Fibrillin-1 and -2 differentially modulate endogenous TGF-β and BMP bioavailability during bone formation

Identification of a Frameshift Mutation in Osterix in a Patient with Recessive Osteogenesis Imperfecta

(2010) Pablo Lapunzina et al.   AMERICAN JOURNAL OF HUMAN GENETICS

Extracellular Microfibrils Control Osteoblast-supported Osteoclastogenesis by Restricting TGFβ Stimulation of RANKL Production

(2010) Harikiran Nistala et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Microfibril Structure Masks Fibrillin-2 in Postnatal Tissues

(2010) Noe L. Charbonneau et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Genetic Control of Bone Formation

(2009) Gerard Karsenty et al.   Annual Review of Cell and Developmental Biology

Biogenesis and function of fibrillin assemblies

(2009) Francesco Ramirez et al.   CELL AND TISSUE RESEARCH

Extracellular microfibrils: contextual platforms for TGFβ and BMP signaling

(2009) Francesco Ramirez et al.   CURRENT OPINION IN CELL BIOLOGY

Latent Transforming Growth Factor β-binding Proteins and Fibulins Compete for Fibrillin-1 and Exhibit Exquisite Specificities in Binding Sites

(2009) Robert N. Ono et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

New regulatory mechanisms of TGF-β receptor function

(2009) Jong Seok Kang et al.   TRENDS IN CELL BIOLOGY

p38 MAPK Is an Early Determinant of Promiscuous Smad2/3 Signaling in the Aortas of Fibrillin-1 (Fbn1)-null Mice

(2008) Luca Carta et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

Targeting of Bone Morphogenetic Protein Growth Factor Complexes to Fibrillin

(2008) Gerhard Sengle et al.   JOURNAL OF BIOLOGICAL CHEMISTRY

A New Model for Growth Factor Activation: Type II Receptors Compete with the Prodomain for BMP-7

(2008) Gerhard Sengle et al.   JOURNAL OF MOLECULAR BIOLOGY

Fibrillin Assembly Requires Fibronectin

(2008) Laetitia Sabatier et al.   MOLECULAR BIOLOGY OF THE CELL

Angiotensin II Blockade and Aortic-Root Dilation in Marfan's Syndrome

(2008) Benjamin S. Brooke et al.   NEW ENGLAND JOURNAL OF MEDICINE

Biogenesis of extracellular microfibrils: Multimerization of the fibrillin-1 C terminus into bead-like structures enables self-assembly

(2008) D. Hubmacher et al.   PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA