondrial complex I

(2011) Heike Angerer et al.   BIOCHEMICAL JOURNAL

The Pentatricopeptide Repeat Protein OTP87 Is Essential for RNA Editing ofnad7andatp1Transcripts inArabidopsisMitochondria

(2011) Kamel Hammani et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

The failure to express a protein disulphide isomerase-like protein results in a floury endosperm and an endoplasmic reticulum stress response in rice

(2011) Xiaohua Han et al.   JOURNAL OF EXPERIMENTAL BOTANY

The Subunit Composition of Mitochondrial NADH:Ubiquinone Oxidoreductase (Complex I) FromPichia pastoris

(2010) Hannah R. Bridges et al.   MOLECULAR & CELLULAR PROTEOMICS

Remodeled Respiration in ndufs4 with Low Phosphorylation Efficiency Suppresses Arabidopsis Germination and Growth and Alters Control of Metabolism at Night

(2009) E. H. Meyer et al.   PLANT PHYSIOLOGY

AtnMat2, a nuclear-encoded maturase required for splicing of group-II introns in Arabidopsis mitochondria

(2009) I. Keren et al.   RNA

Assembly of mitochondrial complex I and defects in disease

(2008) Michael Lazarou et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR CELL RESEARCH

A role for the mitochondrial deacetylase Sirt3 in regulating energy homeostasis

(2008) B.-H. Ahn et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA