Therapeutic hepatocyte transplant for inherited metabolic disorders: functional considerations, recent outcomes and future prospects

Improved Amino Acid, Bioenergetic Metabolite and Neurotransmitter Profiles following Human Amnion Epithelial Cell Transplant in Intermediate Maple Syrup Urine Disease Mice

(2013) Kristen J. Skvorak et al.   MOLECULAR GENETICS AND METABOLISM

Hepatocyte Transplantation Using the Domino Concept in a Child with Tetrabiopterin Nonresponsive Phenylketonuria

(2012) X. Stéphenne et al.   CELL TRANSPLANTATION

Liver Regenerative Medicine: Advances and Challenges

(2012) Dimitry A. Chistiakov   CELLS TISSUES ORGANS

Kayser–Fleischer ring in Wilson's disease: A cohort study

(2012) M. Fenu et al.   European Journal of Internal Medicine

Placental stem cell correction of murine intermediate maple syrup urine disease

(2012) Kristen J. Skvorak et al.   HEPATOLOGY

Therapeutic liver repopulation for metabolic liver diseases: Advances from bench to bedside

(2012) Zhen Wan et al.   HEPATOLOGY RESEARCH

Hepatocyte transplantation in bile salt export pump-deficient mice: selective growth advantage of donor hepatocytes under bile acid stress

(2012) Huey-Ling Chen et al.   JOURNAL OF CELLULAR AND MOLECULAR MEDICINE

Long-term strategies for the treatment of Refsum's disease using therapeutic apheresis

(2012) D. Zolotov et al.   JOURNAL OF CLINICAL APHERESIS

In Vivo Selection of Transplanted Hepatocytes by Pharmacological Inhibition of Fumarylacetoacetate Hydrolase in Wild-type Mice

(2012) Nicole K Paulk et al.   MOLECULAR THERAPY

An update on primary hyperoxaluria

(2012) Bernd Hoppe   Nature Reviews Nephrology

Liver cell transplantation in severe infantile oxalosis--a potential bridging procedure to orthotopic liver transplantation?

(2012) B. B. Beck et al.   NEPHROLOGY DIALYSIS TRANSPLANTATION

Single Liver Lobe Repopulation with Wildtype Hepatocytes Using Regional Hepatic Irradiation Cures Jaundice in Gunn Rats

(2012) Hongchao Zhou et al.   PLoS One

Progressive familial intrahepatic cholestasis and inborn errors of bile acid synthesis

(2012) Irena Jankowska et al.   Clinics and Research in Hepatology and Gastroenterology

Progressive familial intrahepatic cholestasis

(2012) Emmanuel Jacquemin   Clinics and Research in Hepatology and Gastroenterology

Improving the Techniques for Human Hepatocyte Transplantation: Report from a Consensus Meeting in London

(2011) Juliana Puppi et al.   CELL TRANSPLANTATION

Interrupting the mechanisms of brain injury in a model of maple syrup urine disease encephalopathy

(2011) William J. Zinnanti et al.   JOURNAL OF INHERITED METABOLIC DISEASE

Liver Transplantation for Classical Maple Syrup Urine Disease: Long-Term Follow-Up in 37 Patients and Comparative United Network for Organ Sharing Experience

(2011) George V. Mazariegos et al.   JOURNAL OF PEDIATRICS

Cell therapies for liver diseases

(2011) Yue Yu et al.   LIVER TRANSPLANTATION

Hepatocytes from wild-type or heterozygous donors are equally effective in achieving successful therapeutic liver repopulation in murine phenylketonuria (PKU)

(2011) Kelly J. Hamman et al.   MOLECULAR GENETICS AND METABOLISM

Up to date knowledge on different treatment strategies for phenylketonuria

(2011) Amaya Bélanger-Quintana et al.   MOLECULAR GENETICS AND METABOLISM

Hepatocyte Transplantation Followed by Auxiliary Liver Transplantation-a Novel Treatment for Ornithine Transcarbamylase Deficiency

