Pathogenic mutation of UBQLN2 impairs its interaction with UBXD8 and disrupts endoplasmic reticulum-associated protein degradation
出版年份 2013 全文链接
标题
Pathogenic mutation of UBQLN2 impairs its interaction with UBXD8 and disrupts endoplasmic reticulum-associated protein degradation
作者
关键词
-
出版物
JOURNAL OF NEUROCHEMISTRY
Volume 129, Issue 1, Pages 99-106
出版商
Wiley
发表日期
2013-11-12
DOI
10.1111/jnc.12606
参考文献
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注意:仅列出部分参考文献,下载原文获取全部文献信息。- Expression of ALS-linked TDP-43 mutant in astrocytes causes non-cell-autonomous motor neuron death in rats
- (2013) Jianbin Tong et al. EMBO JOURNAL
- A Ubiquitin-like Domain Recruits an Oligomeric Chaperone to a Retrotranslocation Complex in Endoplasmic Reticulum-associated Degradation
- (2013) Yue Xu et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Reactive astrocytes secrete lcn2 to promote neuron death
- (2013) F. Bi et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Entorhinal cortical neurons are the primary targets of FUS mislocalization and ubiquitin aggregation in FUS transgenic rats
- (2012) Cao Huang et al. HUMAN MOLECULAR GENETICS
- Sustained Expression of TDP-43 and FUS in Motor Neurons in Rodent's Lifetime
- (2012) Cao Huang et al. International Journal of Biological Sciences
- TDP-43 Potentiates Alpha-synuclein Toxicity to Dopaminergic Neurons in Transgenic Mice
- (2012) Tian Tian et al. International Journal of Biological Sciences
- Neurotoxin-induced ER stress in mouse dopaminergic neurons involves downregulation of TRPC1 and inhibition of AKT/mTOR signaling
- (2012) Senthil Selvaraj et al. JOURNAL OF CLINICAL INVESTIGATION
- XBP1 depletion precedes ubiquitin aggregation and Golgi fragmentation in TDP-43 transgenic rats
- (2012) Jianbin Tong et al. JOURNAL OF NEUROCHEMISTRY
- Reduced Calreticulin Levels Link Endoplasmic Reticulum Stress and Fas-Triggered Cell Death in Motoneurons Vulnerable to ALS
- (2012) N. Bernard-Marissal et al. JOURNAL OF NEUROSCIENCE
- Dynamic flexibility of the ATPase p97 is important for its interprotomer motion transmission
- (2012) C. Huang et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
- Importin β Interacts with the Endoplasmic Reticulum-associated Degradation Machinery and Promotes Ubiquitination and Degradation of Mutant α1-Antitrypsin
- (2011) Yongwang Zhong et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- Mutant TDP-43 in motor neurons promotes the onset and progression of ALS in rats
- (2011) Cao Huang et al. JOURNAL OF CLINICAL INVESTIGATION
- Mutations in UBQLN2 cause dominant X-linked juvenile and adult-onset ALS and ALS/dementia
- (2011) Han-Xiang Deng et al. NATURE
- FUS Transgenic Rats Develop the Phenotypes of Amyotrophic Lateral Sclerosis and Frontotemporal Lobar Degeneration
- (2011) Cao Huang et al. PLoS Genetics
- Transgenic Rat Model of Neurodegeneration Caused by Mutation in the TDP Gene
- (2010) Hongxia Zhou et al. PLoS Genetics
- Ubiquilin and p97/VCP bind erasin, forming a complex involved in ERAD
- (2009) Precious J. Lim et al. JOURNAL OF CELL BIOLOGY
- Seipinopathy: a novel endoplasmic reticulum stress-associated disease
- (2008) Daisuke Ito et al. BRAIN
- ALS-linked mutant SOD1 induces ER stress- and ASK1-dependent motor neuron death by targeting Derlin-1
- (2008) H. Nishitoh et al. GENES & DEVELOPMENT
- Impaired ERAD and ER stress are early and specific events in polyglutamine toxicity
- (2008) M. L. Duennwald et al. GENES & DEVELOPMENT
- Unsaturated Fatty Acids Inhibit Proteasomal Degradation of Insig-1 at a Postubiquitination Step
- (2008) Joon No Lee et al. JOURNAL OF BIOLOGICAL CHEMISTRY
- SEL1L nucleates a protein complex required for dislocation of misfolded glycoproteins
- (2008) B. Mueller et al. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA
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