(2010) J. Puppi et al.   AMERICAN JOURNAL OF TRANSPLANTATION

Transplantation of allogeneic bone marrow mesenchymal stromal cell-derived hepatocyte-like cells in homozygous familial hypercholesterolemia

(2010) Mehdi Mohamadnejad et al.   CYTOTHERAPY

Therapeutic Liver Reconstitution With Murine Cells Isolated Long After Death

(2010) Laura Erker et al.   GASTROENTEROLOGY

Early orthotopic liver transplantation in urea cycle defects: Follow up of a developmental outcome study

(2010) Philippe M. Campeau et al.   MOLECULAR GENETICS AND METABOLISM

Liver, liver cell and stem cell transplantation for the treatment of urea cycle defects

(2010) Jochen Meyburg et al.   MOLECULAR GENETICS AND METABOLISM

Transplantation of Human Adipose Tissue-Derived Multilineage Progenitor Cells Reduces Serum Cholesterol in Hyperlipidemic Watanabe Rabbits

(2010) Hanayuki Okura et al.   TISSUE ENGINEERING PART C-METHODS

Hepatocyte transplantation (HTx) corrects selected neurometabolic abnormalities in murine intermediate maple syrup urine disease (iMSUD)

(2009) Kristen J. Skvorak et al.   BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE

Dual mechanism of brain injury and novel treatment strategy in maple syrup urine disease

(2009) W. J. Zinnanti et al.   BRAIN

Liver after Hepatocyte Transplantation for Liver-Based Metabolic Disorders in Children

(2009) Alberto Quaglia et al.   CELL TRANSPLANTATION

Purification and Use of Glycomacropeptide for Nutritional Management of Phenylketonuria

(2009) Caitlin E. LaClair et al.   JOURNAL OF FOOD SCIENCE

Classical maple syrup urine disease and brain development: Principles of management and formula design

(2009) Kevin A. Strauss et al.   MOLECULAR GENETICS AND METABOLISM

Hepatocyte Transplantation Improves Phenotype and Extends Survival in a Murine Model of Intermediate Maple Syrup Urine Disease

(2009) Kristen J Skvorak et al.   MOLECULAR THERAPY

One Liver for Four Children: First Clinical Series of Liver Cell Transplantation for Severe Neonatal Urea Cycle Defects

(2009) Jochen Meyburg et al.   TRANSPLANTATION

Living Related Liver Transplantation in Crigler-Najjar Syndrome Type 1

(2009) F. Özçay et al.   TRANSPLANTATION PROCEEDINGS

Liver Transplantation for Homozygous Familial Hypercholesterolemia: Two Case Reports

(2009) F. Kakaei et al.   TRANSPLANTATION PROCEEDINGS

First example of hepatocyte transplantation to alleviate ornithine transcarbamylase deficiency, monitored by NMR-based metabonomics

(2009) Cristina Legido-Quigley et al.   Bioanalysis

Bile salt-induced pro-oxidant liver damage promotes transplanted cell proliferation for correcting Wilson disease in the Long-Evans Cinnamon rat model

(2008) Brigid Joseph et al.   HEPATOLOGY

Hepatic repopulation with stably transduced conditionally immortalized hepatocytes in the Gunn rat

(2008) Yujo Kawashita et al.   JOURNAL OF HEPATOLOGY

Correction of Hyperoxaluria by Liver Repopulation With Hepatocytes in a Mouse Model of Primary Hyperoxaluria Type-1

(2008) Jinlan Jiang et al.   TRANSPLANTATION

Liver cell transplantation for Crigler-Najjar syndrome type I: Update and perspectives

(2008) Philippe A Lysy et al.   WORLD JOURNAL OF GASTROENTEROLOGY

Hepatic stress in hereditary tyrosinemia type 1 (HT1) activates the AKT survival pathway in the fah−/− knockout mice model

(2007) Diana Orejuela et al.   JOURNAL OF HEPATOLOGY